Progress in clinical neurosciences: the evidence for ALS as a multisystems disorder of limited phenotypic expression. (Q34477724)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

review article

1 reference

title

Progress in clinical neurosciences: the evidence for ALS as a multisystems disorder of limited phenotypic expression (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

amyotrophic lateral sclerosis

5 December 2019

main subject

1 reference

1 reference

ORCID Public Data File 2021

author name string

M J Strong

series ordinal

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

publication date

1 November 2001

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

Canadian Journal of Neurological Sciences

5 December 2019

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

volume

28

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

issue

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

page(s)

283-298

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

Cholinesterase inhibitors lack therapeutic effect in amyotrophic lateral sclerosis. A controlled study of physostigmine versus neostigmine.

5 December 2019

cites work

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A double-blind, placebo-controlled trial of TRH in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A double-blind placebo-controlled clinical trial of subcutaneous recombinant human ciliary neurotrophic factor (rHCNTF) in amyotrophic lateral sclerosis. ALS CNTF Treatment Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A double-blind placebo-controlled trial ofl-threonine in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis: a double-blind crossover trial of thyrotropin-releasing hormone

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Trial of oral physostigmine in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cerebral blood flow and oxygen metabolism in progressive dementia associated with amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Functional and pharmacokinetic studies of tetrahydroaminoacridine in patients with amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Ultrastructural evidence for altered calcium in motor nerve terminals in amyotropic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

An analysis of extended survival in patients with amyotrophic lateral sclerosis treated with riluzole

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Elevation of the neurotoxin quinolinic acid occurs following spinal cord trauma.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Chronic inhibition of glutamate uptake produces a model of slow neurotoxicity

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Mitochondria in sporadic amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Plasmapheresis with immunosuppression in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Caspase-1 and -3 are sequentially activated in motor neuron death in Cu,Zn superoxide dismutase-mediated familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Murine brain macrophages induced NMDA receptor mediated neurotoxicity in vitro by secreting glutamate

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Selegiline is ineffective in a collaborative double-blind, placebo-controlled trial for treatment of amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Functional and morphometric study of the liver in motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Treatment of the adult retina with microglia-suppressing factors retards axotomy-induced neuronal degradation and enhances axonal regeneration in vivo and in vitro.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cytotoxic Effect of Brain Macrophages on Developing.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Studies of the coding region of the neuronal glutamate transporter gene in amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neurofilament light and polyadenylated mRNA levels are decreased in amyotrophic lateral sclerosis motor neurons

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Placebo-controlled trial of gabapentin in patients with amyotrophic lateral sclerosis. WALS Study Group. Western Amyotrophic Lateral Sclerosis Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Presenile dementia with motor neuron disease in Japan: clinico-pathological review of 26 cases

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis and its association with dementia, parkinsonism and other neurological disorders: a review

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Hepatic ultrastructural changes and liver dysfunction in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Increased 3-nitrotyrosine and oxidative damage in mice with a human copper/zinc superoxide dismutase mutation.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superox

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Assembly of type IV neuronal intermediate filaments in nonneuronal cells in the absence of preexisting cytoplasmic intermediate filaments

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Rapidly progressive aphasic dementia and motor neuron disease.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Reactive microglia in cerebral ischaemia: an early mediator of tissue damage?

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cost effectiveness of recombinant human insulin-like growth factor I therapy in patients with ALS.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Selective loss of glial glutamate transporter GLT-1 in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neuron disease and adult hexosaminidase A deficiency in two families: evidence for multisystem degeneration.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neurofilaments are obligate heteropolymers in vivo

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Apparent hydroxyl radical production by peroxynitrite: implications for endothelial injury from nitric oxide and superoxide

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Variants of the heavy neurofilament subunit are associated with the development of amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Blood superoxide dismutase, catalase and glutathione peroxidase activities in familial and sporadic amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Oxidative damage to protein in sporadic motor neuron disease spinal cord

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Alterations of skin glycosaminoglycans in patients with ALS.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The role of calcium-binding proteins in selective motoneuron vulnerability in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Intracellular calcium parallels motoneuron degeneration in SOD-1 mutant mice.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The relationship between abnormalities of cognitive function and cerebral activation in amyotrophic lateral sclerosis. A neuropsychological and positron emission tomography study.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Plasmapheresis in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Controlled trial of thyrotropin releasing hormone in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neurons are selectively vulnerable to AMPA/kainate receptor-mediated injury in vitro

