The Wobbler Mouse: A Neurodegeneration Jigsaw Puzzle (Q33339275)

25 July 2017

1 reference

title

The wobbler mouse: a neurodegeneration jigsaw puzzle (English)

1 reference

https://api.crossref.org/works/10.1385/MN:28:1:65

25 July 2017

The Wobbler Mouse: A Neurodegeneration Jigsaw Puzzle (English)

1 reference

15 March 2024

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14514986

15 March 2024

1 reference

https://api.crossref.org/works/10.1385/MN:28:1:65

15 March 2024

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1

Séverine Boillée

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14514986

15 March 2024

author name string

Marc Peschanski

series ordinal

2

1 reference

25 July 2017

Marie-Pierre Junier

series ordinal

3

1 reference

25 July 2017

language of work or name

English

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=14514986

15 March 2024

publication date

1 August 2003

1 reference

full work available at URL

25 July 2017

http://www.springerlink.com/index/pdf/10.1385/MN:28:1:65

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https://api.crossref.org/works/10.1385/MN:28:1:65

15 March 2024

published in

Molecular Neurobiology

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25 July 2017

volume

28

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25 July 2017

issue

1

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25 July 2017

page(s)

65-106

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Acetylcholine esterase and peripherin mRNA level decrease in wobbler mouse

25 July 2017

cites work

1 reference

12 December 2020

Alterations in acetylcholinesterase and choline acetyltransferase activities and neuropeptide levels in the ventral spinal cord of the Wobbler mouse during inherited motoneuron disease

1 reference

12 December 2020

Sec61p and BiP directly facilitate polypeptide translocation into the ER.

1 reference

12 December 2020

Neurofilament distribution is altered in the Mnd (motor neuron degeneration) mouse

1 reference

12 December 2020

'Wasted', a new mutant of the mouse with abnormalities characteristic to ataxia telangiectasia.

1 reference

12 December 2020

Acid protease activity in spinal cord and muscle in wobbler mouse

1 reference

12 December 2020

Transforming growth factor alpha expression as a response of murine motor neurons to axonal injury and mutation-induced degeneration

1 reference

12 December 2020

Effects of cardiotrophin-1 (CT-1) in a mouse motor neuron disease

1 reference

12 December 2020

Polyglutamine length-dependent interaction of Hsp40 and Hsp70 family chaperones with truncated N-terminal huntingtin: their role in suppression of aggregation and cellular toxicity

1 reference

12 December 2020

A controlled trial of recombinant methionyl human BDNF in ALS: The BDNF Study Group (Phase III)

1 reference

12 December 2020

Overexpression of neurofilament subunit NF-L and NF-H extends survival of a mouse model for amyotrophic lateral sclerosis

1 reference

12 December 2020

Reactive astrocytes: cellular and molecular cues to biological function

1 reference

12 December 2020

Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.

1 reference

12 December 2020

Spatiotemporal progression of neurodegeneration and glia activation in the wobbler neuropathy of the mouse.

1 reference

12 December 2020

Protein fate in neurodegenerative proteinopathies: polyglutamine diseases join the (mis)fold

1 reference

12 December 2020

Increased expression of neurofilament subunit NF-L produces morphological alterations that resemble the pathology of human motor neuron disease

1 reference

12 December 2020

Impaired slow axonal transport in wobbler mouse motor neuron disease

1 reference

12 December 2020

Effects of brain-derived neurotrophic factor on motor dysfunction in wobbler mouse motor neuron disease

1 reference

12 December 2020

Reduced branching and length of dendrites detected in cervical spinal cord motoneurons of wobbler mouse, a model for inherited motoneuron disease

1 reference

12 December 2020

Measurement of neuropeptides in the brain and spinal cord of Wobbler mouse: a model for motoneuron disease

1 reference

12 December 2020

Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions

1 reference

12 December 2020

Retardation of fast axonal transport in wobbler mice

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12 December 2020

GAP-43: an intrinsic determinant of neuronal development and plasticity

1 reference

12 December 2020

Decreased immunoreactive (IR) calcitonin gene-related peptide correlates with sprouting of IR-peptidergic and serotonergic neuronal processes in spinal cord and brain nuclei from the Wobbler mouse during motoneuron disease

1 reference

12 December 2020

Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant

1 reference

12 December 2020

Acid hydrolases and other enzymes in secondary demyelination: a quantitative histochemical study in the wobbler mouse.

