Phytanic acid alpha-oxidation in peroxisomal disorders: studies in cultured human fibroblasts (Q73893093)

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7 November 2019

title

Phytanic acid alpha-oxidation in peroxisomal disorders: studies in cultured human fibroblasts (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

7 November 2019

main subject

2-hydroxyphytanoyl-CoA

1 reference

ChEBI release 2020-05-28

ChEBI ID

15475

2-hydroxyphytanic acid

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ChEBI release 2020-05-28

N M Verhoeven

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

7 November 2019

D S Schor

2

1 reference

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7 November 2019

C R Roe

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

7 November 2019

R J Wanders

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

7 November 2019

C Jakobs

5

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7 November 2019

language of work or name

English

0 references

publication date

1 October 1997

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

Biochimica et Biophysica Acta

7 November 2019

published in

1 reference

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7 November 2019

volume

1361

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7 November 2019

issue

3

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7 November 2019

page(s)

281-286

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

Identification of phytanoyl-CoA ligase as a distinct acyl-CoA ligase in peroxisomes from cultured human skin fibroblasts

7 November 2019

cites work

1 reference

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7 January 2021

Phytanic acid must be activated to phytanoyl-CoA prior to its alpha-oxidation in rat liver peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Phytanic acid alpha-oxidation in rat liver peroxisomes. Production of alpha-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

alpha-Oxidation of 3-methyl-substituted fatty acids in rat liver. Production of formic acid instead of CO2, cofactor requirements, subcellular localization and formation of a 2-hydroxy-3-methylacyl-CoA intermediate

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Formic acid is a product of the alpha-oxidation of fatty acids by human skin fibroblasts: deficiency of formic acid production in peroxisome-deficient fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Intraorganellar localization of CoASH-independent phytanic acid oxidation in human liver peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

α-Oxidation of 3-methyl-substituted fatty acids in rat liver

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Differential protein import deficiencies in human peroxisome assembly disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: direct, unequivocal evidence for the new, revised pathway of phytanic acid alpha-oxidation in humans

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

1 reference

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7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

In Vivo Study of Phytanic Acid α-Oxidation in Classic Refsum's Disease and Chondrodysplasia Punctata

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Postnatal diagnosis of peroxisomal disorders: a biochemical approach

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Phenotype of patients with peroxisomal disorders subdivided into sixteen complementation groups

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Complementation analysis of patients with intact peroxisomes and impaired peroxisomal beta-oxidation

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

2-Hydroxyphytanic acid oxidase activity in rat and human liver and its deficiency in the Zellweger syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

The formation of alpha-hydroxy phytanic acid from phytanic acid in mammalian tissues

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

Evidence against alpha-hydroxyphytanic acid as an intermediate in the metabolism of phytanic acid

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900045-8

7 January 2021

10.1016/S0925-4439(97)00045-8

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9375802%20AND%20SRC:MED&resulttype=core&format=json

7 November 2019

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