The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist (Q36491436)

14 August 2017

1 reference

title

The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist (English)

1 reference

14 August 2017

P. Brown

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1673176

25 October 2022

L. G. Goldfarb

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1673176

25 October 2022

D. C. Gajdusek

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1673176

25 October 2022

language of work or name

English

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publication date

1 April 1991

1 reference

14 August 2017

27 April 1991

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=1673176

full work available at URL

25 October 2022

https://api.elsevier.com/content/article/PII:014067369192670W?httpAccept=text/xml

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

https://api.elsevier.com/content/article/PII:014067369192670W?httpAccept=text/plain

25 October 2022

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

25 October 2022

1 reference

14 August 2017

337

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14 August 2017

1019-1022

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14 August 2017

8748

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Degenerative disease of the central nervous system in New Guinea; the endemic occurrence of kuru in the native population

14 August 2017

1

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Creutzfeldt-Jakob disease: clinical analysis of a consecutive series of 230 neuropathologically verified cases.

25 October 2022

2

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Creutzfeldt-Jakob disease virus isolations from the Gerstmann-Sträussler syndrome with an analysis of the various forms of amyloid plaque deposition in the virus-induced spongiform encephalopathies

25 October 2022

3

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Diagnosis of Creutzfeldt-Jakob disease by Western blot identification of marker protein in human brain tissue.

25 October 2022

4

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Experimental transmission of a Kuru-like syndrome to chimpanzees

25 October 2022

5

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Creutzfeldt-Jakob Disease (Spongiform Encephalopathy): Transmission to the Chimpanzee

25 October 2022

6

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Transmissible and non-transmissible amyloidoses: autocatalytic post-translational conversion of host precursor proteins to beta-pleated sheet configurations

25 October 2022

8

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Separation and properties of cellular and scrapie prion proteins

25 October 2022

9

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

The precursor of Alzheimer's disease amyloid A4 protein resembles a cell-surface receptor

25 October 2022

10

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Localization of a human gene homologous to the PrP gene on the p arm of chromosome 20 and detection of PrP-related antigens in normal human brain

25 October 2022

13

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene

25 October 2022

14

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Some factors controlling the incidence of scrapie in Cheviot sheep injected with a Cheviot-passaged scrapie agent.

25 October 2022

16

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Identification of a gene which controls the incubation period of some strains of scrapie agent in mice.

25 October 2022

17

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Linkage of prion protein and scrapie incubation time genes

25 October 2022

18

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Distinct prion proteins in short and long scrapie incubation period mice

25 October 2022

19

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Linkage of the gene for the scrapie-associated fibril protein (PrP) to the Sip gene in Cheviot sheep

25 October 2022

21

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Insertion in prion protein gene in familial Creutzfeldt-Jakob disease

25 October 2022

22

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

25 October 2022

24

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

25 October 2022

25

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Creutzfeldt-Jakob disease patients with congophilic kuru plaques have the missense variant prion protein common to Gerstmann-Sträussler syndrome

25 October 2022

26

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Creutzfeldt-Jakob disease and kuru patients lack a mutation consistently found in the Gerstmann-Sträussler-Scheinker syndrome

25 October 2022

27

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Clinical and molecular genetic study of a large German kindred with Gerstmann-Straussler-Scheinker syndrome

25 October 2022

28

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

The molecular genetics of familial Creutzfeldt-Jakob disease in France

25 October 2022

29

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Gerstmann-Sträussler-Scheinker disease. I. Extending the clinical spectrum.

25 October 2022

30

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Immunochemical, molecular genetic, and transmission studies on a case of Gerstmann-Straussler-Scheinker syndrome

25 October 2022

31

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

25 October 2022

32

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Identical mutation in unrelated patients with Creutzfeldt-Jakob disease.

25 October 2022

33

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Mutation in codon 200 of scrapie amyloid protein gene in two clusters of Creutzfeldt-Jakob disease in Slovakia

25 October 2022

34

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Mutation in codon 200 of scrapie amyloid precursor gene linked to Creutzfeldt-Jakob disease in Sephardic Jews of Libyan and non-Libyan origin

25 October 2022

35

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

New mutation in scrapie amyloid precursor gene (at codon 178) in Finnish Creutzfeldt-Jakob kindred

25 October 2022

36

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Codon 178 mutation in ethnically diverse Creutzfeldt-Jakob disease families

25 October 2022

37

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Spontaneous neurodegeneration in transgenic mice with mutant prion protein

25 October 2022

41

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Nature of the Scrapie Agent

25 October 2022

42

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Self-replication and scrapie

25 October 2022

43

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Requirement of a protein component for scrapie infectivity.

25 October 2022

45

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Novel proteinaceous infectious particles cause scrapie

25 October 2022

46

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Induced frameshifting mechanism of replication for an information-carrying scrapie prion

25 October 2022

47

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Molecular mass, biochemical composition, and physicochemical behavior of the infectious form of the scrapie precursor protein monomer

25 October 2022

48

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Conservation of infectivity in purified fibrillary extracts of scrapie-infected hamster brain after sequential enzymatic digestion or polyacrylamide gel electrophoresis

25 October 2022

49

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Resistance of scrapie infectivity to steam autoclaving after formaldehyde fixation and limited survival after ashing at 360 degrees C: practical and theoretical implications

25 October 2022

50

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

Iatrogenic Creutzfeldt-Jakob disease

25 October 2022

51

1 reference

https://api.crossref.org/works/10.1016/0140-6736(91)92670-W

25 October 2022

Identifiers

1 reference

14 August 2017

1 reference