Malfolded protein structure and proteostasis in lung diseases. (Q30353585)

21 August 2017

Malfolded protein structure and proteostasis in lung diseases. (English)

1 reference

21 August 2017

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6

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21 August 2017

William E Balch

1

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21 August 2017

Jacob I Sznajder

2

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21 August 2017

Scott Budinger

3

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21 August 2017

Daniel Finley

4

1 reference

21 August 2017

Aaron D Laposky

5

1 reference

21 August 2017

Ivor J Benjamin

7

1 reference

21 August 2017

Esther Barreiro

8

1 reference

21 August 2017

Richard I Morimoto

9

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21 August 2017

Lisa Postow

10

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21 August 2017

Allan M Weissman

11

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21 August 2017

Dorothy Gail

12

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21 August 2017

Susan Banks-Schlegel

13

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21 August 2017

Thomas Croxton

14

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21 August 2017

Weiniu Gan

15

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21 August 2017

language of work or name

English

0 references

publication date

1 January 2014

1 reference

American Journal of Respiratory and Critical Care Medicine

21 August 2017

1 reference

21 August 2017

189

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21 August 2017

1

1 reference

21 August 2017

96-103

1 reference

Deaths: preliminary data for 2011.

21 August 2017

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The emerging role of the ubiquitin proteasome in pulmonary biology and disease

3 June 2018

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Diversity in the origins of proteostasis networks--a driver for protein function in evolution

3 June 2018

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Expanding proteostasis by membrane trafficking networks

3 June 2018

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Analysis of 6,515 exomes reveals the recent origin of most human protein-coding variants

3 June 2018

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Cigarette smoking affects oxidative protein folding in endoplasmic reticulum by modifying protein disulfide isomerase

3 June 2018

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Chronic obstructive pulmonary disease among adults--United States, 2011.

3 June 2018

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The emerging importance of autophagy in pulmonary diseases

3 June 2018

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Histone deacetylase inhibitor (HDACi) suberoylanilide hydroxamic acid (SAHA)-mediated correction of α1-antitrypsin deficiency

3 June 2018

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3 June 2018

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Role of histone deacetylase 2 in epigenetics and cellular senescence: implications in lung inflammaging and COPD

3 June 2018

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A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease

3 June 2018

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Proteostasis, an emerging therapeutic paradigm for managing inflammatory airway stress disease

3 June 2018

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Therapeutic strategies to correct proteostasis-imbalance in chronic obstructive lung diseases.

3 June 2018

1 reference

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Roles of endoplasmic reticulum and energetic stress in disturbed sleep

3 June 2018

1 reference

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Endoplasmic reticulum stress and type 2 diabetes

3 June 2018

1 reference

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Effect of a monoclonal antibody to PCSK9 on LDL cholesterol

3 June 2018

1 reference

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The heat shock response: systems biology of proteotoxic stress in aging and disease

3 June 2018

1 reference

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Neurobiology and neuropathophysiology of obstructive sleep apnea

3 June 2018

1 reference

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Interplay between histone deacetylases and autophagy--from cancer therapy to neurodegeneration

3 June 2018

1 reference

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The unfolded protein response: from stress pathway to homeostatic regulation

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Autophagy and disease: always two sides to a problem

3 June 2018

1 reference

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Correction of the F508del-CFTR protein processing defect in vitro by the investigational drug VX-809.

3 June 2018

1 reference

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Oxidative stress-induced antibodies to carbonyl-modified protein correlate with severity of chronic obstructive pulmonary disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Proteasomal inhibition after injury prevents fibrosis by modulating TGF-β(1) signalling

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Chemical and biological approaches for adapting proteostasis to ameliorate protein misfolding and aggregation diseases: progress and prognosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

The role of Nogo and the mitochondria-endoplasmic reticulum unit in pulmonary hypertension

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Genetics in pulmonary fibrosis--familial cases provide clues to the pathogenesis of idiopathic pulmonary fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Proteostasis: a new therapeutic paradigm for pulmonary disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

The stress of protein misfolding: from single cells to multicellular organisms

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

A common MUC5B promoter polymorphism and pulmonary fibrosis.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Emergent properties of proteostasis in managing cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Endoplasmic reticulum stress in wake-active neurons progresses with aging

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Critical role of proteostasis-imbalance in pathogenesis of COPD and severe emphysema

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

The mitochondrial UPR - protecting organelle protein homeostasis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Proteostasis strategies for restoring alpha1-antitrypsin deficiency

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Protein Homeostasis in Models of Aging and Age-Related Conformational Disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Oxidative stress: acute and progressive lung injury

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Oxidative protein folding in the secretory pathway and redox signaling across compartments and cells

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Ubiquitination and proteolysis in limb and respiratory muscles of patients with chronic obstructive pulmonary disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

3 June 2018

What makes a good lung?

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Recognition and processing of ubiquitin-protein conjugates by the proteasome

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

A proprotein convertase subtilisin/kexin type 9 neutralizing antibody reduces serum cholesterol in mice and nonhuman primates

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

alpha1-Antitrypsin deficiency, chronic obstructive pulmonary disease and the serpinopathies

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Biological and chemical approaches to diseases of proteostasis deficiency

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

MUC5B is the major mucin in the gel phase of sputum in chronic obstructive pulmonary disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Bortezomib plus melphalan and prednisone for initial treatment of multiple myeloma

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Mutations linked to interstitial lung disease can abrogate anti-amyloid function of prosurfactant protein C.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Epithelial endoplasmic reticulum stress and apoptosis in sporadic idiopathic pulmonary fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Adapting proteostasis for disease intervention

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

In and Out of the ER: Protein Folding, Quality Control, Degradation, and Related Human Diseases

3 June 2018

1 reference

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The alveolar-epithelial barrier: a target for potential therapy

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

Pulmonary fibrosis in hermansky-pudlak syndrome. a case report and review

3 June 2018

1 reference

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Protein synthesis upon acute nutrient restriction relies on proteasome function

3 June 2018

1 reference

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Genetic mutations in surfactant protein C are a rare cause of sporadic cases of IPF

3 June 2018

1 reference

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Rapid degradation of a large fraction of newly synthesized proteins by proteasomes.

3 June 2018

1 reference

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Critical illness myopathy and GLUT4: significance of insulin and muscle contraction

3 June 2018

1 reference

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Does oxidative stress modulate limb muscle atrophy in severe COPD patients?

26 November 2018

1 reference

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Cigarette smoke-induced oxidative stress: A role in chronic obstructive pulmonary disease skeletal muscle dysfunction.

26 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3919126

CFTR Genotype as a Predictor of Prognosis in Cystic Fibrosis

26 November 2018

1 reference

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American Thoracic Society/European Respiratory Society statement: standards for the diagnosis and management of individuals with alpha-1 antitrypsin deficiency.

26 November 2018

1 reference

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Rapidly progressive diaphragmatic weakness and injury during mechanical ventilation in humans

26 November 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/24033344

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Muscle fibre atrophy in critically ill patients is associated with the loss of myosin filaments and the presence of lysosomal enzymes and ubiquitin

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/24033344

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

MUC5AC and MUC5B mucins increase in cystic fibrosis airway secretions during pulmonary exacerbation

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/24033344

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1164/RCCM.201306-1164WS

1 reference

21 August 2017

1 reference

21 August 2017

PubMed publication ID

24033344

1 reference