Peripheral nervous system manifestations in a Sandhoff disease mouse model: nerve conduction, myelin structure, lipid analysis. (Q35991172)

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1 January 2020

title

Peripheral nervous system manifestations in a Sandhoff disease mouse model: nerve conduction, myelin structure, lipid analysis (English)

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1 January 2020

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4

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1 January 2020

Daniel A Kirschner

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1 January 2020

author name string

Melanie A McNally

1

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1 January 2020

Rena C Baek

2

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1 January 2020

Robin L Avila

3

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1 January 2020

Gary R Strichartz

5

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publication date

10 July 2007

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Journal of Negative Results in BioMedicine

1 January 2020

published in

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volume

6

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page(s)

8

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describes a project that uses

1 January 2020

ImageQuant

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ImageQuant

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inferred from PubMed Central ID database lookup

CZ Software Mentions: A large dataset of software mentions in the biomedical literature

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Establishment of immortalized Schwann cells from Sandhoff mice and corrective effect of recombinant human beta-hexosaminidase A on the accumulated GM2 ganglioside

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Lysosomal storage results in impaired survival but normal neurite outgrowth in dorsal root ganglion neurones from a mouse model of Sandhoff disease.

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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.

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Identifiers

DOI

10.1186/1477-5751-6-8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17623103%20AND%20SRC:MED&resulttype=core&format=json

1 January 2020

1 reference

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1 January 2020

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