Motor behavioral and neuropathological deficits in mice deficient for normal prion protein expression (Q34512335)

2 August 2017

title

Motor behavioral and neuropathological deficits in mice deficient for normal prion protein expression (English)

1 reference

2 August 2017

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3

Glenn C Telling

1 reference

2 August 2017

2

Tanya Seward

1 reference

2 August 2017

Karah E Nazor

1

1 reference

2 August 2017

language of work or name

English

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publication date

24 April 2007

1 reference

Biochimica et Biophysica Acta

2 August 2017

published in

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2 August 2017

volume

1772

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2 August 2017

issue

6

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2 August 2017

page(s)

645-653

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Large-scale gene expression differences across brain regions and inbred strains correlate with a behavioral phenotype

2 August 2017

cites work

1 reference

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Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice

7 July 2018

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Anchorless prion protein results in infectious amyloid disease without clinical scrapie

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Mice devoid of prion protein have cognitive deficits that are rescued by reconstitution of PrP in neurons

7 July 2018

1 reference

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Informatics center for mouse genomics: the dissection of complex traits of the nervous system

7 July 2018

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Cellular prion protein ablation impairs behavior as a function of age.

7 July 2018

1 reference

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Spongiform degeneration in mahoganoid mutant mice

7 July 2018

1 reference

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Cellular prion protein transduces neuroprotective signals

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Post-natal knockout of prion protein alters hippocampal CA1 properties, but does not result in neurodegeneration

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Prion protein protects human neurons against Bax-mediated apoptosis

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Onset of ataxia and Purkinje cell loss in PrP null mice inversely correlated with Dpl level in brain

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Signal transduction through prion protein

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Normal inhibitory avoidance learning and anxiety, but increased locomotor activity in mice devoid of PrP(C)

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Doxycycline control of prion protein transgene expression modulates prion disease in mice

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

The cellular prion protein binds copper in vivo

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Prion Protein-Deficient Cells Show Altered Response to Oxidative Stress Due to Decreased SOD-1 Activity

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

High prion and PrPSc levels but delayed onset of disease in scrapie-inoculated mice heterozygous for a disrupted PrP gene

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Mice deficient for prion protein exhibit normal neuronal excitability and synaptic transmission in the hippocampus

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Mice devoid of PrP are resistant to scrapie

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

PrP gene dosage determines the timing but not the final intensity or distribution of lesions in scrapie pathology

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

The sequential development of the brain lesion of scrapie in three strains of mice

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Scrapie in mice. Agent-strain differences in the distribution and intensity of grey matter vacuolation

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Fatal familial insomnia: a second kindred with mutation of prion protein gene at codon 178

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Early behavioral deficits in R6/2 mice suitable for use in preclinical drug testing

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Differences among eight inbred strains of mice in motor ability and motor learning on a rotorod

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Coenzyme Q10 and remacemide hydrochloride ameliorate motor deficits in a Huntington's disease transgenic mouse model

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Mice with mutations in the mahogany gene Atrn have cerebral spongiform changes

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Motor skills and motor learning in Lurcher mutant mice during aging

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Prions prevent neuronal cell-line death.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

A 2-year longitudinal study of swimming navigation in mice devoid of the prion protein: no evidence for neurological anomalies or spatial learning impairments

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Prion protein expression and superoxide dismutase activity

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Can loss-of-function prion-related diseases exist?

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

The cellular prion protein binds copper in vivo

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Hippocampal slices from prion protein null mice: disrupted Ca(2+)-activated K+ currents.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Interactions between wild-type and mutant prion proteins modulate neurodegeneration in transgenic mice

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Normal host prion protein necessary for scrapie-induced neurotoxicity

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Prion protein is necessary for normal synaptic function

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Transmission of fatal familial insomnia to laboratory animals

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Spontaneous neurodegeneration in transgenic mice with mutant prion protein

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3025296

Altered circadian activity rhythms and sleep in mice devoid of prion protein

27 October 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/17531449

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Patch-clamp analysis of synaptic transmission to cerebellar purkinje cells of prion protein knockout mice

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/17531449

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Transmission of the BSE agent to mice in the absence of detectable abnormal prion protein

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/17531449

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1016/J.BBADIS.2007.04.004

1 reference

2 August 2017

1 reference

2 August 2017

1 reference