VWF73, a region from D1596 to R1668 of von Willebrand factor, provides a minimal substrate for ADAMTS-13 (Q33356956)

26 July 2017

VWF73, a region from D1596 to R1668 of von Willebrand factor, provides a minimal substrate for ADAMTS-13 (English)

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https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

author name string

Koichi Kokame

1

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26 July 2017

Masanori Matsumoto

2

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26 July 2017

Yoshihiro Fujimura

3

1 reference

26 July 2017

Toshiyuki Miyata

4

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26 July 2017

language of work or name

English

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publication date

25 September 2003

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full work available at URL

26 July 2017

published in

Blood

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26 July 2017

103

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26 July 2017

2

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26 July 2017

607-612

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Upshaw-Schulman syndrome revisited: a concept of congenital thrombotic thrombocytopenic purpura

26 July 2017

2

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Von Willebrand factor: molecular size and functional activity

14 March 2024

4

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

von Willebrand factor

5

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https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Biochemistry and genetics of von Willebrand factor

14 March 2024

6

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https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Processing of von Willebrand factor by ADAMTS-13.

14 March 2024

7

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Von Willebrand factor-cleaving protease and Upshaw-Schulman syndrome

14 March 2024

8

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

ADAMTS13 and TTP

10

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https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Platelet activation and the formation of the platelet plug: deficiency of ADAMTS13 causes thrombotic thrombocytopenic purpura

14 March 2024

11

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Binding of von Willebrand factor to glycoproteins Ib and IIb/IIIa complex: affinity is related to multimeric size

14 March 2024

13

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura

14 March 2024

14

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity

14 March 2024

15

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

von Willebrand factor cleaving protease and ADAMTS13 mutations in childhood TTP.

14 March 2024

16

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

ADAMTS13 gene mutation in congenital thrombotic thrombocytopenic purpura with previously reported normal VWF cleaving protease activity

14 March 2024

17

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

ADAMTS13 gene defects in two brothers with constitutional thrombotic thrombocytopenic purpura and normalization of von Willebrand factor-cleaving protease activity by recombinant human ADAMTS13.

14 March 2024

18

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome

14 March 2024

19

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura

14 March 2024

20

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family

14 March 2024

21

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Partial amino acid sequence of purified von Willebrand factor-cleaving protease

14 March 2024

22

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

A novel human metalloprotease synthesized in the liver and secreted into the blood: possibly, the von Willebrand factor-cleaving protease?

14 March 2024

23

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura

14 March 2024

24

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Cloning, expression, and functional characterization of the von Willebrand factor-cleaving protease (ADAMTS13).

14 March 2024

25

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Cloning, expression analysis, and structural characterization of seven novel human ADAMTSs, a family of metalloproteinases with disintegrin and thrombospondin-1 domains

14 March 2024

26

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Cleavage of von Willebrand factor requires the spacer domain of the metalloprotease ADAMTS13.

14 March 2024

27

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

ADAMTS-13 cysteine-rich/spacer domains are functionally essential for von Willebrand factor cleavage

14 March 2024

28

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Identification of a cleavage site directing the immunochemical detection of molecular abnormalities in type IIA von Willebrand factor

14 March 2024

29

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Von Willebrand factor-cleaving protease (ADAMTS13) in thrombocytopenic disorders: a severely deficient activity is specific for thrombotic thrombocytopenic purpura

14 March 2024

33

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Is severe deficiency of ADAMTS-13 specific for thrombotic thrombocytopenic purpura? Yes

14 March 2024

34

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Ticlopidine-Associated thrombotic thrombocytopenic purpura with an IgG-type inhibitor to von Willebrand factor-cleaving protease activity

14 March 2024

35

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Simple plasma exchange reduced autoantibody to von Willebrand factor-cleaving protease in a Japanese man with ticlopidine-associated thrombotic thrombocytopenic purpura

14 March 2024

36

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Predicting response to plasma exchange in patients with thrombotic thrombocytopenic purpura with measurement of vWF-cleaving protease activity

14 March 2024

37

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Evaluation and clinical application of a new method for measuring activity of von Willebrand factor-cleaving metalloprotease (ADAMTS13).

14 March 2024

40

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Assays of von Willebrand factor-cleaving protease: a test for diagnosis of familial and acquired thrombotic thrombocytopenic purpura

14 March 2024

41

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

Decreased levels of von Willebrand factor-cleaving protease in coronary heart disease and thrombotic thrombocytopenic purpura: study of a simplified method for assaying the enzyme activity based on ristocetin-induced platelet aggregation

14 March 2024

42

1 reference

https://api.crossref.org/works/10.1182/BLOOD-2003-08-2861

14 March 2024

Identifiers

1 reference

26 July 2017

1 reference