1 reference

12 December 2020

A gene encoding a putative GTPase regulator is mutated in familial amyotrophic lateral sclerosis 2

1 reference

12 December 2020

Elevated expression of membrane type 1 metalloproteinase (MT1-MMP) in reactive astrocytes following neurodegeneration in mouse central nervous system

1 reference

12 December 2020

Protective effect of a novel free radical scavenger, OPC-14117, on wobbler mouse motor neuron disease

1 reference

12 December 2020

The motoneuron degeneration in the wobbler mouse is independent of the overexpression of a Bcl2 transgene in neurons

1 reference

12 December 2020

Murine motor neuron disease (the wobbler mouse): degeneration and regeneration of the lower motor neuron.

1 reference

12 December 2020

Chronic inhibition of glutamate uptake produces a model of slow neurotoxicity

1 reference

12 December 2020

Chaperoning brain diseases.

1 reference

12 December 2020

Integrated radiation hybrid map of human chromosome 2p13: possible involvement of dynactin in neuromuscular diseases

1 reference

12 December 2020

Amyotrophic lateral sclerosis: current issues in classification, pathogenesis and molecular pathology

1 reference

12 December 2020

BDNF and NT-4/5 exert neurotrophic influences on injured adult spinal motor neurons

1 reference

12 December 2020

Definition of tumor-associated antigens in hepatocellular carcinoma.

1 reference

12 December 2020

Comparative transcription map of the wobbler critical region on mouse chromosome 11 and the homologous region on human chromosome 2p13-14.

1 reference

12 December 2020

Motoneuron loss in the abducens nucleus of wobbler mice

1 reference

12 December 2020

Polyglutamine-expanded androgen receptors form aggregates that sequester heat shock proteins, proteasome components and SRC-1, and are suppressed by the HDJ-2 chaperone

1 reference

12 December 2020

Abnormal astrocyte differentiation and defective cellular interactions in wobbler mouse spinal cord.

1 reference

12 December 2020

Ubiquitin-dependent degradation of certain protein substrates in vitro requires the molecular chaperone Hsc70

1 reference

12 December 2020

Early defect in the expression of mouse sperm DnaJ 1, a member of the DNAJ/heat shock protein 40 chaperone protein family, in the spinal cord of the wobbler mouse, a murine model of motoneuronal degeneration

1 reference

12 December 2020

Induction of nitric oxide synthase and motoneuron death in newborn and early postnatal rats following spinal root avulsion

1 reference

12 December 2020

Microglia and the early phase of immune surveillance in the axotomized facial motor nucleus: impaired microglial activation and lymphocyte recruitment but no effect on neuronal survival or axonal regeneration in macrophage-colony stimulating factor-

1 reference

12 December 2020

Modulation of HSP25 expression during anterior horn motor neuron degeneration in the paralysé mouse mutant

1 reference

12 December 2020

Reactive microglia in cerebral ischaemia: an early mediator of tissue damage?

1 reference

12 December 2020

Randomized, double-blind, controlled trial of acetylcysteine in amyotrophic lateral sclerosis

1 reference

12 December 2020

Motor neurone disease and animal models

1 reference

12 December 2020

The wobbler mouse mutant: an animal model of hereditary motor system disease

1 reference

12 December 2020

MSJ-1, a mouse testis-specific DnaJ protein, is highly expressed in haploid male germ cells and interacts with the testis-specific heat shock protein Hsp70-2

1 reference

12 December 2020

Spinal muscular atrophies: recent insights and impact on molecular diagnosis

1 reference

12 December 2020

Inhibition of nitric oxide synthase reduces motoneuron death due to spinal root avulsion

1 reference

12 December 2020

Glucocorticoid receptors and actions in the spinal cord of the Wobbler mouse, a model for neurodegenerative diseases

1 reference

12 December 2020

Glycosaminoglycans boost insulin-like growth factor-I-promoted neuroprotection: blockade of motor neuron death in the wobbler mouse

1 reference

12 December 2020

Deletion of the hypoxia-response element in the vascular endothelial growth factor promoter causes motor neuron degeneration.

