Lysosomal membrane permeability stimulates protein aggregate formation in neurons of a lysosomal disease (Q36955845)

17 August 2017

Lysosomal membrane permeability stimulates protein aggregate formation in neurons of a lysosomal disease (English)

1 reference

17 August 2017

Matthew C Micsenyi

1

1 reference

17 August 2017

Jakub Sikora

2

1 reference

17 August 2017

Gloria Stephney

3

1 reference

17 August 2017

Kostantin Dobrenis

4

1 reference

17 August 2017

Steven U Walkley

5

1 reference

17 August 2017

language of work or name

English

0 references

publication date

1 June 2013

1 reference

17 August 2017

Journal of Neuroscience

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17 August 2017

33

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17 August 2017

26

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17 August 2017

10815-10827

1 reference

describes a project that uses

17 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3693058/fullTextXML

inferred from PubMed Central ID database lookup

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Lysosomes in apoptosis

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Autophagy-mediated clearance of aggresomes is not a universal phenomenon

29 September 2017

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A block of autophagy in lysosomal storage disorders

29 September 2017

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29 September 2017

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p62/SQSTM1 forms protein aggregates degraded by autophagy and has a protective effect on huntingtin-induced cell death

29 September 2017

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29 September 2017

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29 September 2017

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A mouse model of classical late-infantile neuronal ceroid lipofuscinosis based on targeted disruption of the CLN2 gene results in a loss of tripeptidyl-peptidase I activity and progressive neurodegeneration

29 September 2017

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29 September 2017

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Treatment with arimoclomol, a coinducer of heat shock proteins, delays disease progression in ALS mice

29 September 2017

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29 September 2017

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29 September 2017

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29 September 2017

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29 September 2017

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A lysosomal proteinase, the late infantile neuronal ceroid lipofuscinosis gene (CLN2) product, is essential for degradation of a hydrophobic protein, the subunit c of ATP synthase.

29 September 2017

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Aggresomes: a cellular response to misfolded proteins

29 September 2017

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29 September 2017

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Mechanism of L-leucyl-L-leucine methyl ester-mediated killing of cytotoxic lymphocytes: dependence on a lysosomal thiol protease, dipeptidyl peptidase I, that is enriched in these cells

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Neuronal lysosomal enzyme replacement using fragment C of tetanus toxin

29 September 2017

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Increased activity and altered subcellular distribution of lysosomal enzymes determine neuronal vulnerability in Niemann-Pick type C1-deficient mice

29 September 2017

1 reference

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Follow-up study of subunit c of mitochondrial ATP synthase (SCMAS) in Batten disease and in unrelated lysosomal disorders.

27 June 2018

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A vesicular transport pathway shuttles cargo from mitochondria to lysosomes.

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Evidence of lysosomal membrane permeabilization in mucopolysaccharidosis type I: rupture of calcium and proton homeostasis.

4 September 2018

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4 September 2018

1 reference

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A novel procedure for pre-embedding double immunogold-silver labeling at the ultrastructural level.

4 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Mutation of the E6-AP ubiquitin ligase reduces nuclear inclusion frequency while accelerating polyglutamine-induced pathology in SCA1 mice.

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions.

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Incidence of neuronal perikaryal spheroids in neuronal ceroid lipofuscinoses (Batten disease).

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

NBR1 and p62 as cargo receptors for selective autophagy of ubiquitinated targets

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3693058

Monitoring activity and inhibition of 26S proteasomes with fluorogenic peptide substrates

20 October 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23804102

12 December 2020

inferred from PubMed ID database lookup

A histochemical and ultrastructural study of stored material in neuronal ceroid lipofuscinosis

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23804102

12 December 2020

inferred from PubMed ID database lookup

Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease)

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23804102

12 December 2020

inferred from PubMed ID database lookup

Identifiers

DOI

10.1523/JNEUROSCI.0987-13.2013

1 reference

17 August 2017

1 reference

17 August 2017

1 reference