Absence of peroxisomes in mouse hepatocytes causes mitochondrial and ER abnormalities (Q28508098)

GOA release 2020-03-11

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Ilse Vanhorebeek

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Paul P Van Veldhoven

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object named as

Paul P. Van Veldhoven

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24 January 2017

Ruud Dirkx

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24 January 2017

Katrin Martens

3

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24 January 2017

Arno Schad

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24 January 2017

Markus Grabenbauer

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24 January 2017

Dariush Fahimi

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24 January 2017

Peter Declercq

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24 January 2017

Myriam Baes

Peroxisomal abnormalities in metabolic diseases

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24 January 2017

language of work or name

English

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publication date

1 April 2005

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24 January 2017

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24 January 2017

41

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24 January 2017

868–878

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24 January 2017

4

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24 January 2017

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Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse)

21 January 2018

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The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation.

21 January 2018

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Protein serine/threonine phosphatase inhibitors suppress phenobarbital-induced Cyp2b10 gene transcription in mouse primary hepatocytes

21 January 2018

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The cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects

21 January 2018

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7 January 2021

Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome.

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7 January 2021

Biochemical studies in the liver and muscle of patients with Zellweger syndrome.

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7 January 2021

Pathology of hepatic peroxisomes and mitochondria in patients with peroxisomal disorders

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7 January 2021

Light and electron microscopic liver changes in the cerebro-hepato-renal syndrome of Zellweger (Peroxisome deficiency) (author's transl)

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7 January 2021

Ultrastructure of the Liver in the Cerebrohepatorenal Syndrome of Zellweger

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7 January 2021

The cerebro-hepato-renal (Zellweger) syndrome: lamellar lipid profiles in adrenocortical, hepatic mesenchymal, astrocyte cells and increased levels of very long chain fatty acids and phytanic acid in the plasma.

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7 January 2021

Zellweger syndrome: biochemical and morphological studies on two patients treated with clofibrate

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7 January 2021

A mouse model for Zellweger syndrome

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7 January 2021

Dual roles for glucokinase in glucose homeostasis as determined by liver and pancreatic beta cell-specific gene knock-outs using Cre recombinase

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7 January 2021

Generation of Pex5-loxP mice allowing the conditional elimination of peroxisomes

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7 January 2021

Assay of glutathione, glutathione disulfide, and glutathione mixed disulfides in biological samples

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7 January 2021

The tetrazolium dyes MTS and XTT provide new quantitative assays for superoxide and superoxide dismutase

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7 January 2021

Determination of carbonyl content in oxidatively modified proteins

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7 January 2021

Factors underlying significant underestimations of glucokinase activity in crude liver extracts: physiological implications of higher cellular activity.

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7 January 2021

Pyruvate kinase isozymes from rat

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7 January 2021

Intracellular heterogeneity in mitochondrial membrane potentials revealed by a J-aggregate-forming lipophilic cation JC-1.

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7 January 2021

Measuring mitochondrial reactive oxygen species.

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7 January 2021

Decrease of intracellular ATP content downregulated UCP2 expression in mouse hepatocytes

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7 January 2021

Mitochondrial dysfunction in a cell culture model of familial amyotrophic lateral sclerosis

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7 January 2021

Transcription coactivator PBP, the peroxisome proliferator-activated receptor (PPAR)-binding protein, is required for PPARalpha-regulated gene expression in liver

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7 January 2021

Steatohepatitis, spontaneous peroxisome proliferation and liver tumors in mice lacking peroxisomal fatty acyl-CoA oxidase. Implications for peroxisome proliferator-activated receptor alpha natural ligand metabolism.

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7 January 2021

Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D-forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal b

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7 January 2021

Disturbed cholesterol homeostasis in a peroxisome-deficient PEX2 knockout mouse model

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7 January 2021

Pex13 inactivation in the mouse disrupts peroxisome biogenesis and leads to a Zellweger syndrome phenotype

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7 January 2021

Subcellular heterogeneity of mitochondrial function and dysfunction: evidence obtained by confocal imaging

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7 January 2021

Disorders of the mitochondria

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7 January 2021

Dependence of H2O2 formation by rat heart mitochondria on substrate availability and donor age.

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7 January 2021

Titrating the effects of mitochondrial complex I impairment in the cell physiology

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7 January 2021

Mitochondrial complex I deficiency leads to increased production of superoxide radicals and induction of superoxide dismutase

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7 January 2021

Decrease in mitochondrial complex I activity in ischemic/reperfused rat heart: involvement of reactive oxygen species and cardiolipin.

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7 January 2021

Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency

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7 January 2021

Reduced activity of the electron transport chain in liver mitochondria isolated from rats with secondary biliary cirrhosis

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7 January 2021

Role of ALDP (ABCD1) and mitochondria in X-linked adrenoleukodystrophy

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7 January 2021

The effect of peroxisome proliferators on mitochondrial bioenergetics.

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7 January 2021

Mitochondrial respiratory chain dysfunction, a non-receptor-mediated effect of synthetic PPAR-ligands: biochemical and pharmacological implications

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7 January 2021

Phytanic acid activates the peroxisome proliferator-activated receptor alpha (PPARalpha) in sterol carrier protein 2-/ sterol carrier protein x-deficient mice

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7 January 2021