Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy. (Q36444154)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26494620%20AND%20SRC:MED&resulttype=core&format=json

28 February 2020

title

Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26494620%20AND%20SRC:MED&resulttype=core&format=json

28 February 2020

0 references

0 references

1

1 reference

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28 February 2020

Naftali Kaminski

14

1 reference

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28 February 2020

author name string

Donna B Stolz

2

1 reference

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28 February 2020

John F Alcorn

3

1 reference

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28 February 2020

Samuel A Yousem

4

1 reference

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28 February 2020

Jieru Wang

5

1 reference

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28 February 2020

Adriana S Leme

6

1 reference

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28 February 2020

A McGarry Houghton

7

1 reference

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28 February 2020

Pamela Hale

8

1 reference

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28 February 2020

Michael Ewing

9

1 reference

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28 February 2020

Houming Cai

10

1 reference

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28 February 2020

Evelyn Akpadock Garchar

11

1 reference

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28 February 2020

Nunzia Pastore

12

1 reference

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28 February 2020

Patrizia Annunziata

13

1 reference

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28 February 2020

Joseph Pilewski

15

1 reference

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28 February 2020

Steven D Shapiro

16

1 reference

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28 February 2020

Stephen C Pak

17

1 reference

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28 February 2020

Gary A Silverman

18

1 reference

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28 February 2020

Nicola Brunetti-Pierri

19

1 reference

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28 February 2020

David H Perlmutter

20

1 reference

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28 February 2020

language of work or name

English

0 references

publication date

22 October 2015

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26494620%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

28 February 2020

published in

1 reference

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28 February 2020

volume

290

1 reference

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28 February 2020

issue

50

1 reference

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28 February 2020

page(s)

29742-29757

1 reference

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describes a project that uses

28 February 2020

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC4705969/fullTextXML

inferred from PubMed Central ID database lookup

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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Sputum chemotactic activity in chronic obstructive pulmonary disease: effect of alpha(1)-antitrypsin deficiency and the role of leukotriene B(4) and interleukin 8

30 September 2017

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Cell-specific involvement of HNF-1beta in alpha(1)-antitrypsin gene expression in human respiratory epithelial cells

30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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28 June 2018

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28 June 2018

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28 June 2018

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28 June 2018

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28 June 2018

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21 September 2018

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21 September 2018

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Efficient and rapid isolation and purification of mouse alveolar type II epithelial cells.

21 September 2018

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21 September 2018

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Exploring the role of CT densitometry: a randomised study of augmentation therapy in alpha1-antitrypsin deficiency.

21 September 2018

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21 September 2018

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COX-2-derived prostacyclin protects against bleomycin-induced pulmonary fibrosis

21 September 2018

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21 September 2018

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Alpha1-antitrypsin deficiency in 26-year-old subjects: lung, liver, and protease/protease inhibitor studies

21 September 2018

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Z alpha1-antitrypsin polymerizes in the lung and acts as a neutrophil chemoattractant.

21 September 2018

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21 September 2018

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Pharmacological modulation of ion transport across wild-type and DeltaF508 CFTR-expressing human bronchial epithelia

21 September 2018

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12 December 2020

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IKKβ Is Required for Prevention of Apoptosis Mediated by Cell-Bound but Not by Circulating TNFα

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Intracellular inclusions containing mutant alpha1-antitrypsin Z are propagated in the absence of autophagic activity

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12 December 2020

Survival benefit of lung transplantation in individuals with severe α1-anti-trypsin deficiency (PiZZ) and emphysema

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Identifiers

DOI

10.1074/JBC.M115.691253

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26494620%20AND%20SRC:MED&resulttype=core&format=json

28 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26494620%20AND%20SRC:MED&resulttype=core&format=json

28 February 2020

1 reference