Aggregate formation in the spinal cord of mutant SOD1 transgenic mice is reversible and mediated by proteasomes (Q44658075)

5 December 2017

Aggregate formation in the spinal cord of mutant SOD1 transgenic mice is reversible and mediated by proteasomes (English)

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5 December 2017

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https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

2 April 2024

2

Cezary Wojcik

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14622116

2 April 2024

author name string

Krishna Puttaparthi

1

1 reference

5 December 2017

Bhagya Rajendran

3

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5 December 2017

George N. DeMartino

4

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14622116

2 April 2024

Jeffrey L. Elliott

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14622116

2 April 2024

language of work or name

English

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publication date

1 November 2003

1 reference

full work available at URL

5 December 2017

https://onlinelibrary.wiley.com/doi/pdfdirect/10.1046/j.1471-4159.2003.02028.x

file format

Portable Document Format

online access status

open access

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14622116

https://api.wiley.com/onlinelibrary/tdm/v1/articles/10.1046%2Fj.1471-4159.2003.02028.x

2 April 2024

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

https://onlinelibrary.wiley.com/doi/pdf/10.1046/j.1471-4159.2003.02028.x

2 April 2024

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Journal of Neurochemistry

2 April 2024

published in

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5 December 2017

87

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5 December 2017

851-860

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5 December 2017

4

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Relative functions of the alpha and beta subunits of the proteasome activator, PA28

5 December 2017

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https://api.crossref.org/works/10.1046%2FJ.1471-4159.2003.02028.X

Impairment of the ubiquitin-proteasome system by protein aggregation

21 January 2018

1

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

2 April 2024

2

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

From Charcot to SOD1: mechanisms of selective motor neuron death in ALS.

2 April 2024

3

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Oxidation versus aggregation - how do SOD1 mutants cause ALS?

2 April 2024

4

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

The proteasome, a novel protease regulated by multiple mechanisms

2 April 2024

5

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Proteasomes and proteasome inhibition in the central nervous system

2 April 2024

6

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https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Experimental models of amyotrophic lateral sclerosis

2 April 2024

7

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https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Restricted expression of G86R Cu/Zn superoxide dismutase in astrocytes results in astrocytosis but does not cause motoneuron degeneration

2 April 2024

8

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

2 April 2024

9

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

2 April 2024

10

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Decreased levels of proteasome activity and proteasome expression in aging spinal cord

2 April 2024

11

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Accumulation of SOD1 mutants in postnatal motoneurons does not cause motoneuron pathology or motoneuron disease

2 April 2024

12

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

The herbicide paraquat causes up-regulation and aggregation of alpha-synuclein in mice: paraquat and alpha-synuclein

2 April 2024

13

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Proteasomal-dependent aggregate reversal and absence of cell death in a conditional mouse model of Huntington's disease.

2 April 2024

14

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

cDNA cloning, expression, and functional characterization of PI31, a proline-rich inhibitor of the proteasome

2 April 2024

15

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Valosin-containing protein is a multi-ubiquitin chain-targeting factor required in ubiquitin-proteasome degradation

2 April 2024

16

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Neuron-specific expression of mutant superoxide dismutase 1 in transgenic mice does not lead to motor impairment.

2 April 2024

17

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Disease progression in a transgenic model of familial amyotrophic lateral sclerosis is dependent on both neuronal and non-neuronal zinc binding proteins

2 April 2024

18

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

2 April 2024

19

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

2 April 2024

20

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

2 April 2024

21

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Chronic inhibition of glutamate uptake produces a model of slow neurotoxicity

2 April 2024

22

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement.

2 April 2024

23

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Proteasomal inhibition by misfolded mutant superoxide dismutase 1 induces selective motor neuron death in familial amyotrophic lateral sclerosis

2 April 2024

25

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

High molecular weight complexes of mutant superoxide dismutase 1: age-dependent and tissue-specific accumulation

2 April 2024

26

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues

2 April 2024

27

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

2 April 2024

28

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

Reversal of neuropathology and motor dysfunction in a conditional model of Huntington's disease

2 April 2024

29

1 reference

https://api.crossref.org/works/10.1046/J.1471-4159.2003.02028.X

2 April 2024

Identifiers

1 reference

5 December 2017

1 reference