Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth (Q33929671)

30 July 2017

Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth (English)

1 reference

eradication of infectious diseases

30 July 2017

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1 reference

Alejandro A Pezzulo

3

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Lynda S Ostedgaard

Lynda S Ostedgaard

21

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Joel Shilyansky

Joel Shilyansky

28

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David Stoltz

David A Stoltz

1

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David Meyerholz

David K Meyerholz

2

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Paul B McCray

Paul B McCray

29

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Randall S. Prather

Randall S Prather

26

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Timothy D Starner

Timothy D Starner

23

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Aliye Uc

Aliye Uc

22

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Joseph Zabner

Joseph Zabner

30

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Alexander R Horswill

24

Alexander R Horswill

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30 July 2017

Shyam Ramachandran

4

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Mark P Rogan

5

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Greg J Davis

6

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Robert A Hanfland

7

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30 July 2017

Chris Wohlford-Lenane

8

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Cassie L Dohrn

9

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Jennifer A Bartlett

10

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George A Nelson

11

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Eugene H Chang

12

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Peter J Taft

13

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Paula S Ludwig

14

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Mira Estin

15

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Emma E Hornick

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Janice L Launspach

17

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30 July 2017

Melissa Samuel

18

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Tatiana Rokhlina

19

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Philip H Karp

20

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Kim A Brogden

25

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Sandra S Richter

27

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Michael J Welsh

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language of work or name

English

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publication date

1 April 2010

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Science Translational Medicine

30 July 2017

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2

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29

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29ra31

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Pathology of gastrointestinal organs in a porcine model of cystic fibrosis

30 July 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Respiratory microbiology of patients with cystic fibrosis in the United States, 1995 to 2005.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Molecular identification of bacteria in bronchoalveolar lavage fluid from children with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammation in cystic fibrosis--when and why? Friend or foe?

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Microbial ecology of the cystic fibrosis lung

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

CFTR inhibition mimics the cystic fibrosis inflammatory profile

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Digitoxin mimics gene therapy with CFTR and suppresses hypersecretion of IL-8 from cystic fibrosis lung epithelial cells

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

State of the Art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection?

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Activation of NF-kappaB in airway epithelial cells is dependent on CFTR trafficking and Cl- channel function

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammation and infection in naive human cystic fibrosis airway grafts

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Cystic fibrosis and the salt controversy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Pathophysiology of gene-targeted mouse models for cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Severe viral respiratory infections in infants with cystic fibrosis.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Repeat administration of an adenovirus vector encoding cystic fibrosis transmembrane conductance regulator to the nasal epithelium of patients with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Genetic systems in staphylococci

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Management and survival of meconium ileus. A 30-year review

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammatory response in airway epithelial cells isolated from patients with cystic fibrosis.

5 July 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

Lower airway inflammation in infants with cystic fibrosis detected by newborn screening.

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

Physiological basis of cystic fibrosis: a historical perspective

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Hemorrhagic gastroesophageal ulceration by pulmonary infection in extrahepatic cholestatic pigs.

29 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis

29 October 2018

1 reference

12 December 2020

Early pulmonary inflammation in infants with cystic fibrosis

1 reference

12 December 2020

Prevalence and antimicrobial susceptibility of microorganisms isolated from sputa of patients with cystic fibrosis

1 reference

12 December 2020

Observations in cystic fibrosis of the pancreas. 3. Pulmonary lesions

1 reference

12 December 2020

1 reference

12 December 2020

10.1126/SCITRANSLMED.3000928

Identifiers

DOI

1 reference

30 July 2017

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30 July 2017

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