Utrophin lacks the rod domain actin binding activity of dystrophin (Q38317877)

2 September 2017

title

Utrophin lacks the rod domain actin binding activity of dystrophin (English)

1 reference

2 September 2017

Amann KJ

1

1 reference

2 September 2017

Guo AW

series ordinal

2

1 reference

2 September 2017

Ervasti JM

series ordinal

3

1 reference

2 September 2017

language of work or name

English

0 references

publication date

1 December 1999

1 reference

Journal of Biological Chemistry

2 September 2017

number of pages

6

1 reference

based on heuristic

inferred from page(s)

published in

1 reference

2 September 2017

volume

274

1 reference

2 September 2017

issue

50

1 reference

2 September 2017

page(s)

35375-35380

1 reference

A role for the dystrophin-glycoprotein complex as a transmembrane linker between laminin and actin.

2 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

The complete sequence of dystrophin predicts a rod-shaped cytoskeletal protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Analysis of the actin-binding domain of alpha-actinin by mutagenesis and demonstration that dystrophin contains a functionally homologous domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Expression of the N-terminal domain of dystrophin in E. coli and demonstration of binding to F-actin.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Actin-dystrophin interface.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Deletion analysis of the dystrophin-actin binding domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Alternate binding of actin and calmodulin to multiple sites on dystrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Transgenic mdx mice expressing dystrophin with a deletion in the actin-binding domain display a "mild Becker" phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

A new model for the interaction of dystrophin with F-actin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Skeletal muscle-specific expression of a utrophin transgene rescues utrophin-dystrophin deficient mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Subtle neuromuscular defects in utrophin-deficient mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Postsynaptic abnormalities at the neuromuscular junctions of utrophin-deficient mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Dystrophin and utrophin: the missing links!

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Cloning and expression of full length mouse utrophin: the differential association of utrophin and dystrophin with AChR clusters

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Determination of molecular weights and frictional ratios of proteins in impure systems by use of gel filtration and density gradient centrifugation. Application to crude preparations of sulfite and hydroxylamine reductases

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

conformation and phasing of dystrophin structural repeats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Stability of the dystrophin rod domain fold: evidence for nested repeating units

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Identification of the spectrin subunit and domains required for formation of spectrin/adducin/actin complexes

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Extensive but coordinated reorganization of the membrane skeleton in myofibers of dystrophic (mdx) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Prevention of dystrophic pathology in mdx mice by a truncated dystrophin isoform.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Expression of human full-length and minidystrophin in transgenic mdx mice: implications for gene therapy of Duchenne muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Expression of full-length utrophin prevents muscular dystrophy in mdx mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Does utrophin expression in muscles of mdx mice during postnatal development functionally compensate for dystrophin deficiency?

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Very mild muscular dystrophy associated with the deletion of 46% of dystrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Becker muscular dystrophy patient with a large intragenic dystrophin deletion: implications for functional minigenes and gene therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Dystrophin protects the sarcolemma from stresses developed during muscle contraction

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Molecular analysis of a spontaneous dystrophin 'knockout' dog.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Human dystrophin expression in mdx mice after intramuscular injection of DNA constructs

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

A cluster of basic repeats in the dystrophin rod domain binds F-actin through an electrostatic interaction

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Glycoprotein-binding site of dystrophin is confined to the cysteine-rich domain and the first half of the carboxy-terminal domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Molecular organization at the glycoprotein-complex-binding site of dystrophin. Three dystrophin-associated proteins bind directly to the carboxy-terminal portion of dystrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Skeletal and cardiac myopathies in mice lacking utrophin and dystrophin: a model for Duchenne muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Computed circular dichroism spectra for the evaluation of protein conformation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Minimum folding unit of dystrophin rod domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Single molecule force spectroscopy of spectrin repeats: low unfolding forces in helix bundles

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Dystrophin-glycoprotein complex is monomeric and stabilizes actin filaments in vitro through a lateral association

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

In vitro expressed dystrophin fragments do not associate with each other

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Calcium/calmodulin-dependent regulation of the NH2-terminal F-actin binding domain of utrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Characterization of dystrophin and utrophin diversity in the mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

Absence of correlation between utrophin localization and quantity and the clinical severity in Duchenne/Becker dystrophies

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.274.50.35375

21 January 2018

Identifiers

DOI

10.1074/JBC.274.50.35375

1 reference

2 September 2017

1 reference