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Polymorphisms in the glutamate transporter gene EAAT2 in European ALS patients

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis and structural defects in Cu,Zn superoxide dismutase

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic Lateral Sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Microglial cells prevent nitric oxide-induced neuronal apoptosis in vitro

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Selective impairment of verb processing associated with pathological changes in Brodmann areas 44 and 45 in the motor neurone disease-dementia-aphasia syndrome.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The new neuropathology of degenerative frontotemporal dementias

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis and parkinsonism-dementia of Gaum: Clinical, epidemiological, and genetic patterns.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Trial of immunosuppression in amyotrophic lateral sclerosis using total lymphoid irradiation

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Hippocampal and neocortical ubiquitin-immunoreactive inclusions in amyotrophic lateral sclerosis with dementia

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A long surviving case of amyotrophic lateral sclerosis with atrophy of the frontal lobe: a comparison with the Mitsuyama type

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Linkage of a gene causing familial amyotrophic lateral sclerosis to chromosome 21 and evidence of genetic-locus heterogeneity

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Prevalence and correlates of neuropsychological deficits in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Increased expression of neurofilament subunit NF-L produces morphological alterations that resemble the pathology of human motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neuron disease in England and Wales, 1959-1979

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neuropsychological, electroencephalogram and brain computed tomography findings in motor neuron disease.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Branched-chain amino acids and amyotrophic lateral sclerosis: a treatment failure? The Italian ALS Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Reversibility of neurofilamentous inclusion formation following repeated sublethal intracisternal inoculums of AlCl3 in New Zealand white rabbits

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis: oxidative energy metabolism and calcium homeostasis in peripheral blood lymphocytes.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Epidemiologic study of amyotrophic lateral sclerosis in Sardinia, Italy.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Total manifestations of amyotrophic lateral sclerosis. ALS in the totally locked-in state

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Novel insertion in the KSP region of the neurofilament heavy gene in amyotrophic lateral sclerosis (ALS)

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A positron emission tomography study of frontal lobe function (verbal fluency) in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Progressive proximal spinal and bulbar muscular atrophy of late onset. A sex-linked recessive trait

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Evidence of increased oxidative damage in both sporadic and familial amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neuropsychological study of motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Longitudinal Gompertzian analysis of amyotrophic lateral sclerosis mortality in the U.S., 1977-1986: evidence for an inherently susceptible population subset

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The incidence of amyotrophic lateral sclerosis in southwestern Ontario, Canada

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Phosphorylation state of the native high-molecular-weight neurofilament subunit protein from cervical spinal cord in sporadic amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Impairment of mitochondrial function in skeletal muscle of patients with amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A prospective study of cognitive impairment in ALS

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Familial amyotrophic lateral sclerosis with a mutation in the Cu/Zn superoxide dismutase gene.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

An investigation into the early stages of the inflammatory response following ibotenic acid-induced neuronal degeneration.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Analysis of the KSP repeat of the neurofilament heavy subunit in familiar amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Androgen receptor gene mutations in X-linked spinal and bulbar muscular atrophy

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A placebo-controlled trial of insulin-like growth factor-I in amyotrophic lateral sclerosis. European ALS/IGF-I Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Calcium dynamics and buffering in oculomotor neurones from mouse that are particularly resistant during amyotrophic lateral sclerosis (ALS)-related motoneurone disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Decreased cytochrome c oxidase activity but unchanged superoxide dismutase and glutathione peroxidase activities in the spinal cords of patients with amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Adult onset motor neuronopathy in the juvenile type of hexosaminidase A and B deficiency

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis associated with homozygosity for an Asp90Ala mutation in CuZn-superoxide dismutase

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Glutamatergic receptors regulate expression, phosphorylation and accumulation of neurofilaments in spinal cord neurons

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Characterization of neuronal intermediate filament protein expression in cervical spinal motor neurons in sporadic amyotrophic lateral sclerosis (ALS).