1 reference

12 December 2020

Astrocyte overgrowth in the brain stem and spinal cord of mice affected by spinal atrophy, wobbler

1 reference

12 December 2020

Tumor necrosis factor alpha induces a metalloprotease-disintegrin, ADAM8 (CD 156): implications for neuron-glia interactions during neurodegeneration

1 reference

12 December 2020

Transforming growth factor alpha: a promoter of motoneuron survival of potential biological relevance.

1 reference

12 December 2020

A double-blind, placebo-controlled randomized clinical trial of alpha-tocopherol (vitamin E) in the treatment of amyotrophic lateral sclerosis. ALS riluzole-tocopherol Study Group

1 reference

12 December 2020

A phase I/II trial of recombinant methionyl human brain derived neurotrophic factor administered by intrathecal infusion to patients with amyotrophic lateral sclerosis.

1 reference

12 December 2020

Neurofilaments and motor neuron disease

1 reference

12 December 2020

Histometric characteristics and regenerative capacity in wobbler mouse motor neuron disease.

1 reference

12 December 2020

Ultrastructural differences during embryonic cell death in normal and peripherally deprived ciliary ganglia

1 reference

12 December 2020

Evidence for down-regulation of GAP-43 mRNA in Wobbler mouse spinal motoneurons by corticosterone and a 21-aminosteroid

1 reference

12 December 2020

A placebo-controlled trial of recombinant human ciliary neurotrophic (rhCNTF) factor in amyotrophic lateral sclerosis. rhCNTF ALS Study Group

1 reference

12 December 2020

Generalized molecular defects of the neuromuscular junction in skeletal muscle of the wobbler mutant mouse

1 reference

12 December 2020

Molecular profile of reactive astrocytes--implications for their role in neurologic disease

1 reference

12 December 2020

Raised thyrotrophin-releasing hormone, pyroglutamylamino peptidase, and proline endopeptidase are present in the spinal cord of wobbler mice but not in human motor neurone disease

1 reference

12 December 2020

What role(s) for TGFalpha in the central nervous system?

1 reference

12 December 2020

Transforming growth factor alpha (TGF alpha) expression in degenerating motoneurons of the murine mutant wobbler: a neuronal signal for astrogliosis?

1 reference

12 December 2020

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

1 reference

12 December 2020

Localization of the human UGP2 gene encoding the muscle isoform of UDPglucose pyrophosphorylase to 2p13-p14 by fluorescence in situ hybridization

1 reference

12 December 2020

Overexpression of BCL-2 in transgenic mice protects neurons from naturally occurring cell death and experimental ischemia

1 reference

12 December 2020

Involvement of the molecular chaperone Ydj1 in the ubiquitin-dependent degradation of short-lived and abnormal proteins in Saccharomyces cerevisiae

1 reference

12 December 2020

Spinal muscular atrophy gene wobbler of the mouse: evidence from chimeric spinal cord and testis for cell-autonomous function.

1 reference

12 December 2020

Excitatory amino acid receptor antagonist in murine motoneuron disease (the wobbler mouse)

1 reference

12 December 2020

Brain macrophages: neurotoxic or neurotrophic effector cells?

1 reference

12 December 2020

The Fine Structure of the Cervical Spinal Cord, Ventral Root and Brachial Nerves in the Wobbler (WR) Mouse

1 reference

12 December 2020

Motoneuron morphological alterations before and after the onset of the disease in the wobbler mouse.

