Coenzyme Q(10) and idebenone in the therapy of respiratory chain diseases: rationale and comparative benefits (Q34929722)

5 August 2017

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title

Coenzyme Q(10) and idebenone in the therapy of respiratory chain diseases: rationale and comparative benefits (English)

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5 August 2017

7

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Agnès Rötig

6

object named as

Agnès Rötig

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5 August 2017

Vanna Geromel

1

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5 August 2017

Niklas Darin

2

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5 August 2017

Dominique Chrétien

3

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5 August 2017

Paule Bénit

4

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5 August 2017

Pascale DeLonlay

5

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5 August 2017

Pierre Rustin

8

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5 August 2017

1 September 2002

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Molecular Genetics and Metabolism

5 August 2017

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5 August 2017

77

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5 August 2017

1-2

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5 August 2017

21-30

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Biochemical, physiological and medical aspects of ubiquinone function

5 August 2017

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Plasma ubiquinol-10 as a marker for disease: is the assay worthwhile?

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Further evidence for the pool function of ubiquinone as derived from the inhibition of the electron transport by antimycin.

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Protonmotive redox mechanism of the cytochrome b-c 1 complex in the respiratory chain: Protonmotive ubiquinone cycle

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Superoxide-induced massive apoptosis in cultured skin fibroblasts harboring the neurogenic ataxia retinitis pigmentosa (NARP) mutation in the ATPase-6 gene of the mitochondrial DNA.

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Antioxidant-derived prooxidant formation from ubiquinol

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Human cultured skin fibroblasts survive profound inherited ubiquinone depletion

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Selective targeting of a redox-active ubiquinone to mitochondria within cells: antioxidant and antiapoptotic properties

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Three classes of ubiquinone analogs regulate the mitochondrial permeability transition pore through a common site

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Ubiquinone biosynthesis by the microsomal fraction from rat liver

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Mitochondrial ubiquinone homologues, superoxide radical generation, and longevity in different mammalian species

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Chemistry, toxicology, pharmacology and pharmacokinetics of idebenone: a review

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Role of mitochondria in oxidative stress and aging

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Quinone-responsive multiple respiratory-chain dysfunction due to widespread coenzyme Q10 deficiency

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

31P NMR study of improvement in oxidative phosphorylation by vitamins K3 and C in a patient with a defect in electron transport at complex III in skeletal muscle.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

A possible role of coenzyme Q10 in the etiology and treatment of Parkinson's disease

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Coenzyme Q10, exercise lactate and CTG trinucleotide expansion in myotonic dystrophy.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Study of CoQ10-enzymes in gingiva from patients with periodontal disease and evidence for a deficiency of coenzyme Q10

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Blood antioxidant status and urinary levels of catecholamine metabolites in beta-thalassemia

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Mitochondrial encephalomyopathy with coenzyme Q10 deficiency

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Familial cerebellar ataxia with muscle coenzyme Q10 deficiency

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Effect of idebenone on cardiomyopathy in Friedreich's ataxia: a preliminary study

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

The phylogenetic distribution of frataxin indicates a role in iron-sulfur cluster protein assembly

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

The mitochondrial proteins Ssq1 and Jac1 are required for the assembly of iron sulfur clusters in mitochondria

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Disabled early recruitment of antioxidant defenses in Friedreich's ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Glutathione in blood of patients with Friedreich's ataxia.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Oxidative stress in patients with Friedreich ataxia.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Idebenone and reduced cardiac hypertrophy in Friedreich's ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Heart hypertrophy and function are improved by idebenone in Friedreich's ataxia

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Dramatic improvement in mitochondrial cardiomyopathy following treatment with idebenone

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Mitochondrial complex I deficiency leads to increased production of superoxide radicals and induction of superoxide dismutase

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Diseases of the mitochondrial DNA.

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Do idebenone and vitamin therapy shorten the time to achieve visual recovery in Leber hereditary optic neuropathy?

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Networking antioxidants in the isolated rat heart are selectively depleted by ischemia-reperfusion

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Overview of the use of CoQ10 in cardiovascular disease

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Influence of the antioxidants vitamin E and idebenone on retinal cell injury mediated by chemical ischemia, hypoglycemia, or oxidative stress

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Suppression of leukocyte-enhanced cold ischemia/reperfusion injury of liver endothelium with the benzoquinone antioxidant idebenone

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Mitochondria and degenerative disorders

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https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Ubiquinone (coenzyme q10) and mitochondria in oxidative stress of parkinson's disease

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Coenzyme Q10 administration and its potential for treatment of neurodegenerative diseases

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

Safety and efficacy of idebenone versus tacrine in patients with Alzheimer's disease: results of a randomized, double-blind, parallel-group multicenter study

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900145-2

7 January 2021

10.1016/S1096-7192(02)00145-2

Identifiers

DOI

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5 August 2017

1 reference