Cystic fibrosis lung disease: genetic influences, microbial interactions, and radiological assessment (Q36114460)

12 August 2017

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title

Cystic fibrosis lung disease: genetic influences, microbial interactions, and radiological assessment (English)

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12 August 2017

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Samuel M Moskowitz

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12 August 2017

Ronald L Gibson

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2

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12 August 2017

Eric L Effmann

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3

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12 August 2017

language of work or name

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3 May 2005

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12 August 2017

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12 August 2017

35

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12 August 2017

8

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12 August 2017

739-757

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https://scigraph.springernature.com/pub.10.1007/s00247-005-1445-3

12 August 2017

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Relation between mutations of the cystic fibrosis gene and idiopathic pancreatitis.

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Endothelial Nitric Oxide Synthase Variants in Cystic Fibrosis Lung Disease

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Cystic fibrosis: combined hyperpolarized 3He-enhanced and conventional proton MR imaging in the lung--preliminary observations

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12 December 2020

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12 December 2020

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Randomized trial of ceftazidime versus placebo in the management of acute respiratory exacerbations in patients with cystic fibrosis

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12 December 2020

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12 December 2020

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Treatment of pseudomonas aeruginosa colonisation in cystic fibrosis

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12 December 2020

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12 December 2020

Clinically feasible biofilm susceptibility assay for isolates of Pseudomonas aeruginosa from patients with cystic fibrosis

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12 December 2020

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12 December 2020

Polyvariant mutant cystic fibrosis transmembrane conductance regulator genes. The polymorphic (Tg)m locus explains the partial penetrance of the T5 polymorphism as a disease mutation

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12 December 2020

Chest radiographs in cystic fibrosis. A follow-up study with application of a quantitative system.

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12 December 2020

Alginate is not a significant component of the extracellular polysaccharide matrix of PA14 and PAO1 Pseudomonas aeruginosa biofilms

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12 December 2020

Pseudomonas aeruginosa and the in vitro and in vivo biofilm mode of growth

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12 December 2020

Nontuberculous mycobacteria. II: nested-cohort study of impact on cystic fibrosis lung disease.

1 reference

12 December 2020

Elective versus symptomatic intravenous antibiotic therapy for cystic fibrosis.

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12 December 2020

Contribution of genetic factors other than CFTR to disease severity in cystic fibrosis

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12 December 2020

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

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12 December 2020

The systematic evaluation of the chest radiograph in cystic fibrosis

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12 December 2020

Composite Spirometric–Computed Tomography Outcome Measure in Early Cystic Fibrosis Lung Disease

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12 December 2020

Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group

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12 December 2020

The incidence of cystic fibrosis in Scotland calculated from heterozygote frequencies

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Cystic fibrosis: when should high-resolution computed tomography of the chest be obtained?

1 reference

12 December 2020

Gentamicin-Induced Correction of CFTR Function in Patients with Cystic Fibrosis andCFTRStop Mutations

1 reference

12 December 2020

Single and combination antibiotic susceptibilities of planktonic, adherent, and biofilm-grown Pseudomonas aeruginosa isolates cultured from sputa of adults with cystic fibrosis.

1 reference

12 December 2020

Antibiotic prophylaxis in infants and young children with cystic fibrosis: a randomized controlled trial

1 reference

12 December 2020

Efficacy of inhaled tobramycin in the treatment of pulmonary exacerbations in children with cystic fibrosis

1 reference

12 December 2020

High-resolution CT in the acute exacerbation of cystic fibrosis: evaluation of acute findings, reversibility of those findings, and clinical correlation

1 reference

12 December 2020

Relationship between sputum inflammatory markers, lung function, and lung pathology on high-resolution computed tomography in children with cystic fibrosis.

1 reference

12 December 2020

Spirometer-triggered high-resolution computed tomography and pulmonary function measurements during an acute exacerbation in patients with cystic fibrosis

1 reference

12 December 2020

Cystic Fibrosis Foundation consensus conference report on pulmonary complications of cystic fibrosis

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12 December 2020

Modifier genes and variation in cystic fibrosis

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12 December 2020

Mutation in the gene responsible for cystic fibrosis and predisposition to chronic rhinosinusitis in the general population

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12 December 2020

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12 December 2020

Development and evaluation of a PCR-based, line probe assay for the detection of 58 alleles in the cystic fibrosis transmembrane conductance regulator (CFTR) gene

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12 December 2020

Pseudomonas biofilm formation and antibiotic resistance are linked to phenotypic variation

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12 December 2020

The chest roentgenogram in cystic fibrosis: a new scoring system

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12 December 2020

Pulmonary disease assessment in cystic fibrosis: comparison of CT scoring systems and value of bronchial and arterial dimension measurements

