Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation (Q24624885)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

title

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

0 references

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Ronald C. Rubenstein

13

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

5

Jordan M Dunitz

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

7

Scott D Sagel

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

author name string

Frank J Accurso

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Steven M Rowe

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

J P Clancy

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Peter R Durie

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Douglas B Hornick

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Michael W Konstan

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Scott H Donaldson

10

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Richard B Moss

11

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Joseph M Pilewski

12

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Ahmet Z Uluer

14

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Moira L Aitken

15

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Steven D Freedman

16

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Lynn M Rose

17

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Nicole Mayer-Hamblett

18

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Qunming Dong

19

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Jiuhong Zha

20

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Anne J Stone

21

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Eric R Olson

22

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Claudia L Ordoñez

23

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Preston W Campbell

24

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Melissa A Ashlock

25

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Bonnie W Ramsey

26

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

language of work or name

English

0 references

publication date

1 November 2010

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

The New England Journal of Medicine

16 January 2020

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

volume

363

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

issue

21

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

page(s)

1991-2003

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

16 January 2020

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Spirometric reference values from a sample of the general U.S. population

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Determination of the minimal clinically important difference scores for the Cystic Fibrosis Questionnaire-Revised respiratory symptom scale in two populations of patients with cystic fibrosis and chronic Pseudomonas aeruginosa airway infection

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

High treatment burden in adults with cystic fibrosis: challenges to disease self-management

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Detection of cystic fibrosis transmembrane conductance regulator activity in early-phase clinical trials

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Molecular targeting of CFTR as a therapeutic approach to cystic fibrosis.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Gentamicin-Induced Correction of CFTR Function in Patients with Cystic Fibrosis andCFTRStop Mutations

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Relative ion permeability of normal and cystic fibrosis nasal epithelium

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Compacted DNA nanoparticles administered to the nasal mucosa of cystic fibrosis subjects are safe and demonstrate partial to complete cystic fibrosis transmembrane regulator reconstitution

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Molecular basis of defective anion transport in L cells expressing recombinant forms of CFTR.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

An apical-membrane chloride channel in human tracheal epithelium

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Development and validation of The Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Cationic lipid-mediated CFTR gene transfer to the lungs and nose of patients with cystic fibrosis: a double-blind placebo-controlled trial.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3148255

Does lithium carbonate affect the ion transport abnormality in cystic fibrosis?

28 November 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21083385

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1056/NEJMOA0909825

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

1 reference

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21083385%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

2 references