Peroxisomal multifunctional protein-2 deficiency causes motor deficits and glial lesions in the adult central nervous system (Q35088180)

6 August 2017

title

Peroxisomal multifunctional protein-2 deficiency causes motor deficits and glial lesions in the adult central nervous system (English)

1 reference

6 August 2017

4

Paul Van Veldhoven

1 reference

6 August 2017

Steven Huyghe

1

1 reference

6 August 2017

Henning Schmalbruch

2

1 reference

6 August 2017

Leen Hulshagen

3

1 reference

6 August 2017

Myriam Baes

5

1 reference

6 August 2017

Dieter Hartmann

6

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6 August 2017

language of work or name

English

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publication date

1 April 2006

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The American Journal of Pathology

6 August 2017

published in

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6 August 2017

volume

168

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6 August 2017

issue

4

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6 August 2017

page(s)

1321-1334

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Absence of peroxisomes in mouse hepatocytes causes mitochondrial and ER abnormalities

6 August 2017

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8 July 2018

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8 July 2018

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8 July 2018

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Peroxisomal straight-chain Acyl-CoA oxidase and D-bifunctional protein are essential for the retroconversion step in docosahexaenoic acid synthesis

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Mutations in the gene encoding peroxisomal alpha-methylacyl-CoA racemase cause adult-onset sensory motor neuropathy

8 July 2018

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Docosahexaenoic acid deficit is not a major pathogenic factor in peroxisome-deficient mice

8 July 2018

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Presenilin-1 deficiency leads to loss of Cajal-Retzius neurons and cortical dysplasia similar to human type 2 lissencephaly

8 July 2018

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A novel peroxisomal enzyme, D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxyacyl-CoA dehydrogenase bifunctional protein: its expression in the developing human brain

8 July 2018

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8 July 2018

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Docosahexaenoic acid synthesis in human skin fibroblasts involves peroxisomal retroconversion of tetracosahexaenoic acid

8 July 2018

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Rhizomelic chondrodysplasia punctata: report of a case with review of the literature and correlation with other peroxisomal disorders

8 July 2018

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Brain glia release factors with opposing actions upon neuronal survival.

8 July 2018

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Reactive glia as rivals in regulating neuronal survival

8 July 2018

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The pathology of peroxisomal disorders with pathogenetic considerations.

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidation

8 July 2018

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Microperoxisomes in the central nervous system of the postnatal rat

8 July 2018

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Developmental changes of bile acid composition and conjugation in L- and D-bifunctional protein single and double knockout mice

8 July 2018

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Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of leukotrienes.

27 September 2018

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The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation.

27 September 2018

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Fluoro-Jade and silver methods: application to the neuropathology of scrapie, a transmissible spongiform encephalopathy

27 September 2018

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Immunocytochemical localization of acyl-CoA oxidase in the rat central nervous system

27 September 2018

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Docosahexaenoic acid synthesis from n-3 polyunsaturated fatty acids in differentiated rat brain astrocytes

27 September 2018

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Cerebellar atrophy in chronic rhizomelic chondrodysplasia punctata: a potential role for phytanic acid and calcium in the death of its Purkinje cells

27 September 2018

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Enzymatic quantitation of cholesterol esters in lipid extracts.

27 September 2018

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Immunocytochemical localization of catalase in the central nervous system of the rat.

27 September 2018

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Inactivation of the peroxisomal multifunctional protein-2 in mice impedes the degradation of not only 2-methyl-branched fatty acids and bile acid intermediates but also of very long chain fatty acids

27 September 2018

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12 December 2020

Immunocytochemical localization of D-amino acid oxidase in rat brain

1 reference

12 December 2020

Inorganic and organic phosphate measurements in the nanomolar range

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12 December 2020

Effect of harvesting methods, growth conditions and growth phase on diacylglycerol levels in cultured human adherent cells

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12 December 2020

Astrocytes, not neurons, produce docosahexaenoic acid (22:6 omega-3) and arachidonic acid (20:4 omega-6)

1 reference

12 December 2020

Lipase-based quantitation of triacylglycerols in cellular lipid extracts: requirement for presence of detergent and prior separation by thin-layer chromatography

1 reference

12 December 2020

10.2353/AJPATH.2006.041220

Identifiers

DOI

1 reference

6 August 2017

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6 August 2017

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