Is cystic fibrosis lung disease caused by abnormal ion composition or abnormal volume? (Q34322971)

1 August 2017

7 references

13 March 2019

21 March 2019

22 April 2019

19 September 2019

4 November 2019

28 January 2021

6 February 2021

Is cystic fibrosis lung disease caused by abnormal ion composition or abnormal volume? (English)

1 reference

biomedical investigative technique

1 August 2017

6 references

13 March 2019

21 March 2019

22 April 2019

19 September 2019

4 November 2019

28 January 2021

5 references

13 March 2019

21 March 2019

22 April 2019

19 September 2019

4 November 2019

1 reference

19 September 2019

1 reference

4 November 2019

1 reference

6 February 2021

M E Krouse

1

1 reference

1 August 2017

publication date

1 August 2001

8 references

The Journal of General Physiology

1 August 2017

13 March 2019

21 March 2019

22 April 2019

19 September 2019

4 November 2019

28 January 2021

6 February 2021

8 references

1 August 2017

13 March 2019

21 March 2019

22 April 2019

19 September 2019

4 November 2019

28 January 2021

6 February 2021

118

1 reference

1 August 2017

issue

2

1 reference

1 August 2017

page(s)

219-222

1 reference

The relative roles of passive surface forces and active ion transport in the modulation of airway surface liquid volume and composition

1 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Antimicrobial peptides and proteins in the innate defense of the airway surface

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Osmotic water permeabilities of cultured, well-differentiated normal and cystic fibrosis airway epithelia

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Molecular insights into the physiology of the 'thin film' of airway surface liquid

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Gating of cystic fibrosis transmembrane conductance regulator chloride channels by adenosine triphosphate hydrolysis. Quantitative analysis of a cyclic gating scheme

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

The genesis of cystic fibrosis lung disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Salt and water transport across alveolar and distal airway epithelia in the adult lung

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Altered fluid transport across airway epithelium in cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Defective fluid transport by cystic fibrosis airway epithelia

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

ATP alters current fluctuations of cystic fibrosis transmembrane conductance regulator: evidence for a three-state activation mechanism

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Regulation of the gating of cystic fibrosis transmembrane conductance regulator C1 channels by phosphorylation and ATP hydrolysis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Abnormal respiratory epithelial ion transport in cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Nucleoside triphosphates are required to open the CFTR chloride channel.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

Elemental composition of human airway surface fluid in healthy and diseased airways

6 July 2018

1 reference

Crossref

https://api.crossref.org/works/10.1085%2FJGP.118.2.219

Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1085%2FJGP.118.2.219

Physiological basis of cystic fibrosis: a historical perspective

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2233826

28 October 2018

1 reference

https://api.crossref.org/works/10.1085%2FJGP.118.2.219

Lung disease in cystic fibrosis: is airway surface liquid composition abnormal?

21 January 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/11479348

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1085/JGP.118.2.219

1 reference

1 August 2017

1 reference

1 August 2017

1 reference