Tripeptidyl-peptidase I in health and disease (Q36559721)

14 August 2017

1 reference

title

Tripeptidyl-peptidase I in health and disease (English)

1 reference

14 August 2017

Adam A Golabek

1

1 reference

PubMed ID

16895480

14 August 2017

Elizabeth Kida

series ordinal

2

1 reference

14 August 2017

1 August 2006

1 reference

14 August 2017

1 reference

14 August 2017

387

1 reference

14 August 2017

1091-1099

1 reference

14 August 2017

8

1 reference

The substrate range of tripeptidyl-peptidase I.

14 August 2017

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Enzyme replacement for lysosomal diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Lysine 43 is trimethylated in subunit C from bovine mitochondrial ATP synthase and in storage bodies associated with batten disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Changes in brain weights during the span of human life: relation of brain weights to body heights and body weights

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Rat tripeptidyl peptidase I: molecular cloning, functional expression, tissue localization and enzymatic characterization

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Follow-up study of subunit c of mitochondrial ATP synthase (SCMAS) in Batten disease and in unrelated lysosomal disorders.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

A lysosomal proteinase, the late infantile neuronal ceroid lipofuscinosis gene (CLN2) product, is essential for degradation of a hydrophobic protein, the subunit c of ATP synthase.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Characterization of endopeptidase activity of tripeptidyl peptidase-I/CLN2 protein which is deficient in classical late infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Targeted delivery across the blood-brain barrier

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Biosynthesis, glycosylation, and enzymatic processing in vivo of human tripeptidyl-peptidase I.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Maturation of human tripeptidyl-peptidase I in vitro

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Glycosaminoglycans modulate activation, activity, and stability of tripeptidyl-peptidase I in vitro and in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

A general acid-base mechanism for the stabilization of a tetrahedral adduct in a serine-carboxyl peptidase: a computational study

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Safety of direct administration of AAV2(CU)hCLN2, a candidate treatment for the central nervous system manifestations of late infantile neuronal ceroid lipofuscinosis, to the brain of rats and nonhuman primates

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Viral-mediated delivery of the late-infantile neuronal ceroid lipofuscinosis gene, TPP-I to the mouse central nervous system

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Roles of N-linked glycans in the endoplasmic reticulum

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Matrix proteoglycans: from molecular design to cellular function

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Increased brain lysosomal pepstatin-insensitive proteinase activity in patients with neurodegenerative diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Purification and characterization of bovine brain lysosomal pepstatin-insensitive proteinase, the gene product deficient in the human late-infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Transplanted human fetal neural stem cells survive, migrate, and differentiate in ischemic rat cerebral cortex.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Increased expression of subunit c of mitochondrial ATP synthase in brain tissue from neuronal ceroid lipofuscinoses and mucopolysaccharidosis cases but not in long-term fibroblast cultures.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Cellular pathology and pathogenic aspects of neuronal ceroid lipofuscinoses

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

The expression of tripeptidyl peptidase I in various tissues of rats and mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

The lysosomal degradation of neuromedin B is dependent on tripeptidyl peptidase-I: evidence for the impairment of neuropeptide degradation in late-infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Regulation of collagenase activities of human cathepsins by glycosaminoglycans

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Production and characterization of recombinant human CLN2 protein for enzyme-replacement therapy in late infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Structural organization and sequence of CLN2, the defective gene in classical late infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Acidification of the endocytic and exocytic pathways

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Low Density Lipoprotein Receptor-related Protein/[IMAGE][IMAGE]-Macroglobulin Receptor Mediates the Cellular Internalization and Degradation of Thrombospondin

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Fluorescence probe measurement of the intralysosomal pH in living cells and the perturbation of pH by various agents

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Purification and characterization of a tripeptidyl peptidase I from human osteoclastomas: evidence for its role in bone resorption

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Intracranial delivery of CLN2 reduces brain pathology in a mouse model of classical late infantile neuronal ceroid lipofuscinosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Families of serine peptidases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Tripeptidyl-peptidase I is apparently the CLN2 protein absent in classical late-infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Mechanisms of cell-surface rerouting of an endoplasmic reticulum-retained mutant of the vasopressin V1b/V3 receptor by a pharmacological chaperone

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

A cure for traffic jams: small molecule chaperones in the endoplasmic reticulum

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Loci for classical and a variant late infantile neuronal ceroid lipofuscinosis map to chromosomes 11p15 and 15q21-23.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Association of mutations in a lysosomal protein with classical late-infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Mutational analysis of the defective protease in classic late-infantile neuronal ceroid lipofuscinosis, a neurodegenerative lysosomal storage disorder

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Aminoglycoside-mediated suppression of nonsense mutations in late infantile neuronal ceroid lipofuscinosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

A mouse model of classical late-infantile neuronal ceroid lipofuscinosis based on targeted disruption of the CLN2 gene results in a loss of tripeptidyl-peptidase I activity and progressive neurodegeneration

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Mutations in classical late infantile neuronal ceroid lipofuscinosis disrupt transport of tripeptidyl-peptidase I to lysosomes

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Developmental changes in the expression of neuronal ceroid lipofuscinoses-linked proteins.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Determination of the substrate specificity of tripeptidyl-peptidase I using combinatorial peptide libraries and development of improved fluorogenic substrates

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Retro-translocation of proteins from the endoplasmic reticulum into the cytosol

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Mutation of the glycosylated asparagine residue 286 in human CLN2 protein results in loss of enzymatic activity.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Lysosomal storage disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Purification and characterisation of a tripeptidyl aminopeptidase I from rat spleen.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Clinical proteomics in lung diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Ser475, Glu272, Asp276, Asp327, and Asp360 are involved in catalytic activity of human tripeptidyl-peptidase I.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Reevaluation of neuronal ceroid lipofuscinoses: atypical juvenile onset may be the result of CLN2 mutations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Neuronal ceroid lipofuscinoses: classification and diagnosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

Tripeptidyl-peptidase I in neuronal ceroid lipofuscinoses and other lysosomal storage disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

A model of tripeptidyl-peptidase I (CLN2), a ubiquitous and highly conserved member of the sedolisin family of serine-carboxyl peptidases

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

N-glycosylation is crucial for folding, trafficking, and stability of human tripeptidyl-peptidase I.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

ATP synthase--a marvellous rotary engine of the cell.

21 January 2018

1 reference

https://api.crossref.org/works/10.1515%2FBC.2006.135

21 January 2018

Identifiers

DOI

10.1515/BC.2006.135

1 reference

14 August 2017

1 reference

PubMed ID

16895480