Mitochondrial myopathy with succinate dehydrogenase and aconitase deficiency. Abnormalities of several iron-sulfur proteins (Q24594335)

2

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S F Lewis

3

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R G Haller

4

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N G Kennaway

Journal of Clinical Investigation

5

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language of work or name

English

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publication date

December 1993

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published in

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volume

92

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issue

6

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page(s)

2660-6

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cites work

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12 December 2020

Mitochondrial rhodanese: membrane-bound and complexed activity

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12 December 2020

Mitochondrial myopathy with a defect of mitochondrial-protein transport

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12 December 2020

Low succinate dehydrogenase (SDH) activity in a patient with a hereditary myopathy with paroxysmal myoglobinuria

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12 December 2020

Involvement of a histidine residue in the interaction between membrane-anchoring protein (QPs) and succinate dehydrogenase in mitochondrial succinate-ubiquinone reductase

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12 December 2020

Acute ferrous sulfate hepatotoxicity in rats. An electron microscopic and biochemical study

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12 December 2020

Letter: Iron poisoning: another energy crisis

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12 December 2020

Effects of dietary iron deficiency of iron-sulfur proteins and bioenergetic functions of skeletal muscle mitochondria

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12 December 2020

Fatal lactic acidosis in infancy with a defect of complex III of the respiratory chain

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12 December 2020

Multiple defects of the respiratory chain including complex II in a family with myopathy and encephalopathy

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12 December 2020

Mitochondrial myopathies: clinical and biochemical features of 30 patients with major deletions of muscle mitochondrial DNA

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12 December 2020

Structural relationship between an iron-regulated RNA-binding protein (IRE-BP) and aconitase: functional implications

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12 December 2020

Mutational analysis of the mitochondrial Rieske iron-sulfur protein of Saccharomyces cerevisiae. III. Import, protease processing, and assembly into the cytochrome bc1 complex of iron-sulfur protein lacking the iron-sulfur cluster

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12 December 2020

Import of proteins into mitochondria

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12 December 2020

Purification of three iron-sulfur proteins from the iron-protein fragment of mitochondrial NADH-ubiquinone oxidoreductase

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12 December 2020

The role of iron in the activation-inactivation of aconitase

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12 December 2020

Effect of iron deficiency on succinate- and NADH-ubiquinone oxidoreductases in skeletal muscle mitochondria

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12 December 2020

Isolation and amino acid sequence of the 8 kDa DCCD-binding protein of beef heart ubiquinol:cytochrome c reductase

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12 December 2020

Differential investigation of the capacity of succinate oxidation in human skeletal muscle

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12 December 2020

Perturbation of mitochondrial composition in muscle by iron deficiency. Implications regarding regulation of mitochondrial assembly

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12 December 2020

Transport into mitochondria and intramitochondrial sorting of the Fe/S protein of ubiquinol-cytochrome c reductase

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12 December 2020

Effects of iron deficiency and training on mitochondrial enzymes in skeletal muscle

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12 December 2020

Mitochondrial protein import

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12 December 2020

Detection of low-molecular-weight polypeptides on nitrocellulose with monoclonal antibodies

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12 December 2020

Identifiers

DOI

10.1172/JCI116882

1 reference

release_qiin5tgjubbglf6hco72mko5pe

Fatcat ID

0 references

1 reference

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PubMed publication ID

8254022

1 reference