Fibrillin-1 genetic deficiency leads to pathological ageing of arteries in mice. (Q34786838)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21432852%20AND%20SRC:MED&resulttype=core&format=json

26 January 2020

title

Fibrillin-1 genetic deficiency leads to pathological ageing of arteries in mice (English)

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26 January 2020

2

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26 January 2020

Daniela Quaglino

7

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26 January 2020

Philippe Huber

9

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26 January 2020

author name string

Boubacar Mariko

1

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26 January 2020

Brigitte Escoubet

3

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26 January 2020

Stéphanie Bouillot

4

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26 January 2020

Jean-Pierre Andrieu

5

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26 January 2020

Barry Starcher

6

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26 January 2020

Marie-Paule Jacob

8

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26 January 2020

Francesco Ramirez

10

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26 January 2020

Gilles Faury

11

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26 January 2020

publication date

22 March 2011

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26 January 2020

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26 January 2020

volume

224

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26 January 2020

issue

1

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26 January 2020

page(s)

33-44

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Discrete contributions of elastic fiber components to arterial development and mechanical compliance

26 January 2020

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8 July 2018

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Developmental adaptation of the mouse cardiovascular system to elastin haploinsufficiency

8 July 2018

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Extracellular matrix remodeling and matrix metalloproteinases in the vascular wall during aging and in pathological conditions

8 July 2018

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Cell adhesion to fibrillin-1 molecules and microfibrils is mediated by alpha 5 beta 1 and alpha v beta 3 integrins

8 July 2018

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Dysregulation of TGF-beta activation contributes to pathogenesis in Marfan syndrome

8 July 2018

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Inactivation of the lysyl oxidase gene Lox leads to aortic aneurysms, cardiovascular dysfunction, and perinatal death in mice

8 July 2018

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8 July 2018

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Connection between elastin haploinsufficiency and increased cell proliferation in patients with supravalvular aortic stenosis and Williams-Beuren syndrome

8 July 2018

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Fibrillin: from microfibril assembly to biomechanical function

8 July 2018

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Fibulin-5/DANCE is essential for elastogenesis in vivo

8 July 2018

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Function-structure relationship of elastic arteries in evolution: from microfibrils to elastin and elastic fibres

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Elastin is an essential determinant of arterial morphogenesis

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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28 July 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Microfibrils and fibrillin-1 induce integrin-mediated signaling, proliferation and migration in human endothelial cells.

21 January 2018

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Temporally controlled onset of dilated cardiomyopathy through disruption of the SRF gene in adult heart

21 January 2018

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Immunolocalization of microfibril and microfibril-associated proteins in the subendothelial matrix of the developing mouse aorta

26 October 2018

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12 December 2020

Identification of an elastin cross-linking domain that joins three peptide chains. Possible role in nucleated assembly

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12 December 2020

Aortic wall mechanics in the Marfan syndrome assessed by transesophageal tissue Doppler echocardiography

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12 December 2020

The role of endothelial cell attachment to elastic fibre molecules in the enhancement of monolayer formation and retention, and the inhibition of smooth muscle cell recruitment

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12 December 2020

Identifiers

DOI

10.1002/PATH.2840

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21432852%20AND%20SRC:MED&resulttype=core&format=json

26 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21432852%20AND%20SRC:MED&resulttype=core&format=json

26 January 2020

1 reference