The human mitochondrial transcriptome and the RNA-binding proteins that regulate its expression (Q27016551)

Timothy R. Mercer

series ordinal

2

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language of work or name

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2012

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Wiley interdisciplinary reviews. RNA

published in

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volume

3

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issue

5

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page(s)

675-95

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The energetics of genome complexity

cites work

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Distinctive features of the 5'-terminal sequences of the human mitochondrial mRNAs

21 January 2018

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tRNA punctuation model of RNA processing in human mitochondria

21 January 2018

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Long noncoding RNAs are generated from the mitochondrial genome and regulated by nuclear-encoded proteins

21 January 2018

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The human mitochondrial transcriptome

21 January 2018

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The genetics and pathology of oxidative phosphorylation

21 January 2018

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Symmetrical In Vivo Transcription of Mitochondrial DNA in HeLa Cells

21 January 2018

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Identification of initiation sites for heavy-strand and light-strand transcription in human mitochondrial DNA

21 January 2018

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A tridecamer DNA sequence supports human mitochondrial RNA 3'-end formation in vitro

21 January 2018

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Initiation and beyond: multiple functions of the human mitochondrial transcription machinery

21 January 2018

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DNA replication and transcription in mammalian mitochondria

21 January 2018

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Mitochondrial DNA replication and repair: all a flap

21 January 2018

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Mitochondrial DNA maintenance in vertebrates

21 January 2018

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The human mitochondrial replication fork in health and disease

21 January 2018

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RNase P without RNA: identification and functional reconstitution of the human mitochondrial tRNA processing enzyme

21 January 2018

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Involvement of human ELAC2 gene product in 3' end processing of mitochondrial tRNAs

21 January 2018

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RNA processing in human mitochondria

21 January 2018

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Nuclear genetic defects of oxidative phosphorylation

21 January 2018

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A different genetic code in human mitochondria

21 January 2018

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Human mitochondrial mRNAs--like members of all families, similar but different

21 January 2018

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Polyadenylation and degradation of human mitochondrial RNA: the prokaryotic past leaves its mark

21 January 2018

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Polyadenylation and degradation of mRNA in mammalian mitochondria: a missing link?

21 January 2018

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RNA turnover in human mitochondria: more questions than answers?

21 January 2018

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Messenger RNA stability in mitochondria: different means to an end.

21 January 2018

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Polyadenylation in mammalian mitochondria: insights from recent studies.

21 January 2018

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Hungry codons promote frameshifting in human mitochondrial ribosomes

21 January 2018

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Targeting of the cytosolic poly(A) binding protein PABPC1 to mitochondria causes mitochondrial translation inhibition

21 January 2018

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PDE12 removes mitochondrial RNA poly(A) tails and controls translation in human mitochondria

21 January 2018

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LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs

21 January 2018

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Molecular dysfunction associated with the human mitochondrial 3302A>G mutation in the MTTL1 (mt-tRNALeu(UUR)) gene

21 January 2018

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Human mitochondrial RNA turnover caught in flagranti: involvement of hSuv3p helicase in RNA surveillance

21 January 2018

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Structure of transfer RNAs: similarity and variability

21 January 2018

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Mitochondrial tRNA 3' end metabolism and human disease.

21 January 2018

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Search for characteristic structural features of mammalian mitochondrial tRNAs.

21 January 2018

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Human mitochondrial tRNAs: biogenesis, function, structural aspects, and diseases

21 January 2018

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tRNA Modification and Genetic Code Variations in Animal Mitochondria

21 January 2018

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Identification and characterization of mammalian mitochondrial tRNA nucleotidyltransferases

21 January 2018

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A eubacterial origin for the human tRNA nucleotidyltransferase?

21 January 2018

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Global identification of microRNA-target RNA pairs by parallel analysis of RNA ends

21 January 2018

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Proteomic analysis of the mammalian mitochondrial ribosome. Identification of protein components in the 28 S small subunit

21 January 2018

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Structural compensation for the deficit of rRNA with proteins in the mammalian mitochondrial ribosome. Systematic analysis of protein components of the large ribosomal subunit from mammalian mitochondria

21 January 2018

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A structural model for the large subunit of the mammalian mitochondrial ribosome.

21 January 2018

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Structure of the Mammalian Mitochondrial Ribosome Reveals an Expanded Functional Role for Its Component Proteins

21 January 2018

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Identification of small non-coding RNAs from mitochondria and chloroplasts

21 January 2018

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Expression of a novel non-coding mitochondrial RNA in human proliferating cells.

