Quantitation of acyl-CoA and acylcarnitine esters accumulated during abnormal mitochondrial fatty acid oxidation (Q59697241)

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4

L. A. Bindoff

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5

S. Eaton

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N. J. Watmough

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author name string

R. S. Kler

1

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S. Jackson

2

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K. Bartlett

3

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M. Pourfarzam

6

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F. E. Frerman

7

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S. I. Goodman

8

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D. M. Turnbull

10

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full work available at URL

14 November 2022

language of work or name

English

0 references

publication date

5 December 1991

0 references

http://intl.jbc.org/cgi/content/abstract/266/34/22932

online access status

open access

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1744086

https://api.elsevier.com/content/article/PII:S0021925818544446?httpAccept=text/xml

14 November 2022

1 reference

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https://api.elsevier.com/content/article/PII:S0021925818544446?httpAccept=text/plain

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1 reference

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Journal of Biological Chemistry

14 November 2022

published in

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volume

266

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issue

34

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page(s)

22932-8

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cites work

Neonatal glutaric aciduria type II: an X-linked recessive inherited disorder

3

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Fluorometric assay of acyl-CoA dehydrogenases in normal and mutant human fibroblasts

14 November 2022

4

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Long-chain acyl coenzyme A dehydrogenase deficiency: an inherited cause of nonketotic hypoglycemia.

14 November 2022

6

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency

14 November 2022

8

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Isolation of a malonyl-CoA-sensitive CPT/beta-oxidation enzyme complex from heart mitochondria

14 November 2022

9

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

In vitro fibroblast studies in a patient with C6-C10-dicarboxylic aciduria: evidence for a defect in general acyl-CoA dehydrogenase

14 November 2022

10

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Glutaric acidemia type II: heterogeneity of clinical and biochemical phenotypes

14 November 2022

11

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Protein measurement with the Folin phenol reagent

14 November 2022

12

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

A comparison of [9,10-3H]palmitic and [9,10-3H]myristic acids for the detection of defects of fatty acid oxidation in intact cultured fibroblasts

14 November 2022

13

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Regulation of hepatic fatty acid oxidation and ketone body production

14 November 2022

14

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Metabolic consequences of methylenecyclopropylglycine poisoning in rats

14 November 2022

15

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Complementation analysis of fatty acid oxidation disorders

14 November 2022

16

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Dicarboxylic aciduria: deficient [1-14C]octanoate oxidation and medium-chain acyl-CoA dehydrogenase in fibroblasts

14 November 2022

18

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Oxidation of fatty acids in cultured fibroblasts: a model system for the detection and study of defects in oxidation

14 November 2022

19

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

The role of intermediates in mitochondrial fatty acid oxidation

14 November 2022

24

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels

14 November 2022

25

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Intermediates in fatty acid oxidation

14 November 2022

26

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Tetracyano-2,2-bipyridineiron(iii), an improved electron acceptor for the spectrophotometric assay of beta-oxidation and of succinate dehydrogenase in intact mitochondria

14 November 2022

27

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Short-chain acyl-CoA dehydrogenase deficiency associated with a lipid-storage myopathy and secondary carnitine deficiency.

14 November 2022

28

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Multiple acyl-CoA dehydrogenase deficiency: a neonatal onset case responsive to treatment

14 November 2022

29

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

14CO2 production is no adequate measure of [14C]fatty acid oxidation.

14 November 2022

30

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Measurement of the acyl-CoA intermediates of beta-oxidation by h.p.l.c. with on-line radiochemical and photodiode-array detection. Application to the study of [U-14C]hexadecanoate oxidation by intact rat liver mitochondria

14 November 2022

31

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

Impaired mitochondrial beta-oxidation in a patient with an abnormality of the respiratory chain. Studies in skeletal muscle mitochondria

14 November 2022

32

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)54444-6

14 November 2022

Identifiers