1 reference

12 December 2020

Plasminogen activators in the neuromuscular system of the wobbler mutant mouse

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12 December 2020

Excitotoxic cell death

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12 December 2020

Alteration in the levels of thyrotropin releasing hormone, substance P and enkephalins in the spinal cord, brainstem, hypothalamus and midbrain of the Wobbler mouse at different stages of the motoneuron disease

1 reference

12 December 2020

Transcriptional networks regulating neuronal identity in the developing spinal cord

1 reference

12 December 2020

The association between neuronal nitric oxide synthase and neuronal sensitivity in the brain after brain injury

1 reference

12 December 2020

Selective inhibitors of neuronal nitric oxide synthase--is no NOS really good NOS for the nervous system?

1 reference

12 December 2020

A comparative study of "denervation" in muscles from mice with inherited progressive neuromuscular disorders

1 reference

12 December 2020

Genetic modifiers that aggravate the neurological phenotype of the wobbler mouse

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12 December 2020

Transient massive DNA fragmentation in nervous system during the early course of a murine neurodegenerative disease

1 reference

12 December 2020

Increased expression of BDNF and trkB mRNA in rat facial motoneurons after axotomy

1 reference

12 December 2020

A low expressor line of transgenic mice carrying a mutant human Cu,Zn superoxide dismutase (SOD1) gene develops pathological changes that most closely resemble those in human amyotrophic lateral sclerosis

1 reference

12 December 2020

The gene for cytoplasmatic malate dehydrogenase, Mor2, is closely linked to the wobbler spinal muscular atrophy gene (wr).

1 reference

12 December 2020

Neuronal specification in the spinal cord: inductive signals and transcriptional codes

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12 December 2020

An hereditary motor neurone disease with progressive denervation of muscle in the mouse: the mutant 'wobbler'.

1 reference

12 December 2020

A role for transforming growth factor alpha as an inducer of astrogliosis.

1 reference

12 December 2020

Phase III randomized trial of gabapentin in patients with amyotrophic lateral sclerosis

1 reference

12 December 2020

Neuronal pathology in the wobbler mouse brain revealed by in vivo proton magnetic resonance spectroscopy and immunocytochemistry.

1 reference

12 December 2020

The wobbler mouse: amino acid contents in brain and spinal cord.

1 reference

12 December 2020

From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS

1 reference

12 December 2020

Development of central nervous system pathology in a murine transgenic model of human amyotrophic lateral sclerosis

1 reference

12 December 2020

Proximal axonal enlargement in motor neuron disease.

1 reference

12 December 2020

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

1 reference

12 December 2020

Impairment of retrograde axonal transport in wobbler mouse motor neuron disease

1 reference

12 December 2020

Sperm tail axoneme alterations in the Wobbler mouse

1 reference

12 December 2020

Lesion of the rat entorhinal cortex leads to a rapid microglial reaction in the dentate gyrus. A light and electron microscopical study

1 reference

12 December 2020

Evidence that brain-derived neurotrophic factor is a trophic factor for motor neurons in vivo.

1 reference

12 December 2020

Assignment of homologous genes, Peli1/PELI1 and Peli2/PELI2, for the Pelle adaptor protein Pellino to mouse chromosomes 11 and 14 and human chromosomes 2p13.3 and 14q21, respectively, by physical and radiation hybrid mapping

1 reference

12 December 2020

In vivo and in vitro muscle tensions in wobbler mouse motor neuron disease

1 reference

12 December 2020

Homology between human chromosome 2p13.3 and the wobbler critical region on mouse chromosome 11: comparative high-resolution mapping of STS and EST loci on YAC/BAC contigs.

1 reference

12 December 2020

The effects of ciliary neurotrophic factor on motor dysfunction in wobbler mouse motor neuron disease

1 reference

12 December 2020

Dynamic association of proteasomal machinery with the centrosome

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12 December 2020

Histometric effects of ciliary neurotrophic factor in wobbler mouse motor neuron disease

1 reference

12 December 2020

Expression of nitric-oxide synthase (NOS) in injured CNS neurons as shown by NADPH diaphorase histochemistry

1 reference

12 December 2020

Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

1 reference

12 December 2020

Pathoanatomy of Parkinson's disease

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12 December 2020

Abnormal RNA metabolism in spinal motor neurons in the wobbler mouse

1 reference

12 December 2020

Ultrastructure of chromatolytic motoneurons and anterior spinal roots in a case of Werdnig-Hoffmann disease.

