Recovery from liver disease in a Niemann-Pick type C mouse model (Q33993252)

30 July 2017

Recovery from liver disease in a Niemann-Pick type C mouse model (English)

1 reference

30 July 2017

Naomi L Sayre

1

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30 July 2017

Victoria M Rimkunas

2

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30 July 2017

Mark J Graham

3

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30 July 2017

Rosanne M Crooke

4

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30 July 2017

Laura Liscum

5

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30 July 2017

24 April 2010

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Journal of Lipid Research

30 July 2017

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30 July 2017

51

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30 July 2017

8

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30 July 2017

2372-2383

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Hepatic stellate cell: a star cell in the liver

30 July 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Linear clinical progression, independent of age of onset, in Niemann-Pick disease, type C

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Enhanced free cholesterol, SREBP-2 and StAR expression in human NASH.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Reversal of defective lysosomal transport in NPC disease ameliorates liver dysfunction and neurodegeneration in the npc1-/- mouse

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Liver X receptor modulators: effects on lipid metabolism and potential use in the treatment of atherosclerosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

TNF-{alpha} plays a role in hepatocyte apoptosis in Niemann-Pick type C liver disease

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Inflammatory stress exacerbates lipid accumulation in hepatic cells and fatty livers of apolipoprotein E knockout mice

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

In vivo antisense oligonucleotide reduction of NPC1 expression as a novel mouse model for Niemann Pick type C- associated liver disease.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Diacylglycerol acyltranferase 1 anti-sense oligonucleotides reduce hepatic fibrosis in mice with nonalcoholic steatohepatitis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

An apolipoprotein B antisense oligonucleotide lowers LDL cholesterol in hyperlipidemic mice without causing hepatic steatosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

A simple method for the isolation and purification of total lipides from animal tissues

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Pharmacokinetic properties of 2'-O-(2-methoxyethyl)-modified oligonucleotide analogs in rats

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Characterization of Chinese hamster ovary cells that are resistant to 3-beta-[2-(diethylamino)ethoxy]androst-5-en-17-one inhibition of low density lipoprotein-derived cholesterol metabolism

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

Liver failure and the sea-blue histiocyte/adult Niemann-Pick disease. Case report and review of the literature

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2903820

The National Niemann-Pick C1 disease database: report of clinical features and health problems.

5 July 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Niemann-pick disease type C in neonatal cholestasis at a North American Center

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Niemann-Pick disease type C: diagnosis and outcome in children, with particular reference to liver disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Cholesterol accumulation and liver cell death in mice with Niemann-Pick type C disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Delineation of molecular changes in intrahepatic cholesterol metabolism resulting from diminished cholesterol absorption

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Liver X receptor activation enhances cholesterol loss from the brain, decreases neuroinflammation, and increases survival of the NPC1 mouse.

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Sphingomyelinosis, a new mutation in the mouse: a model of Niemann-Pick disease in humans.

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M007211

Intracellular cholesterol transport

21 January 2018

1 reference

12 December 2020

Progressive neonatal liver failure due to type C Niemann-Pick disease

1 reference

12 December 2020

Fetal Niemann-Pick disease type C: ultrastructural and lipid findings in liver and spleen

1 reference

12 December 2020

Severe failure to thrive and liver dysfunction as the main manifestations of a new variant of Niemann-Pick disease

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12 December 2020

Lysosomal unesterified cholesterol content correlates with liver cell death in murine Niemann-Pick type C disease

1 reference

12 December 2020

Characterization of liver disease and lipid metabolism in the Niemann-Pick C1 mouse

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12 December 2020

Identifiers

DOI

10.1194/JLR.M007211

1 reference

30 July 2017

1 reference

30 July 2017

1 reference