Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease (Q34749046)

4 August 2017

title

Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease (English)

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4 August 2017

10

Lorenzo Galluzzi

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Guido Kroemer

18

Guido Kroemer

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Nathanael Larochette

Nathanael Larochette

9

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Hans Zischka

Hans Zischka

1

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Irene Esposito

15

Irene Esposito

1 reference

4 August 2017

4

Nora Jägemann

1 reference

4 August 2017

Josef Lichtmannegger

2

1 reference

4 August 2017

Sabine Schmitt

3

1 reference

4 August 2017

Sabine Schulz

5

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4 August 2017

Daniela Wartini

6

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4 August 2017

Luise Jennen

7

1 reference

4 August 2017

Christian Rust

8

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4 August 2017

Veronique Chajes

11

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4 August 2017

Nathan Bandow

12

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4 August 2017

Valérie S Gilles

13

1 reference

4 August 2017

Alan A DiSpirito

14

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4 August 2017

Martin Goettlicher

16

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4 August 2017

Karl H Summer

17

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4 August 2017

language of work or name

English

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publication date

1 April 2011

1 reference

Journal of Clinical Investigation

4 August 2017

published in

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4 August 2017

volume

121

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4 August 2017

issue

4

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4 August 2017

page(s)

1508-1518

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Mitochondrial membrane permeabilization in neuronal injury

4 August 2017

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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Glutathionylation of mitochondrial proteins

7 July 2018

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7 July 2018

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7 July 2018

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Penicillamine, a new oral therapy for Wilson's disease

7 July 2018

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Wilson's disease; new oral therapy

7 July 2018

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7 July 2018

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7 July 2018

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Undetectable intracellular free copper: the requirement of a copper chaperone for superoxide dismutase

7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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Liver copper storage and transport during development: implications for cytotoxicity

7 July 2018

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The Wilson disease gene is a copper transporting ATPase with homology to the Menkes disease gene

7 July 2018

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The Wilson disease gene is a putative copper transporting P-type ATPase similar to the Menkes gene

7 July 2018

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Oxidant injury to hepatic mitochondria in patients with Wilson's disease and Bedlington terriers with copper toxicosis

7 July 2018

1 reference

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The LEC rat has a deletion in the copper transporting ATPase gene homologous to the Wilson disease gene

7 July 2018

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Long-term storage of mitochondria to preserve energy-linked functions

7 July 2018

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7 July 2018

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7 July 2018

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Progressive lenticular degeneration: a familial nervous disease associated with cirrhosis of the liver, by S. A. Kinnier Wilson, (From the National Hospital, and the Laboratory of the National Hospital, Queen Square, London) Brain 1912: 34; 295-509.

7 July 2018

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Mitochondrial structure and function in the untreated Jackson toxic milk (tx-j) mouse, a model for Wilson disease

26 October 2018

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A new strain of rat for functional analysis of PINA.

26 October 2018

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Apoptosis and age-dependant induction of nuclear and mitochondrial etheno-DNA adducts in Long-Evans Cinnamon (LEC) rats: enhanced DNA damage by dietary curcumin upon copper accumulation

26 October 2018

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Methanobactin, a copper-acquisition compound from methane-oxidizing bacteria.

26 October 2018

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Yeast contain a non-proteinaceous pool of copper in the mitochondrial matrix

26 October 2018

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Oxidant injury to hepatic mitochondrial lipids in rats with dietary copper overload. Modification by vitamin E deficiency

26 October 2018

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12 December 2020

Quantitation of mitochondrial transmembrane potential in cells and in isolated mitochondria

1 reference

12 December 2020

Isolation of methanobactin from the spent media of methane-oxidizing bacteria

1 reference

12 December 2020

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12 December 2020

Electrophoretic analysis of the mitochondrial outer membrane rupture induced by permeability transition

1 reference

12 December 2020

Abnormal hepatic mitochondrial respiration and cytochrome C oxidase activity in rats with long-term copper overload

1 reference

12 December 2020

Mitochondrial and fatty changes in hepatocytes of patients with Wilson's disease

1 reference

12 December 2020

Fraternal concordance of types of abnormal hepatocellular mitochondria in Wilson's disease

1 reference

12 December 2020

1 reference

12 December 2020

Mechanism of production of hydroxyl radicals in the copper-catalyzed oxidation of dithiothreitol

1 reference

12 December 2020

Mechanism of copper-catalyzed autoxidation of cysteine

1 reference

12 December 2020

Mechanism of copper-catalyzed oxidation of glutathione

1 reference

12 December 2020

An array of mitochondrial alterations in the hepatocytes of Long-Evans Cinnamon rats

1 reference

12 December 2020

D-penicillamine prevents the development of hepatitis in Long-Evans Cinnamon rats with abnormal copper metabolism

1 reference

12 December 2020

Diagnosis and treatment of Wilson's disease

1 reference

12 December 2020

Oxidative-phosphorylation defects in liver of patients with Wilson's disease

1 reference

12 December 2020

Premature oxidative aging of hepatic mitochondrial DNA in Wilson's disease

1 reference

12 December 2020

Free copper ions in the cell?

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI45401

1 reference

4 August 2017

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4 August 2017

1 reference