Chemical chaperones reduce endoplasmic reticulum stress and prevent mutant HFE aggregate formation (Q40108203)

17 September 2017

Chemical chaperones reduce endoplasmic reticulum stress and prevent mutant HFE aggregate formation (English)

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17 September 2017

endoplasmic reticulum

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17 September 2017

Maria do Carmo Fonseca

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17 September 2017

Jorge E Azevedo

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Maria de Sousa

object named as

Maria de Sousa

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author name string

Gonçalo Picarote

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17 September 2017

John V Fleming

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17 September 2017

language of work or name

English

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publication date

11 July 2007

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Journal of Biological Chemistry

17 September 2017

8

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based on heuristic

inferred from page(s)

published in

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282

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17 September 2017

27905-27912

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17 September 2017

38

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A novel MHC class I-like gene is mutated in patients with hereditary haemochromatosis

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Mammalian transcription factor ATF6 is synthesized as a transmembrane protein and activated by proteolysis in response to endoplasmic reticulum stress

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ER stress regulation of ATF6 localization by dissociation of BiP/GRP78 binding and unmasking of Golgi localization signals

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XBP1 mRNA is induced by ATF6 and spliced by IRE1 in response to ER stress to produce a highly active transcription factor

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Effect of tauroursodeoxycholic acid on endoplasmic reticulum stress-induced caspase-12 activation

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Chemical chaperones reduce ER stress and restore glucose homeostasis in a mouse model of type 2 diabetes

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Common structure and toxic function of amyloid oligomers implies a common mechanism of pathogenesis

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Protofibrils, pores, fibrils, and neurodegeneration: separating the responsible protein aggregates from the innocent bystanders

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Molecular chaperones and protein quality control

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Identifiers

DOI

10.1074/JBC.M702672200

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17 September 2017

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