Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts (Q57006982)

Cristina Capanni

6

0 references

Paola Braghetta

Paola Braghetta

4

0 references

Guglielmina Pepe

Guglielmina Pepe

10

0 references

Stefano Squarzoni

Stefano Squarzoni

14

0 references

Giovanna Lattanzi

Giovanna Lattanzi

3

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Luciano Merlini

Luciano Merlini

12

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Enrico Bertini

Enrico Bertini

11

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Nadir Mario Maraldi

13

Nadir M. Maraldi

0 references

Patrizia Sabatelli

1

Patrizia Sabatelli

0 references

Marta Columbaro

8

Marta Columbaro

0 references

Natascha Bergamin

5

Natascha Bergamin

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author name string

P Sabatelli

1

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P Bonaldo

2

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G Lattanzi

3

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P Braghetta

4

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N Bergamin

5

0 references

C Capanni

6

0 references

E Mattioli

7

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M Columbaro

8

0 references

A Ognibene

9

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G Pepe

10

0 references

E Bertini

11

0 references

L Merlini

12

0 references

N M Maraldi

13

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S Squarzoni

14

0 references

Paolo Bonaldo

2

0 references

Andrea Ognibene

Structural and functional features of the alpha 3 chain indicate a bridging role for chicken collagen VI in connective tissues

9

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language of work or name

English

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publication date

November 2001

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published in

Matrix Biology

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volume

20

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issue

7

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page(s)

475-86

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475-486

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cites work

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Distinct regions control transcriptional activation of the alpha1(VI) collagen promoter in different tissues of transgenic mice

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Type VI collagen in extracellular, 100-nm periodic filaments and fibrils: identification by immunoelectron microscopy

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Regulation of extracellular matrix gene expression by mechanical stress

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Secretion and matrix assembly of recombinant type VI collagen.

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Integrin-mediated muscle cell spreading. The role of protein kinase c in outside-in and inside-out signaling and evidence of integrin cross-talk

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Binding of soluble form of fibroblast surface protein, fibronectin, to collagen

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Modulation of cell proliferation and differentiation through substrate-dependent changes in fibronectin conformation

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Analysis of fibronectin and vitronectin receptors on human fetal skeletal muscle cells upon differentiation

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Codistribution of heparan sulfate proteoglycan, laminin, and fibronectin in the extracellular matrix of normal rat kidney cells and their coordinate absence in transformed cells

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Integrin signaling and cell growth control

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Type VI collagen increases cell survival and prevents anti-beta 1 integrin-mediated apoptosis

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Perlecan: a gem of a proteoglycan

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Type VI collagen mutations in Bethlem myopathy, an autosomal dominant myopathy with contractures

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Bethlem myopathy: a slowly progressive congenital muscular dystrophy with contractures

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Physical state of the extracellular matrix regulates the structure and molecular composition of cell-matrix adhesions

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Ultrastructure of type VI collagen in human skin and cartilage suggests an anchoring function for this filamentous network

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Molecular composition of type VI collagen. Evidence for chain heterogeneity in mammalian tissues and cultured cells

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Type VI collagen anchors endothelial basement membranes by interacting with type IV collagen

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Reduced collagen VI causes Bethlem myopathy: a heterozygous COL6A1 nonsense mutation results in mRNA decay and functional haploinsufficiency

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The role of the alpha3(VI) chain in collagen VI assembly. Expression of an alpha3(VI) chain lacking N-terminal modules N10-N7 restores collagen VI assembly, secretion, and matrix deposition in an alpha3(VI)-deficient cell line

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Bethlem myopathy and engineered collagen VI triple helical deletions prevent intracellular multimer assembly and protein secretion

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A fibronectin self-assembly site involved in fibronectin matrix assembly: reconstruction in a synthetic peptide

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Fibronectin and integrins in cell adhesion, signaling, and morphogenesis.

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A novel de novo mutation in the triple helix of the COL6A3 gene in a two-generation Italian family affected by Bethlem myopathy. A diagnostic approach in the mutations' screening of type VI collagen

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A heterozygous splice site mutation in COL6A1 leading to an in-frame deletion of the alpha1(VI) collagen chain in an italian family affected by bethlem myopathy

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Integrin and Arg-Gly-Asp dependence of cell adhesion to the native and unfolded triple helix of collagen type VI

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Transcriptional Activation of the α1(VI) Collagen Gene during Myoblast Differentiation Is Mediated by Multiple GA Boxes

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Structure of fibronectin and its fragments in electron microscopy

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Soluble collagen VI drives serum-starved fibroblasts through S phase and prevents apoptosis via down-regulation of Bax.

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Soluble collagen VI induces tyrosine phosphorylation of paxillin and focal adhesion kinase and activates the MAP kinase erk2 in fibroblasts

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Fibronectin fibrillogenesis: a paradigm for extracellular matrix assembly

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Control of cell cycle progression by fibronectin matrix architecture

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Recombinant expression and structural and binding properties of alpha 1(VI) and alpha 2(VI) chains of human collagen type VI

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Type VI collagen represents a major fraction of connective tissue collagens

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Biglycan and decorin bind close to the n-terminal region of the collagen VI triple helix

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