Low dystrophin levels increase survival and improve muscle pathology and function in dystrophin/utrophin double-knockout mice (Q30539986)

16 August 2017

Low dystrophin levels increase survival and improve muscle pathology and function in dystrophin/utrophin double-knockout mice (English)

1 reference

16 August 2017

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8

Gert-Jan B van Ommen

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Louise van der Weerd

object named as

Louise van der Weerd

6

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Annemieke Aartsma-Rus

object named as

Annemieke M Aartsma-Rus

9

0 references

Peter A.C. 't Hoen

7

object named as

Peter A C 't Hoen

1 reference

16 August 2017

Maaike van Putten

1

1 reference

16 August 2017

Margriet Hulsker

2

1 reference

16 August 2017

Courtney Young

3

1 reference

16 August 2017

Vishna D Nadarajah

4

1 reference

16 August 2017

Hans Heemskerk

5

1 reference

16 August 2017

language of work or name

English

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publication date

4 March 2013

1 reference

16 August 2017

1 reference

16 August 2017

27

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16 August 2017

6

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16 August 2017

2484-2495

1 reference

describes a project that uses

16 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3659351/fullTextXML

inferred from PubMed Central ID database lookup

cites work

Rescue of severely affected dystrophin/utrophin-deficient mice through scAAV-U7snRNA-mediated exon skipping

1 reference

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The effects of low levels of dystrophin on mouse muscle function and pathology

20 June 2018

1 reference

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Phase 1 gene therapy for Duchenne muscular dystrophy using a translational optimized AAV vector

20 June 2018

1 reference

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Exon skipping and dystrophin restoration in patients with Duchenne muscular dystrophy after systemic phosphorodiamidate morpholino oligomer treatment: an open-label, phase 2, dose-escalation study

20 June 2018

1 reference

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Serum matrix metalloproteinase-9 (MMP-9) as a biomarker for monitoring disease progression in Duchenne muscular dystrophy (DMD).

20 June 2018

1 reference

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Systemic administration of PRO051 in Duchenne's muscular dystrophy

20 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3659351

Marginal level dystrophin expression improves clinical outcome in a strain of dystrophin/utrophin double knockout mice

20 June 2018

1 reference

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Prevention of dystrophic pathology in severely affected dystrophin/utrophin-deficient mice by morpholino-oligomer-mediated exon-skipping

20 June 2018

1 reference

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Dystrophin and mutations: one gene, several proteins, multiple phenotypes

20 June 2018

1 reference

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Assumption-free analysis of quantitative real-time polymerase chain reaction (PCR) data

20 June 2018

1 reference

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Quantification in cardiac MRI.

20 June 2018

1 reference

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Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy

20 June 2018

1 reference

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Dystrophin: the protein product of the Duchenne muscular dystrophy locus

20 June 2018

1 reference

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20 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3659351

Comparison of skeletal muscle pathology and motor function of dystrophin and utrophin deficient mouse strains

20 June 2018

1 reference

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Gentamicin-induced readthrough of stop codons in Duchenne muscular dystrophy

26 November 2018

1 reference

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A 3 months mild functional test regime does not affect disease parameters in young mdx mice.

26 November 2018

1 reference

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Serum levels of vascular endothelial growth factor elevated in patients with muscular dystrophy

26 November 2018

1 reference

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Disability and survival in Duchenne muscular dystrophy

26 November 2018

1 reference

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Dystrophin levels as low as 30% are sufficient to avoid muscular dystrophy in the human

26 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3659351

Dystrophin expression in muscles of duchenne muscular dystrophy patients after high-density injections of normal myogenic cells.

26 November 2018

1 reference

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Primary non-random X inactivation associated with disruption of Xist promoter regulation.

26 November 2018

1 reference

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Dystrophin and utrophin do not play crucial roles in nonmuscle tissues in mice

26 November 2018

1 reference

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Improved adenoviral vectors for gene therapy of Duchenne muscular dystrophy

26 November 2018

1 reference

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Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice

26 November 2018

1 reference

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Expression of human full-length and minidystrophin in transgenic mdx mice: implications for gene therapy of Duchenne muscular dystrophy

26 November 2018

1 reference

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Generation and Characterization of Transgenic Mice with the Full-length HumanDMDGene

26 November 2018

1 reference

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The frequency of revertants in mdx mouse genetic models for Duchenne muscular dystrophy

26 November 2018

1 reference

12 December 2020

Skeletal and cardiac myopathies in mice lacking utrophin and dystrophin: a model for Duchenne muscular dystrophy

1 reference

12 December 2020

The molecular basis of muscular dystrophy in the mdx mouse: a point mutation

1 reference

12 December 2020

The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy

1 reference

12 December 2020

Transduction of Full-length Dystrophin to Multiple Skeletal Muscles Improves Motor Performance and Life Span in Utrophin/Dystrophin Double Knockout Mice

1 reference

12 December 2020

Diaphragm rescue alone prevents heart dysfunction in dystrophic mice

1 reference

12 December 2020

Assessment of cardiac function in three mouse dystrophinopathies by magnetic resonance imaging

1 reference

12 December 2020

Identifiers

DOI

10.1096/FJ.12-224170

1 reference

release_4he6alkymvb6nflity2xvbcjj4

16 August 2017

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/4he6alkymvb6nflity2xvbcjj4

24 November 2022

mapped directly with Wikidata item

1 reference

16 August 2017

PubMed publication ID

23460734

1 reference