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Clinical characteristics of a family with chromosome 17-linked disinhibition-dementia-parkinsonism-amyotrophy complex.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cognitive impairment in sporadic ALS: a pathologic continuum underlying a multisystem disorder

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

New ubiquitin-positive intraneuronal inclusions in the extra-motor cortices in patients with amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cognitive deficits in non-demented amyotrophic lateral sclerosis patients: a neuropsychological investigation.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Contributions of anterior cingulate cortex to behaviour

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis: effects of acute intravenous and chronic subcutaneous administration of thyrotropin-releasing hormone in controlled trials

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Elevated "hydroxyl radical" generation in vivo in an animal model of amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Linkage of recessive familial amyotrophic lateral sclerosis to chromosome 2q33-q35.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Superoxide dismutase catalyzes nitration of tyrosines by peroxynitrite in the rod and head domains of neurofilament-L.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Major histocompatibility complex antigen expression in the affected tissues in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Immunocytochemical study of the distribution of the free radical scavenging enzymes CU/ZN superoxide dismutase (SOD1); MN superoxide dismutase (MN SOD) and catalase in the normal human spinal cord and in motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Down-regulation of copper/zinc superoxide dismutase causes apoptotic death in PC12 neuronal cells

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Decreased zinc affinity of amyotrophic lateral sclerosis-associated superoxide dismutase mutants leads to enhanced catalysis of tyrosine nitration by peroxynitrite

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

c-Jun, JNK/SAPK kinases and transcription factor NF-kappa B are selectively activated in astrocytes, but not motor neurons, in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Late onset of motor neurons in mice overexpressing wild-type peripherin

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The EAAT2 (GLT-1) gene in motor neuron disease: absence of mutations in amyotrophic lateral sclerosis and a point mutation in patients with hereditary spastic paraplegia

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Cognition, language, and speech in amyotrophic lateral sclerosis: a review.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Familial amyotrophic lateral sclerosis. A subgroup characterized by posterior and spinocerebellar tract involvement and hyaline inclusions in the anterior horn cells

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The mortality of motor neuron disease in Sweden.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Functional Role of Caspase-1 and Caspase-3 in an ALS Transgenic Mouse Model

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Copper/zinc superoxide dismutase mRNA levels are increased in sporadic amyotrophic lateral sclerosis motorneurons

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Frontotemporal lobar degeneration: a consensus on clinical diagnostic criteria

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Nitric oxide synthase expression in cervical spinal cord in sporadic amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neuropsychological dysfunctions in amyotrophic lateral sclerosis: relation to motor disabilities.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Perineuronal glial responses after axotomy of central and peripheral axons. A comparison

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Rising mortality from motoneuron disease in the USA, 1962-84.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Survival prediction in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Microglial-neuronal interactions

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis patients living beyond respiratory failure

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Involvement of the amygdala, dentate and hippocampus in motor neuron disease.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Recovery of N-acetylaspartate in corticomotor neurons of patients with ALS after riluzole therapy.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Effect of recombinant human insulin-like growth factor-I on progression of ALS. A placebo-controlled study. The North America ALS/IGF-I Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Temporary amelioration of symptoms with intravenous cyclophosphamide in amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A clinical trial of verapamil in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A placebo-controlled trial of recombinant human ciliary neurotrophic (rhCNTF) factor in amyotrophic lateral sclerosis. rhCNTF ALS Study Group

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Parvalbumin and calbindin D-28k in the human motor system and in motor neuron disease.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Inter-relation between "classic" motor neuron disease and frontotemporal dementia: neuropsychological and single photon emission computed tomography study

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Neuropsychological measures in amyotrophic lateral sclerosis and their relationship with CT scan-assessed cerebral atrophy.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Inhibition of mononuclear phagocytes reduces ischemic injury in the spinal cord

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Linkage of familial amyotrophic lateral sclerosis with frontotemporal dementia to chromosome 9q21-q22

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Frontal lobe function in amyotrophic lateral sclerosis: a neuropsychologic and positron emission tomography study.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Low-calcium, high-aluminum diet-induced motor neuron pathology in cynomolgus monkeys

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Mutations associated with amyotrophic lateral sclerosis convert superoxide dismutase from an antiapoptotic gene to a proapoptotic gene: studies in yeast and neural cells

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Brain superoxide dismutase, catalase, and glutathione peroxidase activities in amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neuronal death in sporadic amyotrophic lateral sclerosis (ALS) is not apoptotic. A comparative study of ALS and chronic aluminium chloride neurotoxicity in New Zealand white rabbits

