The transforming growth factor-Beta signaling pathway involvement in cardiovascular lesions in mucopolysaccharidosis-I. (Q42183672)

18 October 2017

The transforming growth factor-Beta signaling pathway involvement in cardiovascular lesions in mucopolysaccharidosis-I. (English)

1 reference

18 October 2017

S Yano

1

1 reference

PMCID

3575049

18 October 2017

C Li

series ordinal

2

1 reference

PMCID

3575049

18 October 2017

Z Pavlova

series ordinal

3

1 reference

18 October 2017

18 April 2012

1 reference

Journal of Inherited Metabolic Disorders Reports

18 October 2017

1 reference

18 October 2017

7

1 reference

18 October 2017

55-58

1 reference

Arterial pathology in canine mucopolysaccharidosis-I and response to therapy

18 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Upregulation of elastase proteins results in aortic dilatation in mucopolysaccharidosis I mice

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

TGF-beta signaling in vascular fibrosis.

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Fibrosis in heart disease: understanding the role of transforming growth factor-beta in cardiomyopathy, valvular disease and arrhythmia

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

A critical role for elastin signaling in vascular morphogenesis and disease

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

N-acetyl-Ser-Asp-Lys-Pro inhibits phosphorylation of Smad2 in cardiac fibroblasts.

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Impaired elastogenesis in Hurler disease: dermatan sulfate accumulation linked to deficiency in elastin-binding protein and elastic fiber assembly

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

The structure of acid mucopolysaccharides produced by Hurler fibroblasts in tissue culture

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Reversal of clinical features of Hurler's disease and biochemical improvement after treatment by bone-marrow transplantation

26 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

The heart in the Hurler syndrome: gross, histologic and ultrastructural observations in five necropsy cases

29 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Increased deposition of chondroitin/dermatan sulfate glycosaminoglycan and upregulation of β1,3-glucuronosyltransferase I in pulmonary fibrosis

29 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Postmortem studies on a patient with mucopolysaccharidosis type I: histopathological findings after one year of enzyme replacement therapy

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

A follow-up study of MPS I patients treated with laronidase enzyme replacement therapy for 6 years.

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3575049

Coronary artery disease in the Hurler syndrome. Qualitative and quantitative analysis of the extent of coronary narrowing at necropsy in six children

17 August 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23430495

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

CARDIOVASCULAR MANIFESTATIONS OF THE HURLER SYNDROME: HEMODYNAMIC AND ANGIOCARDIOGRAPHIC OBSERVATIONS IN 15 PATIENTS

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23430495

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1007/8904_2012_141

1 reference

18 October 2017

1 reference

18 October 2017

1 reference

PMCID

3575049