Demonstration of modified inactive first component of complement (C1) inhibitor in the plasmas of C1 inhibitor-deficient patients (Q34534792)

2 August 2017

title

Demonstration of modified inactive first component of complement (C1) inhibitor in the plasmas of C1 inhibitor-deficient patients (English)

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2 August 2017

B L Zuraw

1

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2 August 2017

J G Curd

series ordinal

2

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2 August 2017

language of work or name

English

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publication date

1 August 1986

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Journal of Clinical Investigation

2 August 2017

published in

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2 August 2017

volume

78

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2 August 2017

issue

2

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2 August 2017

page(s)

567-575

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HEREDITARY ANGIONEUROTIC EDEMA: TWO GENETIC VARIANTS.

2 August 2017

cites work

1 reference

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A BIOCHEMICAL ABNORMALITY IN HEREDIATRY ANGIONEUROTIC EDEMA: ABSENCE OF SERUM INHIBITOR OF C' 1-ESTERASE.

7 July 2018

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Proteolytic cleavage and inactivation of alpha 2-plasmin inhibitor and C1 inactivator by human polymorphonuclear leukocyte elastase

7 July 2018

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Detection of active kallikrein in induced blister fluids of hereditary angioedema patients

7 July 2018

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Dissemination of contact activation in plasma by plasma kallikrein

7 July 2018

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Structural and circular-dichroism studies on the interaction between human C1-esterase inhibitor and C1s

7 July 2018

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Prekallikrein activation and high-molecular-weight kininogen consumption in hereditary angioedema

7 July 2018

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Fluid-phase interaction of C1 inhibitor (C1 Inh) and the subcomponents C1r and C1s of the first component of complement, C1

7 July 2018

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5 Preparation and properties of human inhibitor

7 July 2018

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The human complement system serine proteases C1r and C1s and their proenzymes

7 July 2018

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Complexes between C1-inhibitor, kallikrein, high molecular weight kininogen, plasma thromboplastin antecedent, and plasmin in normal human plasma and hereditary angioneurotic edema plasmas containing dysmorphic C1-inhibitors: role of cold activation

7 July 2018

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7 July 2018

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Inactivation of kallikrein in human plasma

7 July 2018

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Contribution of Plasma Protease Inhibitors to the Inactivation of Kallikrein in Plasma

7 July 2018

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Immunochemical studies of human high molecular weight kininogen and of its complexes with plasma prekallikrein or kallikrein

7 July 2018

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Permeability-increasing activity in hereditary angioneurotic edema plasma. II. Mechanism of formation and partial characterization

7 July 2018

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Interaction of plasma kallikrein with the C1 inhibitor

7 July 2018

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Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

7 July 2018

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The stoichiometric measurement of the serum inhibition of the first component of complement by the inhibition of immune hemolysis

7 July 2018

1 reference

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Inhibition by C1INH of Hagemann factor fragment activation of coagulation, fibrinolysis, and kinin generation

7 July 2018

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The inhibition of plasmin, plasma kallikrein, plasma permeability factor, and the C'1r subcomponent of the first component of complement by serum C'1 esterase inhibitor

7 July 2018

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Variability in purified dysfunctional C1(-)-inhibitor proteins from patients with hereditary angioneurotic edema. Functional and analytical gel studies

7 July 2018

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Primary structure of the reactive site of human C1-inhibitor.

7 July 2018

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Distribution of plasma kallikrein between C-1 inactivator and alpha 2-macroglobulin in plasma utilizing a new assay for alpha 2-macroglobulin-kallikrein complexes

7 July 2018

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The regulation of human factor XIIa by plasma proteinase inhibitors

7 July 2018

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Human plasma kallikrein and C1 inhibitor form a complex possessing an epitope that is not detectable on the parent molecules: demonstration using a monoclonal antibody

7 July 2018

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The relationship of structure and function in human Hageman factor. The association of enzymatic and binding activities with separate regions of the molecule

7 July 2018

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The activation of plasminogen by Hageman factor (Factor XII) and Hageman factor fragments

7 July 2018

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Acquired C1 Esterase Inhibitor Deficiency and Angioedema

7 July 2018

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Electrophoretic transfer of proteins from polyacrylamide gels to nitrocellulose sheets: procedure and some applications

7 July 2018

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Formation of complexes composed of C1r, C1s, and C1 inactivator in human serum on activation of C1.

7 July 2018

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Role of the second component of complement (C2) and plasmin in kinin release in hereditary angioneurotic edema (H.A.N.E.) plasma

7 July 2018

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On the interaction of inhibitor and proteases Evidence for the formation of a covalent crosslinkage and non-covalent weak bondings between the inhibitor and proteases

7 July 2018

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Studies on human plasma C1 inactivator-enzyme interactions. I. Mechanisms of interaction with C1s, plasmin, and trypsin

7 July 2018

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Kinetics of the inactivation of human and bovine trypsins and chymotrypsins by α1-proteinase inhibitor and of their reactivation by α2-macroglobulin

7 July 2018

1 reference

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Inhibition of activated factor XII by antithrombin-heparin cofactor

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423595

Kinetics of reaction of human C-inhibitor with the human complement system proteases Cr and Cs

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423595

Activation of plasminogen by human plasma kallikrein

27 October 2018

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12 December 2020

Plasminogen: Purification from Human Plasma by Affinity Chromatography

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Inhibition of activated Hageman factor and activated plasma thromboplastin antecedent by purified serum C1 inactivator

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12 December 2020

Human alpha-1-proteinase inhibitor mechanism of action: Evidence for activation by limited proteolysis

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12 December 2020

Remissions induced in hereditary angioneurotic edema with an attenuated androgen (danazol): correlation between concentrations of C1-inhibitor and the forth and second components of complement

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Comparative studies of the fibrinolytic activity of cultured vascular cells

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The thrombin cleavage site in bovine antithrombin

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A C1-inhibitor-complex assay (INCA): a method to detect C1 activation in vitro and in vivo

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Rocket immunoelectrophoresis of C4 and C4d. A simple sensitive method for detecting complement activation in plasma

1 reference

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The active site of antithrombin. Release of the same proteolytically cleaved form of the inhibitor from complexes with factor IXa, factor Xa, and thrombin

1 reference

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A new role for C-1-inhibitor in homeostasis: control of activation of the first component of human complement

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Purification and characterization of human C1-esterase inhibitor

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Comparison of the interactions of human alpha1-antichymotrypsin with human leukocyte cathepsin G and bovine chymotrypsin

1 reference

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Kinin formation in hereditary angioedema plasma: evidence against kinin derivation from C2 and in support of “spontaneous” formation of bradykinin

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Heparin-stimulated modification of C1-inhibitor by subcomponent C1s of human complement

1 reference

12 December 2020

On the interaction between human plasma kallikrein and C1-esterase inhibitor

1 reference

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Interaction of human plasma kallikrein and its light chain with C1 inhibitor

1 reference

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Human C1 inhibitor: improved isolation and preliminary structural characterization

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Acquired deficiency of the inhibitor of the first component of complement: report of five additional cases with commentary on the syndrome

1 reference

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Partial purification of a serum inhibitor of C'1-esterase

1 reference

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Hereditary angioneurotic edema. II. Deficiency of inhibitor for serum globulin permeability factor and/or plasma kallikrein

1 reference

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Human serum inhibitor of C'1 esterase: identity with alpha-2-neuraminoglycoprotein

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12 December 2020

Identifiers

DOI

10.1172/JCI112610

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2 August 2017

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2 August 2017

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