Kuru prions and sporadic Creutzfeldt-Jakob disease prions have equivalent transmission properties in transgenic and wild-type mice (Q24651920)

Emmanuel A Asante

8

0 references

Andrew F. Hill

Andrew F Hill

11

0 references

Jacqueline M Linehan

3

Jacqueline M Linehan

0 references

John Collinge

12

John Collinge

0 references

author name string

Jonathan D F Wadsworth

1

0 references

Susan Joiner

2

0 references

Katie Fox

5

0 references

Sharon Cooper

6

0 references

Sabrina Cronier

7

0 references

Simon Mead

9

0 references

Sebastian Brandner

Proceedings of the National Academy of Sciences of the United States of America

10

0 references

language of work or name

English

0 references

publication date

11 March 2008

0 references

published in

0 references

volume

105

0 references

issue

10

0 references

page(s)

3885-90

0 references

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

7 April 2017

The state of the prion

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Prion diseases of humans and animals: their causes and molecular basis

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Eight prion strains have PrP(Sc) molecules with different conformations

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Inherited prion disease with 5-OPRI: phenotype modification by repeat length and codon 129.

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Update on human prion disease.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Inherited prion disease with six octapeptide repeat insertional mutation--molecular analysis of phenotypic heterogeneity.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Iatrogenic Creutzfeldt-Jakob disease: the waning of an era.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Dissociation of pathological and molecular phenotype of variant Creutzfeldt-Jakob disease in transgenic human prion protein 129 heterozygous mice

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Kuru in the 21st century--an acquired human prion disease with very long incubation periods

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Prion infectivity in variant Creutzfeldt-Jakob disease rectum.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

The epidemiology of kuru in the period 1987 to 1995.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Pathogenesis and prevalence of variant Creutzfeldt-Jakob disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Molecular neurology of prion disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Neuropathology and molecular biology of variant Creutzfeldt-Jakob disease.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Specificity of lymphoreticular accumulation of prion protein for variant Creutzfeldt-Jakob disease.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Peripheral tissue involvement in sporadic, iatrogenic, and variant Creutzfeldt-Jakob disease: an immunohistochemical, quantitative, and biochemical study

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Subclinical prion infection.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Acquired prion disease: iatrogenic CJD, variant CJD, kuru

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Molecular and clinical classification of human prion disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Balancing selection at the prion protein gene consistent with prehistoric kurulike epidemics

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Strain variations and species barriers

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Identification of multiple quantitative trait loci linked to prion disease incubation period in mice

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Increased susceptibility to Kuru of carriers of the PRNP 129 methionine/methionine genotype

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Iatrogenic Creutzfeldt-Jakob disease at the millennium.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Genetic influence on the structural variations of the abnormal prion protein

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Variant Creutzfeldt-Jakob disease.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Pathology and immunocytochemistry of a kuru brain

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

A new variant of Creutzfeldt-Jakob disease in the UK.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Tissue handling in suspected Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (prion diseases)

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Transmission of Creutzfeldt-Jakob disease from humans to transgenic mice expressing chimeric human-mouse prion protein

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Experimental transmission of a Kuru-like syndrome to chimpanzees

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

The epidemiology of Creutzfeldt-Jakob disease: conclusion of a 15-year investigation in France and review of the world literature

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Mouse polyclonal and monoclonal antibody to scrapie-associated fibril proteins

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Homozygous prion protein genotype predisposes to sporadic Creutzfeldt–Jakob disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

"Friendly fire" in medicine: hormones, homografts, and Creutzfeldt-Jakob disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

An antibody raised against a conserved sequence of the prion protein recognizes pathological isoforms in human and animal prion diseases, including Creutzfeldt-Jakob disease and bovine spongiform encephalopathy.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Iatrogenic Creutzfeldt-Jakob disease in three growth hormone recipients: a neuropathological study.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Kuru and Creutzfeldt-Jakob disease: clinical and aetiological aspects

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Rapid detection of Creutzfeldt-Jakob disease and scrapie prion proteins

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Inherited prion disease with 144 base pair gene insertion. 2. Clinical and pathological features.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Human prion protein with valine 129 prevents expression of variant CJD phenotype

30 May 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

The same prion strain causes vCJD and BSE

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Tissue distribution of protease resistant prion protein in variant Creutzfeldt-Jakob disease using a highly sensitive immunoblotting assay

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Prevalence of lymphoreticular prion protein accumulation in UK tissue samples.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Analysis of 2000 consecutive UK tonsillectomy specimens for disease-related prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Genetic basis of Creutzfeldt-Jakob disease in the United Kingdom: a systematic analysis of predisposing mutations and allelic variation in the PRNP gene.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Strain-specific prion-protein conformation determined by metal ions

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Molecular classification of sporadic Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

21 January 2018

Typing prion isoforms.

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Unaltered susceptibility to BSE in transgenic mice expressing human prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Identification and characterization of a novel mouse prion gene allele

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Diarrhoea as a presentation of bird flu infection: a summary on its correlation to outcome in Thai cases

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

Sporadic Creutzfeldt-Jakob disease in two adolescents

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

High levels of disease related prion protein in the ileum in variant Creutzfeldt-Jakob disease.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Comparative neuropathology of Kuru with the new variant of Creutzfeldt-Jakob disease: evidence for strain of agent predominating over genotype of host.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2268835

Linkage of prion protein and scrapie incubation time genes

28 November 2018

1 reference

12 December 2020

Kuru; clinical, pathological and epidemiological study of an acute progressive degenerative disease of the central nervous system among natives of the Eastern Highlands of New Guinea

1 reference

12 December 2020

Quantitative trait loci affecting prion incubation time in mice

1 reference

12 December 2020

Neuropathology of prion diseases

1 reference

12 December 2020

Characterization of two distinct prion strains derived from bovine spongiform encephalopathy transmissions to inbred mice

1 reference

12 December 2020

Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0800190105

7 January 2021