Forced expression of laminin beta1 in podocytes prevents nephrotic syndrome in mice lacking laminin beta2, a model for Pierson syndrome (Q35217074)

7 August 2017

Forced expression of laminin beta1 in podocytes prevents nephrotic syndrome in mice lacking laminin beta2, a model for Pierson syndrome (English)

1 reference

7 August 2017

1 reference

2

George Jarad

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7 August 2017

4

Jeffrey H Miner

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7 August 2017

Jung Hee Suh

1

1 reference

7 August 2017

Rene G VanDeVoorde

series ordinal

3

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7 August 2017

language of work or name

English

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publication date

29 August 2011

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7 August 2017

6

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Proceedings of the National Academy of Sciences of the United States of America

inferred from page(s)

published in

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7 August 2017

108

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7 August 2017

37

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7 August 2017

15348-15353

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describes a project that uses

7 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3174642/fullTextXML

inferred from PubMed Central ID database lookup

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Laminin alpha1 chain improves laminin alpha2 chain deficient peripheral neuropathy

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Integrin alpha1beta1 and transforming growth factor-beta1 play distinct roles in alport glomerular pathogenesis and serve as dual targets for metabolic therapy

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13 July 2018

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13 July 2018

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13 July 2018

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13 July 2018

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13 July 2018

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A laminin-like adhesive protein concentrated in the synaptic cleft of the neuromuscular junction

13 July 2018

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A retinoic acid-responsive element is present in the 5' flanking region of the laminin B1 gene

13 July 2018

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Variable expression of desmin in rat glomerular epithelial cells

13 July 2018

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The alpha 1-alpha 6 subunits of integrins are characteristically expressed in distinct segments of developing and adult human nephron

13 July 2018

1 reference

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13 July 2018

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The C-terminal region of laminin beta chains modulates the integrin binding affinities of laminins

26 September 2018

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Partial rescue of glomerular laminin alpha5 mutations by wild-type endothelia produce hybrid glomeruli.

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3174642

Laminin alpha1 chain reduces muscular dystrophy in laminin alpha2 chain deficient mice

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3174642

Glomerular-specific gene excision in vivo.

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3174642

Defective glomerulogenesis in the absence of laminin alpha5 demonstrates a developmental role for the kidney glomerular basement membrane.

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3174642

[AN UNUSUAL CONGENITAL AND FAMILIAL CONGENITAL MALFORMATIVE COMBINATION INVOLVING THE EYE AND KIDNEY.]

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3174642

Demonstration of two novel LAMB2 mutations in the original Pierson syndrome family reported 42 years ago

15 November 2018

1 reference

12 December 2020

Pierson syndrome: a novel cause of congenital nephrotic syndrome

1 reference

12 December 2020

Neurodevelopmental deficits in Pierson (microcoria-congenital nephrosis) syndrome

1 reference

12 December 2020

Abnormal glomerular basement membrane laminins in murine, canine, and human Alport syndrome: aberrant laminin alpha2 deposition is species independent

1 reference

12 December 2020

Glomerular endothelial cells and podocytes jointly synthesize laminin-1 and -11 chains

1 reference

12 December 2020

Podocyte injury induced by albumin overload in vivo and in vitro: involvement of TGF-beta and p38 MAPK

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.1108269108

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7 August 2017

0 references

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7 August 2017

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