1 reference

12 December 2020

Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis

1 reference

12 December 2020

Programmed cell death of developing mammalian neurons after genetic deletion of caspases.

1 reference

12 December 2020

Axonal regeneration in wobbler motor neuron disease: quantitative histologic and axonal transport studies

1 reference

12 December 2020

Bcl-2 gene family in the nervous system

1 reference

12 December 2020

Cell death of motoneurons in the chick embryo spinal cord. I. A light and electron microscopic study of naturally occurring and induced cell loss during development

1 reference

12 December 2020

Quantitative autoradiographic distribution of glutamate receptors in the cervical segment of the spinal cord of the wobbler mouse

1 reference

12 December 2020

Amyotrophic lateral sclerosis associated with genetic abnormalities in the gene encoding Cu/Zn superoxide dismutase: molecular pathology of five new cases, and comparison with previous reports and 73 sporadic cases of ALS.

1 reference

12 December 2020

Chaperones Hsp70 and Hsp40 suppress aggregate formation and apoptosis in cultured neuronal cells expressing truncated androgen receptor protein with expanded polyglutamine tract

1 reference

12 December 2020

Cell birth, cell death, cell diversity and DNA breaks: how do they all fit together?

1 reference

12 December 2020

A double-blind placebo-controlled clinical trial of subcutaneous recombinant human ciliary neurotrophic factor (rHCNTF) in amyotrophic lateral sclerosis. ALS CNTF Treatment Study Group

1 reference

12 December 2020

Quantitative measurement of muscle strength in the mouse

1 reference

12 December 2020

A novel behavioral method to detect motoneuron disease in Wobbler mice aged three to seven days old.

1 reference

12 December 2020

Bcl-2 sensitivity differentiates two pathways for motoneuronal death in the wobbler mutant mouse

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12 December 2020

Early detection of mouse wobbler mutation: a model of pathological motoneurone death

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12 December 2020

Oxidative processes and antioxidative defense mechanisms in the aging brain

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12 December 2020

Changes in receptor levels for thyrotropin releasing hormone, serotonin, and substance P in cervical spinal cord of Wobbler mouse: a quantitative autoradiography study during early and late stages of the motoneuron disease.

1 reference

12 December 2020

Excitotoxicity hypothesis

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12 December 2020

Of mice, men and motor neurons

1 reference

12 December 2020

Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II

1 reference

12 December 2020

Early and selective pathology of light chain neurofilament in the spinal cord and sciatic nerve of G86R mutant superoxide dismutase transgenic mice

1 reference

12 December 2020

Regeneration in the CNS: optimism mounts.

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12 December 2020

Mechanisms of programmed cell death in the developing brain

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12 December 2020

Mouse U2af1-rs1 is a neomorphic imprinted gene

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12 December 2020

MSJ-1, a new member of the DNAJ family of proteins, is a male germ cell-specific gene product.

1 reference

12 December 2020

Mouse sperm cell-specific DnaJ first homologue: an evolutionarily conserved protein for spermiogenesis.

1 reference

12 December 2020

Genetic transfer of the wobbler gene to a C57BL/6J x NZB hybrid stock: natural history of the motor neuron disease and response to CNTF and BDNF cotreatment.

1 reference

12 December 2020

A placebo-controlled trial of insulin-like growth factor-I in amyotrophic lateral sclerosis. European ALS/IGF-I Study Group

1 reference

12 December 2020

Glutamate transporters in the spinal cord of the wobbler mouse

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12 December 2020

Genetic interactions between KAR2 and SEC63, encoding eukaryotic homologues of DnaK and DnaJ in the endoplasmic reticulum

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12 December 2020

Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis

1 reference

12 December 2020

Neuroprotective effect of cholinergic differentiation factor/leukemia inhibitory factor on wobbler murine motor neuron disease

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12 December 2020

Glial changes following an excitotoxic lesion in the CNS—I. Microglia/macrophages

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12 December 2020

Modulation of intracellular protein degradation by SSB1-SIS1 chaperon system in yeast S. cerevisiae.

