The GM2 activator protein, its roles as a co-factor in GM2 hydrolysis and as a general glycolipid transport protein. (Q52037999)

20 April 2018

review article

1 reference

title

The GM2 activator protein, its roles as a co-factor in GM2 hydrolysis and as a general glycolipid transport protein. (English)

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20 April 2018

author name string

D J Mahuran

series ordinal

1

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20 April 2018

publication date

1 July 1998

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20 April 2018

Biochimica et Biophysica Acta

published in

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20 April 2018

volume

1393

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20 April 2018

issue

1

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20 April 2018

page(s)

1-18

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20 April 2018

AB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2

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Biochemical characterization of the Cys138Arg substitution associated with the AB variant form of GM2 gangliosidosis: evidence that Cys138 is required for the recognition of the GM2 activator/GM2 ganglioside complex by beta-hexosaminidase A

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Gangliosides are neuronal ligands for myelin-associated glycoprotein

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The abnormal occurrence and the differentiation-dependent distribution of N-acetyl and N-glycolyl species of the ganglioside GM2 in human germ cell tumors. A study with specific monoclonal antibodies

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Ganglioside GM1 binds to the Trk protein and regulates receptor function

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7 January 2021

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7 January 2021

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Mouse models of Tay-Sachs and Sandhoff diseases differ in neurologic phenotype and ganglioside metabolism

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7 January 2021

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Identifiers

DOI

10.1016/S0005-2760(98)00057-5

1 reference

20 April 2018

release_obthe5ve5rg7bdr5jm6wzvmceu

Fatcat ID

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https://api.fatcat.wiki/v0/release/obthe5ve5rg7bdr5jm6wzvmceu

mapped directly with Wikidata item

24 November 2022

based on heuristic

PubMed ID

9714704

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20 April 2018