21 January 2018

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Disruption of a mitochondrial RNA-binding protein gene results in decreased cytochrome b expression and a marked reduction in ubiquinol-cytochrome c reductase activity in mouse heart mitochondria

21 January 2018

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Mitochondrial transcription factors B1 and B2 activate transcription of human mtDNA

21 January 2018

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Architectural role of mitochondrial transcription factor A in maintenance of human mitochondrial DNA

21 January 2018

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In Arabidopsis thaliana, 1% of the genome codes for a novel protein family unique to plants

21 January 2018

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The PPR motif - a TPR-related motif prevalent in plant organellar proteins

21 January 2018

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Structure of human mitochondrial RNA polymerase

21 January 2018

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Multiple interactions involving the amino-terminal domain of yeast mtRNA polymerase determine the efficiency of mitochondrial protein synthesis

21 January 2018

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Stability of the mitochondrial genome requires an amino-terminal domain of yeast mitochondrial RNA polymerase

21 January 2018

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TEFM (c17orf42) is necessary for transcription of human mtDNA

21 January 2018

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tRNA recognition, processing, and disease: hypotheses around an unorthodox type of RNase P in human mitochondria

21 January 2018

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Processing mitochondrial (t)RNAs: new enzyme, old job.

21 January 2018

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Multiple functions of type 10 17beta-hydroxysteroid dehydrogenase

21 January 2018

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A single Arabidopsis organellar protein has RNase P activity.

21 January 2018

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Localization of human RNase Z isoforms: dual nuclear/mitochondrial targeting of the ELAC2 gene product by alternative translation initiation

21 January 2018

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A candidate prostate cancer susceptibility gene at chromosome 17p

21 January 2018

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A candidate prostate cancer susceptibility gene encodes tRNA 3' processing endoribonuclease

21 January 2018

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Pentatricopeptide repeat domain protein 1 lowers the levels of mitochondrial leucine tRNAs in cells

21 January 2018

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RNA processing in a tiny transcriptome.

21 January 2018

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Aminoacyl-tRNA synthetases

21 January 2018

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C to U editing and modifications during the maturation of the mitochondrial tRNA(Asp) in marsupials

21 January 2018

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Nuclear control of cloverleaf structure of human mitochondrial tRNA(Lys).

21 January 2018

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Missense mutation in pseudouridine synthase 1 (PUS1) causes mitochondrial myopathy and sideroblastic anemia (MLASA).

21 January 2018

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Mitochondrial myopathy and sideroblastic anemia (MLASA): missense mutation in the pseudouridine synthase 1 (PUS1) gene is associated with the loss of tRNA pseudouridylation

21 January 2018

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tRNA's wobble decoding of the genome: 40 years of modification

21 January 2018

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Mitochondria-specific RNA-modifying enzymes responsible for the biosynthesis of the wobble base in mitochondrial tRNAs. Implications for the molecular pathogenesis of human mitochondrial diseases

21 January 2018

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A human mitochondrial GTP binding protein related to tRNA modification may modulate phenotypic expression of the deafness-associated mitochondrial 12S rRNA mutation

21 January 2018

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Isolation and characterization of the putative nuclear modifier gene MTO1 involved in the pathogenesis of deafness-associated mitochondrial 12 S rRNA A1555G mutation

21 January 2018

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Taurine as a constituent of mitochondrial tRNAs: new insights into the functions of taurine and human mitochondrial diseases

21 January 2018

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Human mitochondrial diseases caused by lack of taurine modification in mitochondrial tRNAs

21 January 2018

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Codon-specific translational defect caused by a wobble modification deficiency in mutant tRNA from a human mitochondrial disease

21 January 2018

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Wobble modification defect in tRNA disturbs codon-anticodon interaction in a mitochondrial disease

21 January 2018

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Synthesis and investigation of the 5-formylcytidine modified, anticodon stem and loop of the human mitochondrial tRNAMet

21 January 2018

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Unconventional decoding of the AUA codon as methionine by mitochondrial tRNAMet with the anticodon f5CAU as revealed with a mitochondrial in vitro translation system

21 January 2018

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Mammalian mitochondrial methionyl-tRNA transformylase from bovine liver. Purification, characterization, and gene structure.