1 reference

12 December 2020

Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis

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12 December 2020

Axotomy induces NADPH diaphorase activity in neonatal but not adult motoneurones.

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12 December 2020

Progressive neuronopathy in transgenic mice expressing the human neurofilament heavy gene: a mouse model of amyotrophic lateral sclerosis

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12 December 2020

Arrest of motor neuron disease in wobbler mice cotreated with CNTF and BDNF

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12 December 2020

Neuron volume in the ventral horn in Wobbler mouse motoneuron disease: a light microscope stereological study

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12 December 2020

Effects of low doses of glycosaminoglycans and insulin-like growth factor-I on motor neuron disease in wobbler mouse

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12 December 2020

Proopiomelanocortin-derived peptides in mice with motoneurone disease

1 reference

12 December 2020

Implantation of PNS Graft Inhibits the Induction of Neuronal Nitric Oxide Synthase and Enhances the Survival of Spinal Motoneurons Following Root Avulsion

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12 December 2020

Quantitative light and electron microscopic studies on the ventral roots of the wobbler mutant mouse

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12 December 2020

Studies on a murine form of spontaneous lower motor neuron degeneration--the wobbler (wa) mouse

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12 December 2020

Tetramethyl benzidine for horseradish peroxidase neurohistochemistry: a non-carcinogenic blue reaction product with superior sensitivity for visualizing neural afferents and efferents

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12 December 2020

Neuroprotective effect of basic fibroblast growth factor on wobbler mouse motor neuron disease

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12 December 2020

Quantitative reverse transcriptase PCR to gauge increased protease-activated receptor 1 (PAR-1) mRNA copy numbers in the Wobbler mutant mouse

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12 December 2020

Defect of sperm assembly in a neurological mutant of the mouse, wobbler (WR).

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12 December 2020

Reduction of lower motor neuron degeneration in wobbler mice by N-acetyl-L-cysteine

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12 December 2020

Differential regulation of motor neuron survival and choline acetyltransferase expression following axotomy

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12 December 2020

Ubiquitin in neurodegenerative diseases

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12 December 2020

Mutations in Hsp83 and cdc37 impair signaling by the sevenless receptor tyrosine kinase in Drosophila.

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12 December 2020

Neuron-specific expression of mutant superoxide dismutase 1 in transgenic mice does not lead to motor impairment.

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12 December 2020

The mouse mutation muscle deficient (mdf) is characterized by a progressive motoneuron disease

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12 December 2020

T-588, a novel neuroprotective agent, delays progression of neuromuscular dysfunction in wobbler mouse motoneuron disease

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12 December 2020

Muscle lactate dehydrogenase activity is decreased in murine motor neuron disease

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12 December 2020

Role of the protein chaperone YDJ1 in establishing Hsp90-mediated signal transduction pathways

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12 December 2020

Astrocytosis in wobbler mouse spinal cord involves a population of astrocytes which is glutamine synthetase-negative.

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12 December 2020

Otx genes in the development and evolution of the vertebrate brain.

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12 December 2020

The molecular bases of spinal muscular atrophy

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12 December 2020

Motor neuron cell death in wobbler mutant mice follows overexpression of the G-protein-coupled, protease-activated receptor for thrombin

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12 December 2020

A therapeutic trial of gangliosides and thymosin in the Wobbler mouse model of motor neuron disease

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12 December 2020

TRPM-2 expression and tunel staining in neurodegenerative diseases: studies in wobbler and rd mice

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12 December 2020

Reduced protein synthesis in spinal anterior horn neurons in wobbler mouse mutant

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12 December 2020

DnaJ-like proteins: molecular chaperones and specific regulators of Hsp70.

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12 December 2020

Loss of motor neurons from the median nerve motor nucleus of the mutant mouse 'wobbler'

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12 December 2020

Spiny interneurons identified in the normal mouse spinal cord show alterations in the Wobbler mouse: a model for inherited motoneuron disease

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12 December 2020

Early upregulation of medium neurofilament gene expression in developing spinal cord of the wobbler mouse mutant.

