Heat shock protein-based therapy as a potential candidate for treating the sphingolipidoses. (Q34539778)

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22 March 2020

title

Heat shock protein-based therapy as a potential candidate for treating the sphingolipidoses (English)

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22 March 2020

5

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22 March 2020

Ian Martin Williams

15

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22 March 2020

Christoph Arenz

17

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22 March 2020

Marja Jäättelä

19

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22 March 2020

Frances Platt

20

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22 March 2020

author name string

Thomas Kirkegaard

1

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22 March 2020

James Gray

2

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22 March 2020

David A Priestman

3

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22 March 2020

Kerri-Lee Wallom

4

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22 March 2020

Ole Dines Olsen

6

1 reference

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22 March 2020

Alexander Klein

7

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22 March 2020

Svetlana Drndarski

8

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22 March 2020

Nikolaj H T Petersen

9

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22 March 2020

Linda Ingemann

10

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22 March 2020

David A Smith

11

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22 March 2020

Lauren Morris

12

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22 March 2020

Claus Bornæs

13

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22 March 2020

Signe Humle Jørgensen

14

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22 March 2020

Anders Hinsby

16

1 reference

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22 March 2020

David Begley

18

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22 March 2020

language of work or name

English

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publication date

1 September 2016

1 reference

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Science Translational Medicine

22 March 2020

published in

1 reference

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22 March 2020

volume

8

1 reference

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22 March 2020

issue

355

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22 March 2020

page(s)

355ra118

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describes a project that uses

22 March 2020

ImageJ

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC6821533/fullTextXML

inferred from PubMed Central ID database lookup

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Niemann-Pick disease type C

21 January 2018

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Secondary lipid accumulation in lysosomal disease

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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The role of glycosphingolipid metabolism in the developing brain

21 January 2018

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GM1-ganglioside accumulation at the mitochondria-associated ER membranes links ER stress to Ca(2+)-dependent mitochondrial apoptosis

21 January 2018

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The role of heat shock proteins in Amyotrophic Lateral Sclerosis: The therapeutic potential of Arimoclomol

21 January 2018

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Treatment for familial amyotrophic lateral sclerosis/motor neuron disease

21 January 2018

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The proteasome inhibitor bortezomib reduced cholesterol accumulation in fibroblasts from Niemann-Pick type C patients carrying missense mutations.

21 January 2018

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The heat shock response: systems biology of proteotoxic stress in aging and disease

21 January 2018

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Co-induction of the heat shock response ameliorates disease progression in a mouse model of human spinal and bulbar muscular atrophy: implications for therapy

21 January 2018

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Histone deacetylase inhibitors increase glucocerebrosidase activity in Gaucher disease by modulation of molecular chaperones

21 January 2018

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Proteotoxic stress and inducible chaperone networks in neurodegenerative disease and aging

21 January 2018

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Heat shock proteins as cellular lifeguards

21 January 2018

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Chronic cyclodextrin treatment of murine Niemann-Pick C disease ameliorates neuronal cholesterol and glycosphingolipid storage and disease progression

21 January 2018

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Miglustat improves purkinje cell survival and alters microglial phenotype in feline Niemann-Pick disease type C.

21 January 2018

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Iminosugar-based inhibitors of glucosylceramide synthase prolong survival but paradoxically increase brain glucosylceramide levels in Niemann-Pick C mice.

21 January 2018

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Histone deacetylase inhibitor treatment dramatically reduces cholesterol accumulation in Niemann-Pick type C1 mutant human fibroblasts

21 January 2018

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Niemann-Pick type C1 I1061T mutant encodes a functional protein that is selected for endoplasmic reticulum-associated degradation due to protein misfolding

21 January 2018

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21 January 2018

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A murine Niemann-Pick C1 I1061T knock-in model recapitulates the pathological features of the most prevalent human disease allele

21 January 2018

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Exogenous delivery of heat shock protein 70 increases lifespan in a mouse model of amyotrophic lateral sclerosis.

21 January 2018

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Transgenic mice expressing the human heat shock protein 70 have improved post-ischemic myocardial recovery

21 January 2018

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Overexpression of the rat inducible 70-kD heat stress protein in a transgenic mouse increases the resistance of the heart to ischemic injury

21 January 2018

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Targeting protein homeostasis in sporadic inclusion body myositis

21 January 2018

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Lipids on trial: the search for the offending metabolite in Niemann-Pick type C disease

21 January 2018

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Sphingolipid lysosomal storage disorders

21 January 2018

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Protein quality control in the cytosol and the endoplasmic reticulum: brothers in arms.

21 January 2018

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Upregulation of heat shock proteins rescues motoneurones from axotomy-induced cell death in neonatal rats

21 January 2018

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Late stage treatment with arimoclomol delays disease progression and prevents protein aggregation in the SOD1 mouse model of ALS

21 January 2018

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Microdialysis evaluation of clozapine and N-desmethylclozapine pharmacokinetics in rat brain.

21 January 2018

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Murine model of Niemann-Pick C disease: mutation in a cholesterol homeostasis gene.

21 January 2018

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Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling

21 January 2018

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https://api.crossref.org/works/10.1126%2FSCITRANSLMED.AAD9823

Beneficial effects of substrate reduction therapy in a mouse model of GM1 gangliosidosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.AAD9823

Activation of the heat shock response in a primary cellular model of motoneuron neurodegeneration-evidence for neuroprotective and neurotoxic effects

21 January 2018

1 reference

12 December 2020

Chaperoning signaling pathways: molecular chaperones as stress-sensing 'heat shock' proteins.

1 reference

12 December 2020

Pharmacokinetic and tissue distribution mechanism of mouse recombinant heat shock protein 70 in mice

1 reference

12 December 2020

Saposin A Mobilizes Lipids from Low Cholesterol and High Bis(monoacylglycerol)phosphate-containing Membranes

1 reference

12 December 2020

A simple method for the isolation and purification of total lipides from animal tissues

1 reference

12 December 2020

A genetic storage disorder in BALB/C mice with a metabolic block in esterification of exogenous cholesterol

1 reference

12 December 2020

Studies on human liver alpha-galactosidases. II. Purification and enzymatic properties of alpha-galactosidase B (alpha-N-acetylgalactosaminidase)

1 reference

12 December 2020

Effect of BRX-220 against peripheral neuropathy and insulin resistance in diabetic rat models

1 reference

12 December 2020

GM1-ganglioside-mediated activation of the unfolded protein response causes neuronal death in a neurodegenerative gangliosidosis

1 reference

12 December 2020

10.1126/SCITRANSLMED.AAD9823

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27605553%20AND%20SRC:MED&resulttype=core&format=json

release_27p5732qdvga7iyoewbwkt3gke

22 March 2020

Fatcat ID

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/27p5732qdvga7iyoewbwkt3gke

24 November 2022

mapped directly with Wikidata item

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27605553%20AND%20SRC:MED&resulttype=core&format=json

22 March 2020

1 reference