Apical CFTR expression in human nasal epithelium correlates with lung disease in cystic fibrosis (Q34618363)

3 August 2017

title

Apical CFTR expression in human nasal epithelium correlates with lung disease in cystic fibrosis (English)

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3 August 2017

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Marit Arianne van Meegen

1

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3 August 2017

Suzanne Willemina Julia Terheggen-Lagro

2

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3 August 2017

Kirsten Judith Koymans

3

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3 August 2017

Cornelis Korstiaan van der Ent

4

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3 August 2017

Jeffrey Matthijn Beekman

5

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3 August 2017

language of work or name

English

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publication date

6 March 2013

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3 August 2017

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3 August 2017

volume

8

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3 August 2017

issue

3

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3 August 2017

page(s)

e57617

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Creative Commons Attribution 4.0 International

3 August 2017

copyright license

start time

6 March 2013

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April 2022 Public Data File from Crossref

copyright status

copyrighted

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cites work

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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21 January 2018

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21 January 2018

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The DeltaF508 mutation results in loss of CFTR function and mature protein in native human colon

21 January 2018

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Stimulation of beta 2-adrenergic receptor increases cystic fibrosis transmembrane conductance regulator expression in human airway epithelial cells through a cAMP/protein kinase A-independent pathway

21 January 2018

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Amiloride-insensitive nasal potential difference varies with the menstrual cycle in cystic fibrosis.

21 January 2018

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Ataluren (PTC124) induces cystic fibrosis transmembrane conductance regulator protein expression and activity in children with nonsense mutation cystic fibrosis

21 January 2018

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Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous (Delta)F508 mutation

21 January 2018

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CFTR is a conductance regulator as well as a chloride channel

26 October 2018

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Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis

26 October 2018

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12 December 2020

Ezrin is concentrated in the apical microvilli of a wide variety of epithelial cells whereas moesin is found primarily in endothelial cells

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12 December 2020

CFTR-mutation specific applications of CFTR-directed monoclonal antibodies

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12 December 2020

Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion

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Genetic modifiers of lung disease in cystic fibrosis

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10.1371/JOURNAL.PONE.0057617

Identifiers

DOI

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3 August 2017

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3 August 2017

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