Structural and Biophysical Properties of the Pathogenic SOD1 Variant H46R/H48Q † (Q27653849)

2

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Xiaohang Cao

3

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Stephen P Holloway

4

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David R Borchelt

5

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Mark C Carroll

6

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Jody B Proescher

7

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Valeria C Culotta

8

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P John Hart

Structures of the G85R variant of SOD1 in familial amyotrophic lateral sclerosis

9

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language of work or name

English

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publication date

21 April 2009

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published in

Biochemistry

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volume

48

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issue

15

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page(s)

3436-47

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cites work

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Heterodimer formation between superoxide dismutase and its copper chaperone

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12 December 2020

Rats expressing human cytosolic copper-zinc superoxide dismutase transgenes with amyotrophic lateral sclerosis: associated mutations develop motor neuron disease

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12 December 2020

The unusually stable quaternary structure of human Cu,Zn-superoxide dismutase 1 is controlled by both metal occupancy and disulfide status

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12 December 2020

Somatodendritic accumulation of misfolded SOD1-L126Z in motor neurons mediates degeneration: alphaB-crystallin modulates aggregation

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Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

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A characterization of copper/zinc superoxide dismutase mutants at position 124. Zinc-deficient proteins

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12 December 2020

Processing of X-ray diffraction data collected in oscillation mode

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12 December 2020

Decreased zinc affinity of amyotrophic lateral sclerosis-associated superoxide dismutase mutants leads to enhanced catalysis of tyrosine nitration by peroxynitrite

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12 December 2020