Transgenic studies of the influence of the PrP structure on TSE diseases. (Q34304996)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11447693%20AND%20SRC:MED&resulttype=core&format=json

9 November 2019

review article

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title

Transgenic studies of the influence of the PrP structure on TSE diseases (English)

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9 November 2019

1

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9 November 2019

author name string

J Collinge

series ordinal

2

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9 November 2019

publication date

1 January 2001

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Advances in Protein Chemistry

9 November 2019

published in

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11447693%20AND%20SRC:MED&resulttype=core&format=json

9 November 2019

volume

57

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9 November 2019

page(s)

273-311

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Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene

9 November 2019

cites work

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7 January 2021

PrP-expressing tissue required for transfer of scrapie infectivity from spleen to brain

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7 January 2021

Normal host prion protein necessary for scrapie-induced neurotoxicity

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7 January 2021

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B lymphocytes and neuroinvasion

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7 January 2021

Prion Protein-Deficient Cells Show Altered Response to Oxidative Stress Due to Decreased SOD-1 Activity

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7 January 2021

Scrapie strain variation and mutation

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7 January 2021

The disease characteristics of different strains of scrapie in Sinc congenic mouse lines: implications for the nature of the agent and host control of pathogenesis

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7 January 2021

Transmission of bovine spongiform encephalopathy and scrapie to mice: strain variation and the species barrier

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7 January 2021

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

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7 January 2021

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

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7 January 2021

Mice devoid of PrP are resistant to scrapie

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7 January 2021

High prion and PrPSc levels but delayed onset of disease in scrapie-inoculated mice heterozygous for a disrupted PrP gene

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7 January 2021

Linkage of prion protein and scrapie incubation time genes

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7 January 2021

Genetics and polymorphism of the mouse prion gene complex: control of scrapie incubation time

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7 January 2021

The nature of the scrapie agent. Biological characteristics of scrapie in different scrapie strain-host combinations

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7 January 2021

Secondary structure analysis of the scrapie-associated protein PrP 27-30 in water by infrared spectroscopy

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7 January 2021

Neurological illness in transgenic mice expressing a prion protein with an insertional mutation.

1 reference

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7 January 2021

Hippocampal slices from prion protein null mice: disrupted Ca(2+)-activated K+ currents.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Human prion diseases and bovine spongiform encephalopathy (BSE).

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Variant Creutzfeldt-Jakob disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Diagnosis of Gerstmann-Sträussler syndrome in familial dementia with prion protein gene analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Prion protein is necessary for normal synaptic function

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Unaltered susceptibility to BSE in transgenic mice expressing human prion protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Transmission of fatal familial insomnia to laboratory animals

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Biochemical typing of scrapie strains

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Selective neuronal targeting in prion disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Identification of a gene which controls the incubation period of some strains of scrapie agent in mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Dementia associated with a 216 base pair insertion in the prion protein gene. Clinical and neuropathological features

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Diversity of oligosaccharide structures linked to asparagines of the scrapie prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Prion protein (PrP) with amino-proximal deletions restoring susceptibility of PrP knockout mice to scrapie.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A neurotoxic prion protein fragment induces rat astroglial proliferation and hypertrophy.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Creutzfeldt-Jacob disease associated with the PRNP codon 200Lys mutation: an analysis of 45 families

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Biogenesis and transmembrane orientation of the cellular isoform of the scrapie prion protein [published errratum appears in Mol Cell Biol 1987 May;7(5):2035]

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Evidence for a secretory form of the cellular prion protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A transmembrane form of the prion protein in neurodegenerative disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Patch-clamp analysis of synaptic transmission to cerebellar purkinje cells of prion protein knockout mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

The same prion strain causes vCJD and BSE

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Copper binding to the N-terminal tandem repeat regions of mammalian and avian prion protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Spontaneous neurodegeneration in transgenic mice with mutant prion protein

1 reference

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7 January 2021

Association between natural scrapie and PrP genotype in a flock of Suffolk sheep in Scotland

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Scrapie infection of transgenic mice leads to network and intrinsic dysfunction of cortical and hippocampal neurones

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Neurotoxicity of prion peptide 106-126 not confirmed

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Molecular cloning of a human prion protein cDNA

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Transmission of the BSE agent to mice in the absence of detectable abnormal prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Three hamster species with different scrapie incubation times and neuropathological features encode distinct prion proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A protease-resistant protein is a structural component of the scrapie prion

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A single amino acid alteration (101L) introduced into murine PrP dramatically alters incubation time of transmissible spongiform encephalopathy

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Quantifying the kinetic parameters of prion replication.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Fatal familial insomnia: a second kindred with mutation of prion protein gene at codon 178

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Fatal familial insomnia, a prion disease with a mutation at codon 178 of the prion protein gene

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Mice with gene targetted prion protein alterations show that Prnp, Sinc and Prni are congruent

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Developmental expression of the prion protein gene in glial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Heritable disorder resembling neuronal storage disease in mice expressing prion protein with deletion of an α-helix

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Modulation of protein structure and function by asparagine-linked glycosylation

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A dementing illness associated with a novel insertion in the prion protein gene

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Homozygous prion protein genotype predisposes to sporadic Creutzfeldt–Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Regional distribution of protease-resistant prion protein in fatal familial insomnia

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Molecular biology of prion diseases

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Analysis of linkage between scrapie incubation period and the prion protein gene in mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Neuron-specific expression of a hamster prion protein minigene in transgenic mice induces susceptibility to hamster scrapie agent

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

NMR structure of the mouse prion protein domain PrP(121-231)

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

NMR characterization of the full-length recombinant murine prion protein, mPrP(23-231).

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

No propagation of prions in mice devoid of PrP.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Propagation of prions with artificial properties in transgenic mice expressing chimeric PrP genes.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Prion protein gene variation among primates

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Expression of amino-terminally truncated PrP in the mouse leading to ataxia and specific cerebellar lesions

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Biochemical typing of scrapie strains

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Prion protein of 106 residues creates an artifical transmission barrier for prion replication in transgenic mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Experimental transmission of Creutzfeldt-Jakob disease and related diseases to rodents

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Altered circadian activity rhythms and sleep in mice devoid of prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Doxycycline control of prion protein transgene expression modulates prion disease in mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Distinct prion proteins in short and long scrapie incubation period mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Paradoxical shortening of scrapie incubation times by expression of prion protein transgenes derived from long incubation period mice

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

[URE3] as an altered URE2 protein: evidence for a prion analog in Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

A new variant of Creutzfeldt-Jakob disease in the UK.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Rescue of neurophysiological phenotype seen in PrP null mice by transgene encoding human prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Non-hydrophobic extracytoplasmic determinant of stop transfer in the prion protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

Insertion in prion protein gene in familial Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0065-3233%2801%2957025-4

7 January 2021

10.1016/S0065-3233(01)57025-4

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11447693%20AND%20SRC:MED&resulttype=core&format=json

9 November 2019

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