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12 December 2020

Comparison of high-frequency chest wall oscillation and oscillating positive expiratory pressure in the home management of cystic fibrosis: a pilot study

1 reference

12 December 2020

Effect of inhaled tobramycin on early Pseudomonas aeruginosa colonisation in patients with cystic fibrosis

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12 December 2020

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12 December 2020

Serotype-specific serum IgG antibodies to lipopolysaccharides of Pseudomonas aeruginosa in cystic fibrosis: correlation to disease, subclass distribution, and experimental protective capacity

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12 December 2020

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12 December 2020

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12 December 2020

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12 December 2020

Nonmotility and phagocytic resistance of Pseudomonas aeruginosa isolates from chronically colonized patients with cystic fibrosis

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12 December 2020

α1-Antitrypsin Deficiency Alleles in Cystic Fibrosis Lung Disease

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12 December 2020

Computed tomography and radiation: understanding the issues.

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12 December 2020

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1 reference

12 December 2020

Alginate overproduction affects Pseudomonas aeruginosa biofilm structure and function

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12 December 2020

Identification of the cystic fibrosis gene: genetic analysis

1 reference

12 December 2020

Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition

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12 December 2020

Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection

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12 December 2020

Opsonophagocytic killing antibody to Pseudomonas aeruginosa mucoid exopolysaccharide in older noncolonized patients with cystic fibrosis.

1 reference

12 December 2020

Comparison between morphologic changes seen on high-resolution CT and regional pulmonary perfusion seen on SPECT in patients with cystic fibrosis

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12 December 2020

Modulation of deltaF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids

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12 December 2020

Biofilms, antimicrobial resistance, and airway infection.

1 reference

12 December 2020

Quorum-sensing signals indicate that cystic fibrosis lungs are infected with bacterial biofilms

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12 December 2020

Infection withBurkholderia cepaciaComplex Genomovars in Patients with Cystic Fibrosis: Virulent Transmissible Strains of Genomovar III Can ReplaceBurkholderia multivorans

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12 December 2020

Endemicity and inter-city spread of Burkholderia cepacia genomovar III in cystic fibrosis

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12 December 2020

Early pulmonary inflammation in infants with cystic fibrosis

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12 December 2020

Medium term treatment of stable stage cystic fibrosis with recombinant human DNase I.

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12 December 2020

Mechanisms of biofilm resistance to antimicrobial agents

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12 December 2020

Effects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patients

1 reference

12 December 2020

Association of poor clinical status and heavy exposure to tobacco smoke in patients with cystic fibrosis who are homozygous for the F508 deletion

1 reference

12 December 2020

Efficacy of inhaled amikacin as adjunct to intravenous combination therapy (ceftazidime and amikacin) in cystic fibrosis

1 reference

12 December 2020

Randomised controlled trial of inhaled corticosteroids (fluticasone propionate) in cystic fibrosis

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12 December 2020

Evolution of CT findings in patients with cystic fibrosis

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12 December 2020

Lung disease associated with the IVS8 5T allele of the CFTR gene

1 reference

12 December 2020

Wisconsin cystic fibrosis chest radiograph scoring system: validation and standardization for application to longitudinal studies.

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12 December 2020

Efficacy and safety of short-term administration of aerosolised recombinant human DNase I in adults with stable stage cystic fibrosis

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12 December 2020

Changes in strategies for optimal antibacterial therapy in cystic fibrosis.

1 reference

12 December 2020

Helix induction in antimicrobial peptides by alginate in biofilms

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12 December 2020

Effect of chronic intermittent administration of inhaled tobramycin on respiratory microbial flora in patients with cystic fibrosis

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12 December 2020

Siderophore synthesis by mucoid Pseudomonas aeruginosa strains isolated from cystic fibrosis patients

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12 December 2020

A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group

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12 December 2020

Study of pyoverdine type and production by Pseudomonas aeruginosa isolated from cystic fibrosis patients: prevalence of type II pyoverdine isolates and accumulation of pyoverdine-negative mutations

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12 December 2020

Complete mutational screening of the CFTR gene in 120 patients with pulmonary disease

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12 December 2020

Mutations of the cystic fibrosis gene in patients with chronic pancreatitis

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12 December 2020

Role of alginate and its O acetylation in formation of Pseudomonas aeruginosa microcolonies and biofilms

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12 December 2020

Correlation of six different cystic fibrosis chest radiograph scoring systems with clinical parameters

1 reference

12 December 2020

Use of computerized tomography and chest x-rays in evaluating efficacy of aerosolized recombinant human DNase in cystic fibrosis patients younger than age 5 years: a preliminary study.

1 reference

12 December 2020

10.1007/S00247-005-1445-3

Identifiers

DOI

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12 August 2017

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