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12 December 2020

Cutting edge: mouse pellino-2 modulates IL-1 and lipopolysaccharide signaling

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12 December 2020

Bip/GRP78 but not calnexin associates with a precursor of glycosylphosphatidylinositol-anchored protein

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12 December 2020

Dependence of postnatal motoneurones on their targets: review and hypothesis

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12 December 2020

The gene encoding alsin, a protein with three guanine-nucleotide exchange factor domains, is mutated in a form of recessive amyotrophic lateral sclerosis

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12 December 2020

Influence of factors secreted by wobbler astrocytes on neuronal and motoneuronal survival

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12 December 2020

Differential microglial response to progressive neurodegeneration in the murine mutant Wobbler

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12 December 2020

Superoxide dismutase in familial amyotrophic lateral sclerosis: models for gain of function

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12 December 2020

The lethal mutation of the mouse wasted (wst) is a deletion that abolishes expression of a tissue-specific isoform of translation elongation factor 1alpha, encoded by the Eef1a2 gene

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12 December 2020

The Bcl2 family: regulators of the cellular life-or-death switch

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12 December 2020

Wobbler, a mutation affecting motoneuron survival and gonadal functions in the mouse, maps to proximal chromosome 11

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12 December 2020

Thyrotropin-releasing hormone (TRH) neurons sprout in cervical spinal cord of Wobbler mouse

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12 December 2020

Roles of molecular chaperones in protein degradation

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12 December 2020

Effects of assisted feeding on Wobbler mouse motoneuron disease and on serotonergic and peptidergic sprouting in the cervical spinal ventral horn

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12 December 2020

Thyrotropin-releasing hormone (TRH) in murine motor neuron disease (the wobbler mouse).

1 reference

12 December 2020

Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis

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12 December 2020

Suppression of polyglutamine-mediated neurodegeneration in Drosophila by the molecular chaperone HSP70.

1 reference

12 December 2020

The 21-aminosteroid U-74389F attenuates hyperexpression of GAP-43 and NADPH-diaphorase in the spinal cord of wobbler mouse, a model for amyotrophic lateral sclerosis

1 reference

12 December 2020

A simple method for organotypic cultures of nervous tissue

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12 December 2020

Decrease of enkephalins in cerebellum during Wobbler mouse motoneuron disease

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12 December 2020

Lou Gehrig and amyotrophic lateral sclerosis. Is vitamin E to be revisited?

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12 December 2020

Regionalized neurofilament accumulation and motoneuron degeneration are linked phenotypes in wobbler neuromuscular disease

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12 December 2020

Regulation of Growth Factor Gene Expression in Degenerating Motoneurons of the Murine Mutantwobbler: A Cellular Patch-Sampling/RT–PCR Study

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12 December 2020

Expression of nitric oxide synthase by motor neurones in the spinal cord of the mutant mouse wobbler

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12 December 2020

Lecithinized superoxide dismutase retards wobbler mouse motoneuron disease

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12 December 2020

YAC contigs of the Rab1 and wobbler (wr) spinal muscular atrophy gene region on proximal mouse chromosome 11 and of the homologous region on human chromosome 2p

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12 December 2020

Role of brain-derived neurotrophic factor in wobbler mouse motor neuron disease

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12 December 2020

Microglia: a sensor for pathological events in the CNS

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12 December 2020

Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS).

1 reference

12 December 2020

Thrombin perturbs neurite outgrowth and induces apoptotic cell death in enriched chick spinal motoneuron cultures through caspase activation

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12 December 2020

Neurodegeneration: new clues on inclusions

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12 December 2020

Developmental cell death: morphological diversity and multiple mechanisms

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12 December 2020

Neuronal nitric oxide synthase inhibitor, 7-nitroindazole, delays motor dysfunction and spinal motoneuron degeneration in the wobbler mouse.

