The complement factor H-related proteins (Q38991052)

8 September 2017

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title

The complement factor H-related proteins (English)

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8 September 2017

Nicholas Medjeral-Thomas

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1

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PubMed ID

27782332

8 September 2017

Matthew C Pickering

series ordinal

2

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8 September 2017

1 November 2016

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8 September 2017

Immunological Reviews

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8 September 2017

274

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8 September 2017

1

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8 September 2017

191-201

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Accelerated nephrotoxic nephritis is exacerbated in C1q-deficient mice

8 September 2017

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Molecules Great and Small: The Complement System

21 January 2018

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Complement: a key system for immune surveillance and homeostasis

21 January 2018

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Structure and activation of the C1 complex of complement: unraveling the puzzle.

21 January 2018

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Two mechanisms for mannose-binding protein modulation of the activity of its associated serine proteases

21 January 2018

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MASP-1, a promiscuous complement protease: structure of its catalytic region reveals the basis of its broad specificity

21 January 2018

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The tick-over theory revisited: formation and regulation of the soluble alternative complement C3 convertase (C3(H2O)Bb)

21 January 2018

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Formation of the initial C3 convertase of the alternative complement pathway. Acquisition of C3b-like activities by spontaneous hydrolysis of the putative thioester in native C3

21 January 2018

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Specificity of the thioester-containing reactive site of human C3 and its significance to complement activation

21 January 2018

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Complement dysregulation and disease: from genes and proteins to diagnostics and drugs.

21 January 2018

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Properdin: binding to C3b and stabilization of the C3b-dependent C3 convertase

21 January 2018

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Properdin can initiate complement activation by binding specific target surfaces and providing a platform for de novo convertase assembly

21 January 2018

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The killer molecule of complement

21 January 2018

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Complement membrane attack complex stimulates production of reactive oxygen metabolites by cultured rat mesangial cells

21 January 2018

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The human complement factor H: functional roles, genetic variations and disease associations

21 January 2018

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Human complement C3b inactivator: isolation, characterization, and demonstration of an absolute requirement for the serum protein beta1H for cleavage of C3b and C4b in solution

21 January 2018

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Control of the amplification convertase of complement by the plasma protein beta1H

21 January 2018

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Functional anatomy of complement factor H.

21 January 2018

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Truncated forms of human complement factor H.

21 January 2018

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FHL-1/reconectin: a human complement and immune regulator with cell-adhesive function

21 January 2018

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Quantitative variations of the C3b/C4b receptor (CR1) in human erythrocytes are controlled by genes within the regulator of complement activation (RCA) gene cluster

21 January 2018

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A radiation hybrid map of complement factor H and factor H-related genes

21 January 2018

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Clustering of missense mutations in the C-terminal region of factor H in atypical hemolytic uremic syndrome.

21 January 2018

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Determining the population frequency of the CFHR3/CFHR1 deletion at 1q32.

21 January 2018

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Complement factor H related proteins in immune diseases

21 January 2018

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Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome

21 January 2018

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Factor H family proteins and human diseases

21 January 2018

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Characterization of complement factor H-related (CFHR) proteins in plasma reveals novel genetic variations of CFHR1 associated with atypical hemolytic uremic syndrome

21 January 2018

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Plasma lipopolysaccharide-binding protein is found associated with a particle containing apolipoprotein A-I, phospholipid, and factor H-related proteins

21 January 2018

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Complement factor H related proteins (CFHRs)

21 January 2018

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Dimerization of complement factor H-related proteins modulates complement activation in vivo

21 January 2018

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C3 glomerulopathy-associated CFHR1 mutation alters FHR oligomerization and complement regulation

21 January 2018

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Recent insights into C3 glomerulopathy

21 January 2018

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21 January 2018

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An imbalance of human complement regulatory proteins CFHR1, CFHR3 and factor H influences risk for age-related macular degeneration (AMD)

21 January 2018

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The human factor H-related protein 4 (FHR-4). A novel short consensus repeat-containing protein is associated with human triglyceride-rich lipoproteins

21 January 2018

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FHR-4A: a new factor H-related protein is encoded by the human FHR-4 gene.

21 January 2018

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Human factor H-related protein 5 has cofactor activity, inhibits C3 convertase activity, binds heparin and C-reactive protein, and associates with lipoprotein.

