Stimulation of lysosomal sphingomyelin degradation by sphingolipid activator proteins (Q34042889)

30 July 2017

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title

Stimulation of lysosomal sphingomyelin degradation by sphingolipid activator proteins (English)

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30 July 2017

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Ferlinz K

1

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30 July 2017

Linke T

2

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30 July 2017

Bartelsen O

3

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30 July 2017

Weiler M

4

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30 July 2017

Sandhoff K

5

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30 July 2017

1 November 1999

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Chemistry and Physics of Lipids

30 July 2017

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30 July 2017

102

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30 July 2017

1-2

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30 July 2017

35-43

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Expression of recombinant human acid sphingomyelinase in insect Sf21 cells: purification, processing and enzymatic characterization

30 July 2017

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Prosaposin deficiency: further characterization of the sphingolipid activator protein-deficient sibs. Multiple glycolipid elevations (including lactosylceramidosis), partial enzyme deficiencies and ultrastructure of the skin in this generalized sphi

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Isolation of two forms of an activator protein for the enzymic sphingomyelin degradation from human Gaucher spleen

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Targeted disruption of the mouse sphingolipid activator protein gene: a complex phenotype, including severe leukodystrophy and wide-spread storage of multiple sphingolipids.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Activator proteins and topology of lysosomal sphingolipid catabolism.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Interaction of the GM2-activator protein with phospholipid-ganglioside bilayer membranes and with monolayers at the air-water interface

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Lysosomal storage diseases

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Functional role of glycosphingolipids in cell recognition and signaling

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Sphingolipid activator protein deficiency in a 16-week-old atypical Gaucher disease patient and his fetal sibling: biochemical signs of combined sphingolipidoses

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Cellular uptake of saposin (SAP) precursor and lysosomal delivery by the low density lipoprotein receptor-related protein (LRP).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Cloning of a human acid sphingomyelinase cDNA with a new mutation that renders the enzyme inactive

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

A lipid associated with the antiphospholipid syndrome regulates endosome structure and function

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Biochemistry of glycosphingolipid degradation

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Purification of acid sphingomyelinase from human placenta: characterization and N-terminal sequence

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Mouse model of GM2 activator deficiency manifests cerebellar pathology and motor impairment

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Saposin D: a sphingomyelinase activator

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Additional biochemical findings in a patient and fetal sibling with a genetic defect in the sphingolipid activator protein (SAP) precursor, prosaposin. Evidence for a deficiency in SAP-1 and for a normal lysosomal neuraminidase

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Acid sphingomyelinase possesses a domain homologous to its activator proteins: saposins B and D

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Studies on the activation of the enzymatic hydrolysis of sphingomyelin liposomes.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Isolation of cDNA clones encoding human acid sphingomyelinase: occurrence of alternatively processed transcripts

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Signal transduction through lipid second messengers

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Effect of saposins on acid sphingomyelinase

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Biosynthesis, processing, and targeting of sphingolipid activator protein (SAP )precursor in cultured human fibroblasts. Mannose 6-phosphate receptor-independent endocytosis of SAP precursor

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Lysosomal degradation on vesicular membrane surfaces. Enhanced glucosylceramide degradation by lysosomal anionic lipids and activators.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

Immunochemical characterization of two activator proteins stimulating enzymic sphingomyelin degradation in vitro. Absence of one of them in a human Gaucher disease variant

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0009-3084%2899%2900073-0

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7 January 2021

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Identifiers

DOI

10.1016/S0009-3084(99)00073-0

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30 July 2017

1 reference