Cerebrotendinous xanthomatosis: a defect in mitochondrial 26-hydroxylation required for normal biosynthesis of cholic acid (Q28367184)

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S Skrede

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A Schreiner

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J I Pederson

Journal of Clinical Investigation

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language of work or name

English

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publication date

June 1980

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published in

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volume

65

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issue

6

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page(s)

1418-30

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cites work

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SYNTHESIS AND METABOLISM OF CHOLEST-4-ENE-7-ALPHA,12-ALPHA-DIOL-3-ONE AND 5-BETA-CHOLESTANE-7-ALPHA,12-ALPHA-DIOL-3-ONE. BILE ACIDS AND STEROIDS 153

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ON THE STEREOSPECIFICITY OF 26-HYDROXYLATION OF CHOLESTEROL. BILE ACIDS AND STEROIDS. 155

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Formation of trihydroxycoprostanic acid from cholesterol in man

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Enzymatic characteristics of CO-sensitive 26-hydroxylase system for 5beta-cholestane-3 alpha, 7 alpha, 12 alpha-triol in rat-liver mitochondria and its intramitochondrial localization

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A novel specific assay of 25-hydroxy vitamin D

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