1 reference

12 December 2020

Effect of recombinant human insulin-like growth factor-I on progression of ALS. A placebo-controlled study. The North America ALS/IGF-I Study Group

1 reference

12 December 2020

Coadministration of interleukin-6 (IL-6) and soluble IL-6 receptor delays progression of wobbler mouse motor neuron disease.

1 reference

12 December 2020

Restricted expression of G86R Cu/Zn superoxide dismutase in astrocytes results in astrocytosis but does not cause motoneuron degeneration

1 reference

12 December 2020

Cytoskeletal pathology in motor neuron diseases

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12 December 2020

Mechanisms of selective motor neuron death in ALS: insights from transgenic mouse models of motor neuron disease

1 reference

12 December 2020

Identification and characterization of a spinal muscular atrophy-determining gene

1 reference

12 December 2020

The loss of motorneurons corresponding to specific muscles in the wobbler mutant mouse

1 reference

12 December 2020

Characterization of immunologic and neuropathologic abnormalities in wasted mice

1 reference

12 December 2020

A controlled trial of riluzole in amyotrophic lateral sclerosis. ALS/Riluzole Study Group

1 reference

12 December 2020

Reactive mononuclear phagocytes release neurotoxins after ischemic and traumatic injury to the central nervous system

1 reference

12 December 2020

Neuronal nitric oxide synthase is induced in spinal neurons by traumatic injury

1 reference

12 December 2020

Analysis of the role of heat shock protein (Hsp) molecular chaperones in polyglutamine disease

1 reference

12 December 2020

Abnormal neuromuscular junctions in the lateral rectus muscle of wobbler mice

1 reference

12 December 2020

In vitro differences between astrocytes of control and wobbler mice spinal cord

1 reference

12 December 2020

JTP-2942, a novel thyrotropin-releasing hormone analogue, protects against spinal motor neuron degeneration in the wobbler mouse

1 reference

12 December 2020

Reactive microgliosis

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12 December 2020

Mutant Cu/Zn-superoxide dismutase proteins have altered solubility and interact with heat shock/stress proteins in models of amyotrophic lateral sclerosis

1 reference

12 December 2020

Astrocyte proliferation induced by wobbler astrocyte conditioned medium is blocked by tumor necrosis factor-alpha (TNF-alpha) and interleukin-1beta (IL-1beta) neutralizing antibodies in vitro

1 reference

12 December 2020

Beneficial effects of insulin-like growth factor-I on wobbler mouse motoneuron disease

1 reference

12 December 2020

Heterogeneity of the glial fibrillary acidic protein in gliosed human brains.

1 reference

12 December 2020

Expression of nerve-regulated genes in muscles of mouse mutants affected by spinal muscular atrophies and muscular dystrophies.

1 reference

12 December 2020

Alterations in contractile properties and expression of myofibrillar proteins in wobbler mouse muscles

1 reference

12 December 2020

Neurotrophins promote motor neuron survival and are present in embryonic limb bud.

1 reference

12 December 2020

Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases

1 reference

12 December 2020

Studies on the localization of the lesion in the Wobbler mutant mouse [proceedings]

1 reference

12 December 2020

Vacuolated anterior horn cells in wobbler mouse motor neuron disease: peripheral axons and regenerative capacity

1 reference

12 December 2020

POMC neuropeptides and their receptors in the neuromuscular system of wobbler mice

1 reference

12 December 2020

The selective vulnerability of nerve cells in Huntington's disease

1 reference

12 December 2020

Decreased Spinal Cord cGMP in Murine (Wobbler) Spontaneous Lower Motor Neuron Degeneration

1 reference

12 December 2020

Ablation of NF1 function in neurons induces abnormal development of cerebral cortex and reactive gliosis in the brain

1 reference

12 December 2020

Astrocyte responses to CNS injury

1 reference

12 December 2020

Extracellular matrix degradation by metalloproteinases and central nervous system diseases

1 reference

12 December 2020

Identifiers

DOI

10.1385/MN:28:1:65

1 reference

Dimensions Publication ID

25 July 2017

1032041335

0 references

1 reference