Excretion-Reuptake Route of β-Hexosaminidase in Normal and I-Cell Disease Cultured Fibroblasts (Q37037143)

17 August 2017

Excretion-reuptake route of beta-hexosaminidase in normal and I-cell disease cultured fibroblasts (English)

1 reference

PMCID

371993

https://api.crossref.org/works/10.1172/JCI109341

17 August 2017

Excretion-Reuptake Route of β-Hexosaminidase in Normal and I-Cell Disease Cultured Fibroblasts (English)

1 reference

10 May 2023

author name string

G. D. Vladutiu

series ordinal

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A438323

10 May 2023

M. C. Rattazzi

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A438323

10 May 2023

language of work or name

English

0 references

publication date

1 April 1979

1 reference

PMCID

371993

full work available at URL

17 August 2017

https://europepmc.org/articles/PMC371993

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A438323

https://europepmc.org/articles/PMC371993?pdf=render

10 May 2023

file format

Portable Document Format

online access status

open access

content deliverer

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A438323

Journal of Clinical Investigation

10 May 2023

published in

1 reference

17 August 2017

63

1 reference

17 August 2017

4

1 reference

17 August 2017

595-601

1 reference

Phosphohexosyl recognition is a general characteristic of pinocytosis of lysosomal glycosidases by human fibroblasts

17 August 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Cellular transport of lysosomal enzymes: an alternative hypothesis

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Evidence for lysosomal enzyme recognition by human fibroblasts via a phosphorylated carbohydrate moiety

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Correlation of structural features of phosphomannans with their ability to inhibit pinocytosis of human beta-glucuronidase by human fibroblasts

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

The distribution of hydrolytic enzyme activities in human fibroblast cultures and their intercellular transfer

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Immunoaffinity Chromatography of Human β-Hexosaminidase A

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Kinetics of phagocytosis. II. Analysis of in vivo clearance with demonstration of competitive inhibition between similar and dissimilar foreign particles.

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

A hypothesis for I-cell disease: defective hydrolases that do not enter lysosomes

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

Chemical characterization and subunit structure of human N-acetylhexosaminidases A and B

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=371993

I-cell disease Desialylation of β-hexosaminidase and its effect on uptake by fibroblasts

27 June 2018

1 reference

12 December 2020

Modulation of lysosomal enzyme levels in cultured cells: effects of alterations in cell density, balanced growth, and endocytosis

1 reference

12 December 2020

Recognition and receptor-mediated uptake of a lysosomal enzyme, alpha-l-iduronidase, by cultured human fibroblasts

1 reference

12 December 2020

Sandhoff disease: defective glycosaminoglycan catabolism in cultured fibroblasts and its correction by beta-N-acetylhexosaminidase

1 reference

12 December 2020

A recognition marker required for uptake of a lysosomal enzyme by cultured fibroblasts

1 reference

12 December 2020

Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II)

1 reference

12 December 2020

Sanfilippo disease type B: enzyme replacement and metabolic correction in cultured fibroblasts

1 reference

12 December 2020

Multiple lysosomal enzyme deficiency due to enzyme leakage?

1 reference

12 December 2020

Intercellular exchange of lysosomal enzymes: enzyme assays in single human fibroblasts after co-cultivation

1 reference

12 December 2020

Multiple isoelectric and recognition forms of human β-glucuronidase activity

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI109341

1 reference

17 August 2017

1 reference

17 August 2017

1 reference

PMCID

371993