Human embryonic stem cell-derived motor neurons expressing SOD1 mutants exhibit typical signs of motor neuron degeneration linked to ALS. (Q30486275)

12 October 2017

Human embryonic stem cell-derived motor neurons expressing SOD1 mutants exhibit typical signs of motor neuron degeneration linked to ALS. (English)

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amyotrophic lateral sclerosis

12 October 2017

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human embryonic stem cell

inferred from title

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8

Harley I Kornblum

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12 October 2017

Saravanan Karumbayaram

1

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12 October 2017

Theresa K Kelly

2

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12 October 2017

Andres A Paucar

3

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12 October 2017

Anne J T Roe

4

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12 October 2017

Joy A Umbach

5

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12 October 2017

Andrew Charles

6

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12 October 2017

Steven A Goldman

7

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12 October 2017

Martina Wiedau-Pazos

9

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12 October 2017

language of work or name

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23 February 2009

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Disease Models & Mechanisms

12 October 2017

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12 October 2017

2

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12 October 2017

3-4

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12 October 2017

189-195

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describes a project that uses

12 October 2017

ImageJ

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC2650191/fullTextXML

inferred from PubMed Central ID database lookup

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Integrative genomic and functional analyses reveal neuronal subtype differentiation bias in human embryonic stem cell lines

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GDNF secreting human neural progenitor cells protect dying motor neurons, but not their projection to muscle, in a rat model of familial ALS.

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Onset and progression in inherited ALS determined by motor neurons and microglia

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Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis

20 June 2018

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26 November 2018

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Interneurone bursts are spontaneously associated with muscle contractions only during early phases of mouse spinal network development: a study in organotypic cultures

26 November 2018

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Wild-Type Nonneuronal Cells Extend Survival of SOD1 Mutant Motor Neurons in ALS Mice

26 November 2018

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Characterization of the circuits that generate spontaneous episodes of activity in the early embryonic mouse spinal cord.

26 November 2018

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In vivo peroxidative activity of FALS-mutant human CuZnSODs expressed in yeast

26 November 2018

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26 November 2018

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Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man

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12 December 2020

Morphometric and biochemical studies of peripheral nerves in amyotrophic lateral sclerosis

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12 December 2020

Prognosis in familial amyotrophic lateral sclerosis: progression and survival in patients with glu100gly and ala4val mutations in Cu,Zn superoxide dismutase

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12 December 2020

QUANTITATIVE ASPECTS OF REPETITIVE FIRING OF MAMMALIAN MOTONEURONES, CAUSED BY INJECTED CURRENTS

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12 December 2020

Selective vulnerability and pruning of phasic motoneuron axons in motoneuron disease alleviated by CNTF

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12 December 2020

Protein-bound crotonaldehyde accumulates in the spinal cord of superoxide dismutase-1 mutation-associated familial amyotrophic lateral sclerosis and its transgenic mouse model

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12 December 2020

Stem cells and drug discovery: the beginning of a new era?

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12 December 2020

Neuroscience: Standard model

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12 December 2020

Identifiers

DOI

10.1242/DMM.002113

1 reference

12 October 2017

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12 October 2017

PubMed publication ID

19259395

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