21 January 2018

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21 January 2018

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Complement factor H and related proteins: an expanding family of complement-regulatory proteins?

21 January 2018

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Human factor H-related protein 2 (CFHR2) regulates complement activation

21 January 2018

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Functional properties of complement factor H-related proteins FHR-3 and FHR-4: binding to the C3d region of C3b and differential regulation by heparin

21 January 2018

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Human factor H-related protein 5 (FHR-5). A new complement-associated protein

21 January 2018

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21 January 2018

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21 January 2018

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Human complement factor H-related protein 4 binds and recruits native pentameric C-reactive protein to necrotic cells

21 January 2018

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Identification of a mutation in complement factor H-related protein 5 in patients of Cypriot origin with glomerulonephritis

21 January 2018

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A novel CFHR5 fusion protein causes C3 glomerulopathy in a family without Cypriot ancestry

21 January 2018

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A hybrid CFHR3-1 gene causes familial C3 glomerulopathy.

21 January 2018

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Complement factor H-related hybrid protein deregulates complement in dense deposit disease

21 January 2018

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Factor H and factor H-related protein 1 bind to human neutrophils via complement receptor 3, mediate attachment to Candida albicans, and enhance neutrophil antimicrobial activity.

21 January 2018

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Neisseria meningitidis recruits factor H using protein mimicry of host carbohydrates

21 January 2018

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Competition between antagonistic complement factors for a single protein on N. meningitidis rules disease susceptibility

21 January 2018

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Antiphagocytic activity of streptococcal M protein: selective binding of complement control protein factor H.

21 January 2018

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Binding of human factor H-related protein 1 to serum-resistant Borrelia burgdorferi is mediated by borrelial complement regulator-acquiring surface proteins

21 January 2018

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LfhA, a novel factor H-binding protein of Leptospira interrogans

21 January 2018

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Immune evasion of the human pathogen Pseudomonas aeruginosa: elongation factor Tuf is a factor H and plasminogen binding protein

21 January 2018

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Gpm1p is a factor H-, FHL-1-, and plasminogen-binding surface protein of Candida albicans

21 January 2018

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Genetics of HUS: the impact of MCP, CFH, and IF mutations on clinical presentation, response to treatment, and outcome

21 January 2018

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De novo gene conversion in the RCA gene cluster (1q32) causes mutations in complement factor H associated with atypical hemolytic uremic syndrome

21 January 2018

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Eculizumab long-term therapy for pediatric renal transplant in aHUS with CFH/CFHR1 hybrid gene

21 January 2018

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Functional analysis in serum from atypical Hemolytic Uremic Syndrome patients reveals impaired protection of host cells associated with mutations in factor H.

21 January 2018

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A novel atypical hemolytic uremic syndrome-associated hybrid CFHR1/CFH gene encoding a fusion protein that antagonizes factor H-dependent complement regulation

21 January 2018

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Association of factor H autoantibodies with deletions of CFHR1, CFHR3, CFHR4, and with mutations in CFH, CFI, CD46, and C3 in patients with atypical hemolytic uremic syndrome

21 January 2018

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Anti factor H autoantibodies block C-terminal recognition function of factor H in hemolytic uremic syndrome

21 January 2018

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Abnormalities in the alternative pathway of complement in children with hematopoietic stem cell transplant-associated thrombotic microangiopathy

21 January 2018

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Association of genetic variants in complement factor H and factor H-related genes with systemic lupus erythematosus susceptibility

21 January 2018

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Complement factor H polymorphism and age-related macular degeneration

21 January 2018

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A common CFH haplotype, with deletion of CFHR1 and CFHR3, is associated with lower risk of age-related macular degeneration

21 January 2018

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Update on C3 glomerulopathy.

21 January 2018

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New developments in the genetics, pathogenesis, and therapy of IgA nephropathy

21 January 2018

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Genome-wide association study identifies susceptibility loci for IgA nephropathy

21 January 2018

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Geographic differences in genetic susceptibility to IgA nephropathy: GWAS replication study and geospatial risk analysis

21 January 2018

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Variants in Complement Factor H and Complement Factor H-Related Protein Genes, CFHR3 and CFHR1, Affect Complement Activation in IgA Nephropathy

21 January 2018

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21 January 2018

Identifiers

DOI

10.1111/IMR.12477

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8 September 2017

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PubMed ID

27782332