Effect of pirfenidone on the pulmonary fibrosis of Hermansky-Pudlak syndrome (Q44070468)

29 November 2017

Effect of pirfenidone on the pulmonary fibrosis of Hermansky-Pudlak syndrome (English)

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29 November 2017

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William A Gahl

1

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29 November 2017

Mark Brantly

2

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29 November 2017

James Troendle

3

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29 November 2017

Nilo A Avila

4

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29 November 2017

Antonio Padua

5

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29 November 2017

Carlos Montalvo

6

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29 November 2017

Hilda Cardona

7

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29 November 2017

Karim Anton Calis

8

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29 November 2017

Bernadette Gochuico

9

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29 November 2017

1 July 2002

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Molecular Genetics and Metabolism

29 November 2017

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29 November 2017

76

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29 November 2017

3

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29 November 2017

234-242

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Genetic defects and clinical characteristics of patients with a form of oculocutaneous albinism (Hermansky-Pudlak syndrome)

29 November 2017

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Reliability of absent platelet dense bodies as a diagnostic criterion for Hermansky-Pudlak syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Positional cloning of a gene for Hermansky-Pudlak syndrome, a disorder of cytoplasmic organelles

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

A new variant of Hermansky-Pudlak syndrome due to mutations in a gene responsible for vesicle formation

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Altered trafficking of lysosomal proteins in Hermansky-Pudlak syndrome due to mutations in the beta 3A subunit of the AP-3 adaptor

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Mutation of a new gene causes a unique form of Hermansky-Pudlak syndrome in a genetic isolate of central Puerto Rico

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Hermansky-Pudlak syndrome type 3 in Ashkenazi Jews and other non-Puerto Rican patients with hypopigmentation and platelet storage-pool deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Hermansky-Pudlak syndrome is caused by mutations in HPS4, the human homolog of the mouse light-ear gene

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Pulmonary function and high-resolution CT findings in patients with an inherited form of pulmonary fibrosis, Hermansky-Pudlak syndrome, due to mutations in HPS-1.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Hermansky-Pudlak syndrome. Pulmonary manifestations of a ceroid storage disorder

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Pirfenidone in idiopathic pulmonary fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Pirfenidone diminishes cyclophosphamide-induced lung fibrosis in mice

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Small airways in idiopathic pulmonary fibrosis. Comparison of morphologic and physiologic observations

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Pharmacokinetics of an antifibrotic agent, pirfenidone, in haemodialysis patients.

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Hermansky-Pudlak syndrome: models for intracellular vesicle formation

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Hermansky-Pudlak syndrome and related disorders of organelle formation

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

TGF-beta is a critical mediator of acute lung injury

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Treatment of idiopathic pulmonary fibrosis with a new antifibrotic agent, pirfenidone: results of a prospective, open-label Phase II study

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Idiopathic Pulmonary Fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Lung function among asbestos cement factory workers: cross-sectional and longitudinal study

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

Determinants of progression in idiopathic pulmonary fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1096-7192%2802%2900044-6

7 January 2021

10.1016/S1096-7192(02)00044-6

Identifiers

DOI

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release_nxeqrk6z4rftpafgmuuxjncu34

29 November 2017

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Fatcat

https://api.fatcat.wiki/v0/release/nxeqrk6z4rftpafgmuuxjncu34

24 November 2022

mapped directly with Wikidata item

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