Sulfatide storage in neurons causes hyperexcitability and axonal degeneration in a mouse model of metachromatic leukodystrophy. (Q33294970)

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3 January 2020

title

Sulfatide storage in neurons causes hyperexcitability and axonal degeneration in a mouse model of metachromatic leukodystrophy (English)

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3 January 2020

author

Renate Lüllmann-Rauch

4

object named as

Renate Lüllmann-Rauch

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author name string

Matthias Eckhardt

1

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3 January 2020

Kerstin Khalaj Hedayati

2

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3 January 2020

Julika Pitsch

3

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3 January 2020

Renate Lüllmann-Rauch

4

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3 January 2020

Heinz Beck

5

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3 January 2020

Simon Ngamli Fewou

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3 January 2020

Volkmar Gieselmann

7

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language of work or name

English

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publication date

1 August 2007

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3 January 2020

published in

Journal of Neuroscience

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volume

27

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issue

34

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page(s)

9009-9021

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An apoptotic depletion of oligodendrocytes in the twitcher, a murine model of globoid cell leukodystrophy.

3 January 2020

cites work

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Neuromotor alterations and cerebellar deficits in aged arylsulfatase A-deficient transgenic mice.

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Decline in brainstem auditory-evoked potentials coincides with loss of spiral ganglion cells in arylsulfatase A-deficient mice

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Axonal pathology in myelin disorders

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Neuropathology in mice expressing human alpha-synuclein

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Hyperactivity, neuromotor defects, and impaired learning and memory in a mouse model for metachromatic leukodystrophy.

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Morphological alterations in the inner ear of the arylsulfatase A-deficient mouse.

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Lysosomal sulfoglycolipid storage in the kidneys of mice deficient for arylsulfatase A (ASA) and of double-knockout mice deficient for ASA and galactosylceramide synthase.

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Kidney sulfatides in mouse models of inherited glycosphingolipid disorders: determination by nano-electrospray ionization tandem mass spectrometry.

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Expression of the myelin and oligodendrocyte progenitor marker sulfatide in neurons and astrocytes of adult rat brain

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Sulfatide controls insulin secretion by modulation of ATP-sensitive K(+)-channel activity and Ca(2+)-dependent exocytosis in rat pancreatic beta-cells

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N-glycosylation is required for full enzymic activity of the murine galactosylceramide sulphotransferase

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Lysosomal sulfatide storage in the brain of arylsulfatase A-deficient mice: cellular alterations and topographic distribution

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Accumulation of sulfatide in neuronal and glial cells of arylsulfatase A deficient mice

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Sulfatide and Na+-K+-ATPase: a salinity-sensitive relationship in the gill basolateral membrane of rainbow trout

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Delay of myelin formation in arylsulphatase A-deficient mice

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Oligodendrocyte-specific ceramide galactosyltransferase (CGT) expression phenotypically rescues CGT-deficient mice and demonstrates that CGT activity does not limit brain galactosylceramide level

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Reversal of non-hydroxy:alpha-hydroxy galactosylceramide ratio and unstable myelin in transgenic mice overexpressing UDP-galactose:ceramide galactosyltransferase

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Sulfatide with short fatty acid dominates in astrocytes and neurons

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Regulatory effect of sulphatides on BKCa channels

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Microanalysis of complex tissue lipids by high-performance thin-layer chromatography.

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Ceramide Galactoside of Enriched Neuronal and Glial Fractions from Rat Brain

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Isolation of biologically active ribonucleic acid from sources enriched in ribonuclease

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12 December 2020

Adult metachromatic leukodystrophy (sulphatide lipidosis) simulating acute schizophrenia. Report of a case

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12 December 2020

Synthesis of cerebroside by brain from uridine diphosphate galactose and ceramide containing hydroxy fatty acid

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12 December 2020

Cerebroside sulfotransferase in Golgi-enriched fractions from rat brain

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Motor function analysis of myelin mutant mice using a rotarod

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12 December 2020

Phenotype of arylsulfatase A-deficient mice: relationship to human metachromatic leukodystrophy

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12 December 2020

Late juvenile metachromatic leukodystrophy (MLD) in three patients with a similar clinical course and identical mutation on one allele

1 reference

12 December 2020

Occurrence, distribution, and phenotype of arylsulfatase A mutations in patients with metachromatic leukodystrophy.

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12 December 2020

Endogenous serine protease inhibitor modulates epileptic activity and hippocampal long-term potentiation

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12 December 2020

Metachromatic leukodystrophy: molecular genetics and an animal model

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12 December 2020

10.1523/JNEUROSCI.2329-07.2007

Identifiers

DOI

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