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A morphological analysis of the motor neuron degeneration and microglial reaction in acute and chronic in vivo aluminum chloride neurotoxicity

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

The Relationship of Microglial Cells to Dying Neurons During Natural Neuronal Cell Death and Axotomy-induced Degeneration of the Rat Retina

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Focal reductions of cerebral blood flow in amyotrophic lateral sclerosis: a [99mTc]-d,l-HMPAO SPECT study

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A clinical trial of dextromethorphan in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Failure of immunosuppression with a ten- to 14-day course of high-dose intravenous cyclophosphamide to alter the progression of amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

An open-randomized clinical trial of selegiline in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A double-blind placebo-controlled study of 3,4-diaminopyridine in amytrophic lateral sclerosis patients on a rehabilitation unit

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Therapeutic trial of tilorone in ALS: Lack of benefit in a double-blind, placebo-controlled study

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Genetic disorders of motor neurons.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Mice overexpressing the human neurofilament heavy gene as a model of ALS.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Autosomal dominant juvenile amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Amyotrophic lateral sclerosis. A study of central monoamine metabolism and therapeutic trial of levodopa

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Modified snake venom in amyotrophic lateral sclerosis. Lack of clinical effectiveness

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

X-linked recessive bulbospinal neuronopathy: a report of ten cases

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Calcineurin A and calbindin immunoreactivity in the spinal cord of G93A superoxide dismutase transgenic mice.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Molecular basis of an adult form of beta-hexosaminidase B deficiency with motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

N-acetyl-beta-hexosaminidase beta locus defect and juvenile motor neuron disease: a case study

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Progressive neuronopathy in transgenic mice expressing the human neurofilament heavy gene: a mouse model of amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Changes in the incidence of amyotrophic lateral sclerosis in Israel.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Familial amyotrophic lateral sclerosis with a mutation in exon 4 of the Cu/Zn superoxide dismutase gene: pathological and immunocytochemical changes

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Dementia lacking distinctive histopathology: clinicopathological evaluation of 32 cases

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Role of SOD-1 and nitric oxide/cyclic GMP cascade on neurofilament aggregation in ALS/MND.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

N-isopropyl-p-123I-amphetamine single photon emission computer tomography in motor neuron disease

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Development of ophthalmoplegia in amyotrophic lateral sclerosis during long-term use of respirators.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

A double-blind study of the effectiveness of cyclosporine in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Nitration of the low molecular weight neurofilament is equivalent in sporadic amyotrophic lateral sclerosis and control cervical spinal cord

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Autosomal recessive adult-onset amyotrophic lateral sclerosis associated with homozygosity for Asp90Ala CuZn-superoxide dismutase mutation. A clinical and genealogical study of 36 patients

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Immunocytochemical and ultrastructural studies of lower motor neurons in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Increasing trend of ALS in France and elsewhere: are the changes real?

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Dynamics of neuronal intermediate filaments: a developmental perspective

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Linkage of the gene for an autosomal dominant form of juvenile amyotrophic lateral sclerosis to chromosome 9q34.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Do posttranslational modifications of CuZnSOD lead to sporadic amyotrophic lateral sclerosis?

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Hereditary motor system diseases (chronic juvenile amyotrophic lateral sclerosis). Conditions combining a bilateral pyramidal syndrome with limb and bulbar amyotrophy

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Colocalization of NOS and SOD1 in neurofilament accumulation within motor neurons of amyotrophic lateral sclerosis: an immunohistochemical study

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Duration of amyotrophic lateral sclerosis is age dependent

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Immunosuppressive treatment of motor neuron syndromes. Attempts to distinguish a treatable disorder

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Familial amyotrophic lateral sclerosis with a point mutation of SOD-1: intrafamilial heterogeneity of disease duration associated with neurofibrillary tangles

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Intravenous immunoglobulin therapy in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Spinobulbar muscular atrophy can mimic ALS: the importance of genetic testing in male patients with atypical ALS.

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

Recombinant growth hormone treatment of amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1017%2FS0317167100001505

7 January 2021

10.1017/S0317167100001505

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11766772%20AND%20SRC:MED&resulttype=core&format=json

5 December 2019

1 reference