Heptahelical protein PQLC2 is a lysosomal cationic amino acid exporter underlying the action of cysteamine in cystinosis therapy (Q27940141)

GOA release 2020-03-11

Ypq2p YDR352W

1 reference

Cationic amino acid transporter YOL092W

GOA release 2020-03-11

1 reference

Correction for Jézégou et al., Heptahelical protein PQLC2 is a lysosomal cationic amino acid exporter underlying the action of cysteamine in cystinosis therapy

GOA release 2020-03-11

corrigendum / erratum

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author

Sylvie Kieffer-Jaquinod

4

object named as

Sylvie Kieffer-Jaquinod

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author name string

Adrien Jézégou

1

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Elisa Llinares

2

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Christine Anne

3

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Sylvie Kieffer-Jaquinod

4

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Seana O'Regan

5

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Joëlle Aupetit

6

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Allel Chabli

7

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Corinne Sagné

8

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Cécile Debacker

9

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Bernadette Chadefaux-Vekemans

10

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Agnès Journet

11

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Bruno André

12

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Bruno Gasnier

Proceedings of the National Academy of Sciences of the United States of America

13

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language of work or name

English

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publication date

11 December 2012

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published in

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1 December 2016

109

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issue

50

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page(s)

E3434-43

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cites work

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29 September 2017

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Pantethine and cystamine deplete cystine from cystinotic fibroblasts via efflux of cysteamine-cysteine mixed disulfide

29 September 2017

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Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo

29 September 2017

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29 September 2017

1 reference

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ClC-7 is a slowly voltage-gated 2Cl(-)/1H(+)-exchanger and requires Ostm1 for transport activity

29 September 2017

1 reference

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2 June 2018

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Accumulation of amino acids within intracellular lysosomes of rat polymorphonuclear leukocytes incubated with amino acid methyl esters. Evidence for the internal acidification of azurophilic granules

2 June 2018

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Detection and characterization of carrier-mediated cationic amino acid transport in lysosomes of normal and cystinotic human fibroblasts. Role in therapeutic cystine removal?

2 June 2018

1 reference

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YTPdb: a wiki database of yeast membrane transporters

2 June 2018

1 reference

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Deletion of btn1, an orthologue of CLN3, increases glycolysis and perturbs amino acid metabolism in the fission yeast model of Batten disease

27 November 2018

1 reference

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The Yeast Vacuolar Membrane Proteome

27 November 2018

1 reference

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The Cl-/H+ antiporter ClC-7 is the primary chloride permeation pathway in lysosomes.

27 November 2018

1 reference

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27 November 2018

1 reference

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27 November 2018

1 reference

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27 November 2018

1 reference

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Modulation of the intracellular cystine content of cystinotic fibroblasts by extracellular albumin

27 November 2018

1 reference

12 December 2020

A cis-dominant regulatory mutation linked to the argB-argC gene cluster in Saccharomyces cerevisiae

1 reference

12 December 2020

Important differences in cationic amino acid transport by lysosomal system c and system y+ of the human fibroblast

1 reference

12 December 2020

Lys80p of Saccharomyces cerevisiae, previously proposed as a specific repressor of LYS genes, is a pleiotropic regulatory factor identical to Mks1p

1 reference

12 December 2020

Measurement of cystine in granulocytes using liquid chromatography-tandem mass spectrometry

1 reference

12 December 2020

Nephropathic cystinosis in adults: natural history and effects of oral cysteamine therapy

1 reference

12 December 2020

Purification and proteomic analysis of chloroplasts and their sub-organellar compartments

1 reference

12 December 2020

Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults

1 reference

12 December 2020

Sucrose Efflux Mediated by SWEET Proteins as a Key Step for Phloem Transport

1 reference

12 December 2020

Nonionic detergent phase extraction for the proteomic analysis of heart membrane proteins using label-free LC-MS

1 reference

12 December 2020

Isolation of a novel gene from Schizosaccharomyces pombe: stm1+ encoding a seven-transmembrane loop protein that may couple with the heterotrimeric Galpha 2 protein, Gpa2

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.1211198109

1 reference

release_2rcyk4b2tvf67eu3xlbfsimu3i

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Fatcat

https://api.fatcat.wiki/v0/release/2rcyk4b2tvf67eu3xlbfsimu3i

24 November 2022

mapped directly with Wikidata item

2151767

1 reference

1 reference

1 reference