Comprehensive functional characterization of murine infantile Batten disease including Parkinson-like behavior and dopaminergic markers. (Q30405389)

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20 February 2020

title

Comprehensive functional characterization of murine infantile Batten disease including Parkinson-like behavior and dopaminergic markers (English)

1 reference

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20 February 2020

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6

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20 February 2020

author name string

Joshua T Dearborn

1

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20 February 2020

Steven K Harmon

2

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20 February 2020

Stephen C Fowler

3

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20 February 2020

Karen L O'Malley

4

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20 February 2020

George T Taylor

5

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20 February 2020

David F Wozniak

7

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20 February 2020

language of work or name

English

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publication date

4 August 2015

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20 February 2020

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20 February 2020

volume

5

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20 February 2020

page(s)

12752

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Creative Commons Attribution 4.0 International

20 February 2020

copyright license

start time

4 August 2015

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April 2022 Public Data File from Crossref

copyright status

copyrighted

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cites work

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Evaluation of neurodegeneration in a mouse model of infantile batten disease by magnetic resonance imaging and magnetic resonance spectroscopy

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Molecular correlates of axonal and synaptic pathology in mouse models of Batten disease

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Force-plate quantification of progressive behavioral deficits in the R6/2 mouse model of Huntington's disease

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Cerebellar pathology and motor deficits in the palmitoyl protein thioesterase 1-deficient mouse

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20 June 2018

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A murine model of infantile neuronal ceroid lipofuscinosis-ultrastructural evaluation of storage in the central nervous system and viscera.

20 June 2018

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Impaired spatial learning and defective theta burst induced LTP in mice lacking fibroblast growth factor 14

20 June 2018

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Successive neuron loss in the thalamus and cortex in a mouse model of infantile neuronal ceroid lipofuscinosis

20 June 2018

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Gait dynamics in mouse models of Parkinson's disease and Huntington's disease

20 June 2018

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Progress towards understanding the neurobiology of Batten disease or neuronal ceroid lipofuscinosis

20 June 2018

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Disruption of PPT1 or PPT2 causes neuronal ceroid lipofuscinosis in knockout mice

20 June 2018

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A force-plate actometer for quantitating rodent behaviors: illustrative data on locomotion, rotation, spatial patterning, stereotypies, and tremor

20 June 2018

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Lipid thioesters derived from acylated proteins accumulate in infantile neuronal ceroid lipofuscinosis: correction of the defect in lymphoblasts by recombinant palmitoyl-protein thioesterase

20 June 2018

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Purification and properties of a palmitoyl-protein thioesterase that cleaves palmitate from H-Ras

20 June 2018

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20 June 2018

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Infantile type of so-called neuronal ceroid-lipofuscinosis

20 June 2018

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CNS-directed AAV2-mediated gene therapy ameliorates functional deficits in a murine model of infantile neuronal ceroid lipofuscinosis.

20 June 2018

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21 January 2018

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21 January 2018

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A zebrafish model of CLN2 disease is deficient in tripeptidyl peptidase 1 and displays progressive neurodegeneration accompanied by a reduction in proliferation.

21 January 2018

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21 January 2018

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21 January 2018

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Apoptotic neurodegeneration induced by ethanol in neonatal mice is associated with profound learning/memory deficits in juveniles followed by progressive functional recovery in adults

21 January 2018

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PubMed

https://pubmed.ncbi.nlm.nih.gov/26238334

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12 December 2020

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1 reference

https://pubmed.ncbi.nlm.nih.gov/26238334

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12 December 2020

based on heuristic

Identifiers

DOI

10.1038/SREP12752

1 reference

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Dimensions Publication ID

20 February 2020

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20 February 2020

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