21 January 2018

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Recognition of tRNAs by Methionyl-tRNA transformylase from mammalian mitochondria

21 January 2018

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Mutations in MTFMT underlie a human disorder of formylation causing impaired mitochondrial translation

21 January 2018

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Phenotype of non-syndromic deafness associated with the mitochondrial A1555G mutation is modulated by mitochondrial RNA modifying enzymes MTO1 and GTPBP3

21 January 2018

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Biochemical evidence for nuclear gene involvement in phenotype of non-syndromic deafness associated with mitochondrial 12S rRNA mutation

21 January 2018

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Mutation in TRMU related to transfer RNA modification modulates the phenotypic expression of the deafness-associated mitochondrial 12S ribosomal RNA mutations

21 January 2018

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Elucidation of separate, but collaborative functions of the rRNA methyltransferase-related human mitochondrial transcription factors B1 and B2 in mitochondrial biogenesis reveals new insight into maternally inherited deafness

21 January 2018

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Human mitochondrial transcription factor B1 methylates ribosomal RNA at a conserved stem-loop

21 January 2018

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Human mitochondrial transcription factor B1 as a modifier gene for hearing loss associated with the mitochondrial A1555G mutation

21 January 2018

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Methylation of 12S rRNA is necessary for in vivo stability of the small subunit of the mammalian mitochondrial ribosome

21 January 2018

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Something old, something new, something borrowed ...

21 January 2018

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Mitochondrial stress engages E2F1 apoptotic signaling to cause deafness

21 January 2018

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Defective mitochondrial mRNA maturation is associated with spastic ataxia

21 January 2018

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Identification of a novel human nuclear-encoded mitochondrial poly(A) polymerase

21 January 2018

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Structural basis for dimerization and activity of human PAPD1, a noncanonical poly(A) polymerase

21 January 2018

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Human polynucleotide phosphorylase: location matters

21 January 2018

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Mammalian polynucleotide phosphorylase is an intermembrane space RNase that maintains mitochondrial homeostasis

21 January 2018

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LRPPRC is a mitochondrial matrix protein that is conserved in metazoans

21 January 2018

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The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster

21 January 2018

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LRPPRC and SLIRP interact in a ribonucleoprotein complex that regulates posttranscriptional gene expression in mitochondria.

21 January 2018

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Identification of a gene causing human cytochrome c oxidase deficiency by integrative genomics

21 January 2018

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Mitochondrial and nuclear genomic responses to loss of LRPPRC expression

21 January 2018

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A computational screen for regulators of oxidative phosphorylation implicates SLIRP in mitochondrial RNA homeostasis

21 January 2018

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Human ATP-dependent RNA/DNA helicase hSuv3p interacts with the cofactor of survivin HBXIP.

21 January 2018

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Localisation of the human hSuv3p helicase in the mitochondrial matrix and its preferential unwinding of dsDNA

21 January 2018

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Human mitochondrial SUV3 and polynucleotide phosphorylase form a 330-kDa heteropentamer to cooperatively degrade double-stranded RNA with a 3'-to-5' directionality

21 January 2018

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The 2-5A/RNase L/RNase L inhibitor (RLI) [correction of (RNI)] pathway regulates mitochondrial mRNAs stability in interferon alpha-treated H9 cells

21 January 2018

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Regulation of mitochondrial mRNA stability by RNase L is translation-dependent and controls IFNalpha-induced apoptosis

21 January 2018

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Mutation in TACO1, encoding a translational activator of COX I, results in cytochrome c oxidase deficiency and late-onset Leigh syndrome.

21 January 2018

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Unilateral aminoacylation specificity between bovine mitochondria and eubacteria

21 January 2018

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Dual mode recognition of two isoacceptor tRNAs by mammalian mitochondrial seryl-tRNA synthetase.

21 January 2018

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Crystal structure of human mitochondrial tyrosyl-tRNA synthetase reveals common and idiosyncratic features

21 January 2018

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Loss of a primordial identity element for a mammalian mitochondrial aminoacylation system.

21 January 2018

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Biogenesis of glutaminyl-mt tRNAGln in human mitochondria

21 January 2018

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Human diseases with impaired mitochondrial protein synthesis

21 January 2018

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Reconstructing the evolution of the mitochondrial ribosomal proteome.

21 January 2018

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The large subunit of the mammalian mitochondrial ribosome. Analysis of the complement of ribosomal proteins present

21 January 2018

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Properties of human mitochondrial ribosomes

21 January 2018

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Mitochondrial ribosomal proteins: candidate genes for mitochondrial disease

21 January 2018

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Mitochondrial ribosomal protein L12 selectively associates with human mitochondrial RNA polymerase to activate transcription

21 January 2018

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Termination of protein synthesis in mammalian mitochondria

21 January 2018

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Translation termination in human mitochondrial ribosomes.

21 January 2018

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How do mammalian mitochondria synthesize proteins?

21 January 2018

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Unique features of animal mitochondrial translation systems. The non-universal genetic code, unusual features of the translational apparatus and their relevance to human mitochondrial diseases

21 January 2018

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Evidence for an active role of IF3mt in the initiation of translation in mammalian mitochondria

21 January 2018

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A single mammalian mitochondrial translation initiation factor functionally replaces two bacterial factors

21 January 2018

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Crystal structure of the bovine mitochondrial elongation factor Tu.Ts complex

21 January 2018

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Aminoacyl-tRNA surveillance by EF-Tu in mammalian mitochondria.

