I-cell disease: Isoelectric focusing, concanavalin asepharose 4B binding and kinetic properties of human lier acid β-d-galactosidases (Q41352808)

29 September 2017

title

I-Cell disease: isoelectric focusing, concanavalin A-Sepharose 4B binding and kinetic properties of human liver acid beta-D-galactosidases (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A413580

29 June 2022

I-cell disease: Isoelectric focusing, concanavalin asepharose 4B binding and kinetic properties of human lier acid β-d-galactosidases (English)

1 reference

https://api.crossref.org/works/10.1016/0005-2744(78)90333-9

25 April 2023

1 reference

A. L. Miller

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A413580

29 June 2022

language of work or name

English

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=413580

29 June 2022

publication date

1 January 1978

1 reference

29 September 2017

12 January 1978

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=413580

full work available at URL

29 June 2022

https://api.elsevier.com/content/article/PII:0005274478903339?httpAccept=text/xml

1 reference

https://api.crossref.org/works/10.1016/0005-2744(78)90333-9

https://api.elsevier.com/content/article/PII:0005274478903339?httpAccept=text/plain

25 April 2023

1 reference

https://api.crossref.org/works/10.1016/0005-2744(78)90333-9

Biochimica et Biophysica Acta

25 April 2023

published in

1 reference

29 September 2017

volume

522

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29 September 2017

issue

1

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29 September 2017

page(s)

174-186

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Mutant enzymatic and cytological phenotypes in cultured human fibroblasts

29 September 2017

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25 April 2023

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Purification of human liver acid beta-D-galactosidases using affinity chromatography

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Binding of human liver beta-galactosidases to plant lectins insolubilized on agarose

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Differential effect of chloride ions on β-galactosidase isoenzymes: A method for separate assay

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Separation of beta-galactosidases and beta-glucosidases from human liver

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Affinity chromatography of glycopeptides using concanavalin A

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Structure of the three major sialyl-oligosaccharides excreted in the urine of five patients with three distinct inborn diseases: "I cell disease" and two new types of mucolipidosis

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25 April 2023

Identifiers

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29 September 2017

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