Astrocyte dysfunction triggers neurodegeneration in a lysosomal storage disorder (Q36212862)

12 August 2017

Astrocyte dysfunction triggers neurodegeneration in a lysosomal storage disorder (English)

1 reference

12 August 2017

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Carmine Settembre

3

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Andrea Ballabio

object named as

Andrea Ballabio

series ordinal

4

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author name string

Chiara Di Malta

series ordinal

1

1 reference

12 August 2017

John D Fryer

series ordinal

2

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12 August 2017

language of work or name

English

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publication date

23 July 2012

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Proceedings of the National Academy of Sciences of the United States of America

12 August 2017

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12 August 2017

109

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12 August 2017

35

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12 August 2017

E2334-42

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describes a project that uses

12 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3435187/fullTextXML

based on heuristic

inferred from PubMed Central ID database lookup

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The sorting and trafficking of lysosomal proteins

1 October 2017

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Loss of autophagy in the central nervous system causes neurodegeneration in mice

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Storage solutions: treating lysosomal disorders of the brain

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1 October 2017

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A mouse model of classical late-infantile neuronal ceroid lipofuscinosis based on targeted disruption of the CLN2 gene results in a loss of tripeptidyl-peptidase I activity and progressive neurodegeneration

1 October 2017

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1 October 2017

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1 October 2017

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1 October 2017

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1 October 2017

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1 October 2017

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1 October 2017

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p62 Is a common component of cytoplasmic inclusions in protein aggregation diseases

1 October 2017

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Sulfamidase deficiency in a family of Dachshunds: a canine model of mucopolysaccharidosis IIIA (Sanfilippo A).

29 June 2018

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A model of mucopolysaccharidosis IIIB (Sanfilippo syndrome type IIIB): N‐acetyl‐α‐D‐glucosaminidase deficiency in Schipperke dogs

21 January 2018

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Central nervous system inflammation is a hallmark of pathogenesis in mouse models of GM1 and GM2 gangliosidosis

21 January 2018

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Chromosomal mapping of the GFP-LC3 transgene in GFP-LC3 mice.

21 January 2018

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22 September 2018

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12 December 2020

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Identifiers

DOI

10.1073/PNAS.1209577109

1 reference

12 August 2017

0 references

1 reference

12 August 2017

1 reference