21 January 2018

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EF-G2mt is an exclusive recycling factor in mammalian mitochondrial protein synthesis

21 January 2018

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mtRF1a is a human mitochondrial translation release factor decoding the major termination codons UAA and UAG

21 January 2018

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A functional peptidyl-tRNA hydrolase, ICT1, has been recruited into the human mitochondrial ribosome

21 January 2018

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Mutations in C12orf65 in patients with encephalomyopathy and a mitochondrial translation defect

21 January 2018

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The human mitochondrial ribosome recycling factor is essential for cell viability

21 January 2018

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hNOA1 interacts with complex I and DAP3 and regulates mitochondrial respiration and apoptosis

21 January 2018

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NOA1 is an essential GTPase required for mitochondrial protein synthesis

21 January 2018

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ERAL1 is associated with mitochondrial ribosome and elimination of ERAL1 leads to mitochondrial dysfunction and growth retardation

21 January 2018

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Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

21 January 2018

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MTERF4 regulates translation by targeting the methyltransferase NSUN4 to the mammalian mitochondrial ribosome

21 January 2018

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C7orf30 is necessary for biogenesis of the large subunit of the mitochondrial ribosome

21 January 2018

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C7orf30 specifically associates with the large subunit of the mitochondrial ribosome and is involved in translation

21 January 2018

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Construction of Parallel Analysis of RNA Ends (PARE) libraries for the study of cleaved miRNA targets and the RNA degradome

21 January 2018

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RNA sequencing: advances, challenges and opportunities

21 January 2018

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Short non-coding RNA fragments accumulating in chloroplasts: footprints of RNA binding proteins?

21 January 2018

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Protein-mediated protection as the predominant mechanism for defining processed mRNA termini in land plant chloroplasts

21 January 2018

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Meta-analysis of small RNA-sequencing errors reveals ubiquitous post-transcriptional RNA modifications.

21 January 2018

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Traces of post-transcriptional RNA modifications in deep sequencing data

21 January 2018

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Pentatricopeptide repeat proteins: a socket set for organelle gene expression.

21 January 2018

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Genome-wide analysis of Arabidopsis pentatricopeptide repeat proteins reveals their essential role in organelle biogenesis

21 January 2018

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Genome-wide analysis of RNA-protein interactions in plants

21 January 2018

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Studying the structure and processing of chloroplast transcripts

21 January 2018

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Mechanism of RNA stabilization and translational activation by a pentatricopeptide repeat protein

21 January 2018

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In vitro RNA-binding assay for studying trans-factors for RNA editing in chloroplasts.

21 January 2018

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Selection patterns on restorer-like genes reveal a conflict between nuclear and mitochondrial genomes throughout angiosperm evolution.

21 January 2018

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Pentatricopeptide repeat (PPR) proteins as sequence-specificity factors in post-transcriptional processes in organelles

21 January 2018

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Sequence-specific binding of a chloroplast pentatricopeptide repeat protein to its native group II intron ligand.

21 January 2018

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Modular recognition of nucleic acids by PUF, TALE and PPR proteins

21 January 2018

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Revisiting the yeast PPR proteins--application of an Iterative Hidden Markov Model algorithm reveals new members of the rapidly evolving family

21 January 2018

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A genome wide study in fission yeast reveals nine PPR proteins that regulate mitochondrial gene expression

21 January 2018

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Pentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translation

21 January 2018

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The evolution of RNA editing and pentatricopeptide repeat genes.

21 January 2018

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RNA editing in plant organelles: machinery, physiological function and evolution

21 January 2018

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Pentatricopeptide repeat proteins stimulate mRNA adenylation/uridylation to activate mitochondrial translation in trypanosomes

21 January 2018

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Identification of pentatricopeptide repeat proteins in Trypanosoma brucei

21 January 2018

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DMR1 (CCM1/YGR150C) of Saccharomyces cerevisiae encodes an RNA-binding protein from the pentatricopeptide repeat family required for the maintenance of the mitochondrial 15S ribosomal RNA.

21 January 2018

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The pentatricopeptide repeats present in Pet309 are necessary for translation but not for stability of the mitochondrial COX1 mRNA in yeast.

21 January 2018

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Human Mitochondrial mRNAs Are Stabilized with Polyadenylation Regulated by Mitochondria-specific Poly(A) Polymerase and Polynucleotide Phosphorylase

21 January 2018

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