Degradation of membrane-bound ganglioside GM2 by beta -hexosaminidase A. Stimulation by GM2 activator protein and lysosomal lipids (Q43559357)

24 November 2017

title

Degradation of membrane-bound ganglioside GM2 by beta -hexosaminidase A. Stimulation by GM2 activator protein and lysosomal lipids (English)

1 reference

24 November 2017

0 references

Werth N

1

1 reference

24 November 2017

Schuette CG

2

1 reference

24 November 2017

Wilkening G

3

1 reference

24 November 2017

Lemm T

4

1 reference

24 November 2017

Sandhoff K

5

1 reference

24 November 2017

language of work or name

English

0 references

publication date

16 January 2001

1 reference

Journal of Biological Chemistry

24 November 2017

number of pages

6

1 reference

based on heuristic

inferred from page(s)

published in

1 reference

24 November 2017

volume

276

1 reference

24 November 2017

issue

16

1 reference

24 November 2017

page(s)

12685-12690

1 reference

Topology of glycosphingolipid degradation

24 November 2017

cites work

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Lysosomal degradation on vesicular membrane surfaces. Enhanced glucosylceramide degradation by lysosomal anionic lipids and activators.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Enzyme alterations and lipid storage in three variants of Tay-Sachs disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Interaction of the GM2-activator protein with phospholipid-ganglioside bilayer membranes and with monolayers at the air-water interface

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

A lipid associated with the antiphospholipid syndrome regulates endosome structure and function

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

The biological role of dolichol

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Complete localization of disulfide bonds in GM2 activator protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Small-volume extrusion apparatus for preparation of large, unilamellar vesicles

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Characterization of an alternatively spliced GM2 activator protein, GM2A protein. An activator protein which stimulates the enzymatic hydrolysis of N-acetylneuraminic acid, but not N-acetylgalactosamine, from GM2.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Fluorescence probe measurement of the intralysosomal pH in living cells and the perturbation of pH by various agents

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Degradation of membrane-bound ganglioside GM1. Stimulation by bis(monoacylglycero)phosphate and the activator proteins SAP-B and GM2-AP.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Activator proteins and topology of lysosomal sphingolipid catabolism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Sphingolipid activator protein D (sap-D) stimulates the lysosomal degradation of ceramide in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Photoaffinity labeling of human lysosomal beta-hexosaminidase B. Identification of Glu-355 at the substrate binding site

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Specificity of human liver hexosaminidases A and B against glycosphingolipids GM2 and GA2. Purification of the enzymes by affinity chromatography employing specific elution

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Biosynthesis, processing, and intracellular transport of GM2 activator protein in human epidermal keratinocytes. The lysosomal targeting of the GM2 activator is independent of a mannose-6-phosphate signal

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Effect of saposins A and C on the enzymatic hydrolysis of liposomal glucosylceramide

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Complexing of Glycolipids and Their Transfer between Membranes by the Activator Protein for Degradation of Lysosomal Ganglioside GM2

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Prosaposin deficiency: further characterization of the sphingolipid activator protein-deficient sibs. Multiple glycolipid elevations (including lactosylceramidosis), partial enzyme deficiencies and ultrastructure of the skin in this generalized sphi

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Activating Proteins for Ganglioside GM2Degradation by β-Hexosaminidase Isoenzymes in Tissue Extracts from Different Species

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

Electron paramagnetic resonance studies on the fluidity and surface dynamics of egg phosphatidylcholine vesicles containing gangliosides

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007970200

21 January 2018

Identifiers

DOI

10.1074/JBC.M007970200

1 reference

24 November 2017

1 reference